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[Kinsbourne syndrome: review of our cases].

Authors :
Rodríguez-Barrionuevo AC
Caballero-Morales MA
Delgado-Marqués MP
Mora-Ramírez MD
Martínez-Antón J
Source :
Revista de neurologia [Rev Neurol] 1998 Jun; Vol. 26 (154), pp. 956-9.
Publication Year :
1998

Abstract

Introduction: The childhood opsoclonus-myoclonus or Kinsbourne syndrome, is a uncommon process, of acute or subacute beginning, which affects infant and children. It's course is characterized by opsoclonus, polimyoclonias and cerebellar ataxia. The disease is frequently associated to neuroblastoma (46%).<br />Material and Methods: We present a retrospective study on 9 patients, emphasizing the clinical presentation and the evolution aspects.<br />Results and Conclusions: We found changes in the EEG in three cases. Most surprising is the scarce incidence of neuroblastoma, which has been found only in a one out of nine patients. We found three cases with relapse during the treatment or on withdrawal and one of them relapsed twice again. The evolution has been variable, since 5/9 patient have presented some type of mild or moderate neuro-psychological sequelae. Out of three patient with relapses, two presented permanent neurological sequelae. A patient which suffered three relapses, is also the one which presents more serious sequelae.

Details

Language :
Spanish; Castilian
ISSN :
0210-0010
Volume :
26
Issue :
154
Database :
MEDLINE
Journal :
Revista de neurologia
Publication Type :
Academic Journal
Accession number :
9658467