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[Diagnosis and management of patients with pheochromocytoma/paraganglioma: Consensus of experts of the Russian Medical Society for Arterial Hypertension and the Multidisciplinary Group for the Diagnosis and Treatment of Neuroendocrine Tumors].

Authors :
Blinova NV
Ilovayskaya IA
Chikhladze NM
Lugovskaya AY
Britvin TA
Gurevich LE
Nefedova LN
Shikina VE
Chazova IE
Source :
Terapevticheskii arkhiv [Ter Arkh] 2024 Jul 30; Vol. 96 (7), pp. 645-658. Date of Electronic Publication: 2024 Jul 30.
Publication Year :
2024

Abstract

The understanding of the nature of catecholamine-secreting tumors has changed significantly in recent years, affecting terminology and classification. Phaeochromocytoma/paraganglioma (PCC/PG) is a rare neuroendocrine tumor from chromaffin tissue that produces and secretes catecholamines. The incidence of PCC/PG is relatively low, with 2-8 cases per 1 million population per year; among patients with arterial hypertension, their prevalence is 0.2-0.6%. However, delayed diagnosis of PCC/PG is associated with a high risk of cardiovascular complications and a high mortality rate. The consensus presents the clinical manifestations of the disease with an emphasis on the course of arterial hypertension as the most common symptom in PCC/PG; modern ideas about the features of diagnosis, aspects of preoperative preparation, treatment, and follow-up of patients with PCC/PG are considered.

Details

Language :
Russian
ISSN :
0040-3660
Volume :
96
Issue :
7
Database :
MEDLINE
Journal :
Terapevticheskii arkhiv
Publication Type :
Academic Journal
Accession number :
39106507
Full Text :
https://doi.org/10.26442/00403660.2024.07.202779