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[Alder's anomaly in mucopolysaccharidosis type VI. Cytological, cytochemical and ultrastructural study].
- Source :
-
Nouvelle revue francaise d'hematologie [Nouv Rev Fr Hematol (1978)] 1985; Vol. 27 (3), pp. 183-8. - Publication Year :
- 1985
-
Abstract
- A cytological study of the blood and bone marrow of a child with mucopolysaccharidosis with Alder's anomaly was analysed at the optical and ultrastructural level. Morphological abnormalities of the blood and bone marrow leucocytes are defined; cytochemical and cytoenzymological abnormalities are indicated, allowing a differential diagnosis with "toxic granulations". The ultrastructural patterns of the storage cells are described compared to descriptions in the literature and the question of their mastocytic or macrophagic filiation is discussed.
- Subjects :
- Bone Marrow pathology
Child
Cytoplasmic Granules pathology
Granulocytes pathology
Hematologic Diseases pathology
Histocytochemistry
Humans
Leukocytes enzymology
Lymphocytes pathology
Macrophages pathology
Microscopy, Electron
Mucopolysaccharidosis VI pathology
Neutrophils pathology
Hematologic Diseases complications
Leukocytes pathology
Mucopolysaccharidoses complications
Mucopolysaccharidosis VI complications
Subjects
Details
- Language :
- French
- Volume :
- 27
- Issue :
- 3
- Database :
- MEDLINE
- Journal :
- Nouvelle revue francaise d'hematologie
- Publication Type :
- Academic Journal
- Accession number :
- 3929230