An erythematous patch on the ear and face of a young boy.

Due to the high prevalence of ECMs, providers should conduct comprehensive screening of all patients with craniofacial scleroderma and strongly consider aggressive treatment with systemic immunomodulators. Keywords: histology; localized scleroderma; microtia; morphea; pediatric EN histology localized scleroderma microtia morphea pediatric e45 e47 3 12/23/21 20211101 NES 211101 CASE REPORT A 4-year-old boy presented with a 3-month history of an asymptomatic erythematous patch of the right ear. Diagnosis: Linear scleroderma, craniofacial subtype DISCUSSION The patient was initially thought to have cutaneous lupus as the skin biopsy revealed a vacuolar interface dermatitis with a superficial and deep perivascular and perifollicular lymphocytic infiltrate with extension to the subcutaneous fat (Figure 2). [Extracted from the article]