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Mid-aortic syndrome presenting in childhood.
- Source :
-
The British journal of surgery [Br J Surg] 1996 Feb; Vol. 83 (2), pp. 235-40. - Publication Year :
- 1996
-
Abstract
- Mid-aortic syndrome (MAS) is an uncommon condition characterized by segmental narrowing of the proximal abdominal aorta and ostial stenosis of its major branches. It is usually diagnosed in young adults, but may present in childhood as a challenging problem. Over the past 20 years 13 patients with MAS have presented to this institution. All had hypertension, four had associated neurofibromatosis, three persistent eosinophilia and three had Williams syndrome. In all cases arteriography showed a smooth segmental narrowing of the abdominal aorta with concomitant stenosis at the origins of the renal arteries. Six children were successfully treated with antihypertensive medication alone. Percutaneous transluminal angioplasty was attempted in two cases with poor result. Surgery was indicated in seven children with refractory hypertension and progressive renal impairment. Techniques used to revascularize the kidneys included thoracoabdominal to infrarenal aortic bypass with renal artery reimplantation, splenorenal bypass, gastroduodenal to renal bypass, aortorenal bypass and autotransplantation.
- Subjects :
- Adolescent
Anastomosis, Surgical methods
Angioplasty, Balloon, Coronary
Aorta, Abdominal
Aortic Diseases surgery
Aortic Diseases therapy
Child
Child, Preschool
Constriction, Pathologic
Female
Humans
Hypertension, Renovascular drug therapy
Hypertension, Renovascular etiology
Infant
Male
Neurofibromatoses etiology
Radiography
Renal Artery Obstruction etiology
Syndrome
Aortic Diseases diagnostic imaging
Hypertension, Renovascular diagnostic imaging
Subjects
Details
- Language :
- English
- ISSN :
- 0007-1323
- Volume :
- 83
- Issue :
- 2
- Database :
- MEDLINE
- Journal :
- The British journal of surgery
- Publication Type :
- Academic Journal
- Accession number :
- 8689175