Hemophagocytic Lymphohistiocytosis syndrome (HLH) associated with acute pancreatitis: A case report.

Hemophagocytic Lymphohistiocytosis syndrome is fatal hyper‐inflammatory condition due to over‐activation of the immune system, being of primary and secondary types. This case report emphasizes the difficulty and challenge in and of the HLH diagnosis, and therapy should be employed promptly given the high mortality associated with HLH. Hemophagocytic Lymphohistiocytosis is a rare and often fatal inflammatory disease that requires high suspicion in any patient with fever, unexplained cytopenia, splenomegaly and increased inflammatory markers. If diagnosed, treatment should be administered promptly without delay. [ABSTRACT FROM AUTHOR]