Neonatal Ileal Perforation due to Type IV Ileocecal Valve Atresia.

Only ten cases of ileocecal valve atresia are found in the English literature. Herein, we present a case with ileal perforation due to double membranous atresia (type IV atresia), one at the ileocecal valve, and one at cecum. The plain abdominal graph of a five-day-old girl revealed subdiaphragmatic free air. In the emergent laparotomy, there was a perforation in the distal ileum. We performed an end-ileostomy. During the second operation (5-month-old), the catheter placed to the distal of the ileostomy did not go further through the ileocecal valve. The catheter that passed from the appendix stump also stopped at a distance of 1 cm. An anastomosis was made between the ileum and the colon. The differential diagnosis of ileocecal valve atresia includes ileal atresia, meconium ileus and necrotizing enterocolitis. In case of a perforation, we recommend opening an ileostomy initially and then starting a treatment for sepsis. We advise to check the distal colon for further atresia. [ABSTRACT FROM AUTHOR]