Modern management of children with haemophagocytic lymphohistiocytosis.

Focuses on the management of children with hemophagocytic lymphohistiocytosis (HLH), an autosomal recessive disease. Conditions leading to HLH; Cardinal symptoms of familial HLH; Genetic markers for HLH; Pathophysiology of HLH; Diagnostic management; Therapeutic management; Restoration of immune function; Problem of EBV-associated HLH; Immunochemotherapy for familial HLH; Bone marrow transplantation.