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Toward enzyme therapy in Gm2 gangliosidosis: beta-hexosaminidase infusion in normal cats.
- Source :
-
Pediatric research [Pediatr Res] 1979 Aug; Vol. 13 (8), pp. 916-23. - Publication Year :
- 1979
- Subjects :
- Animals
Cats
Disease Models, Animal
Female
Hexosaminidases blood
Hexosaminidases therapeutic use
Humans
Liver metabolism
Lysosomes metabolism
Male
Microsomes, Liver metabolism
Mitochondria, Liver metabolism
Subcellular Fractions metabolism
Tissue Distribution
Hexosaminidases metabolism
Sandhoff Disease drug therapy
Subjects
Details
- Language :
- English
- ISSN :
- 0031-3998
- Volume :
- 13
- Issue :
- 8
- Database :
- MEDLINE
- Journal :
- Pediatric research
- Publication Type :
- Academic Journal
- Accession number :
- 573435
- Full Text :
- https://doi.org/10.1203/00006450-197908000-00009