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[Tracheobronchial involvement in relapsing polychondritis and differential diagnoses].
- Source :
-
Revue des maladies respiratoires [Rev Mal Respir] 2024 Jun; Vol. 41 (6), pp. 421-438. Date of Electronic Publication: 2024 May 17. - Publication Year :
- 2024
-
Abstract
- Relapsing polychondritis is a systemic auto-immune disease that mainly affects cartilage structures, progressing through inflammatory flare-ups between phases of remission and ultimately leading to deformation of the cartilages involved. In addition to characteristic damage of auricular or nasal cartilage, tracheobronchial and cardiac involvement are particularly severe, and can seriously alter the prognosis. Tracheobronchial lesions are assessed by means of a multimodal approach, including dynamic thoracic imaging, measurement of pulmonary function (with recent emphasis on pulse oscillometry), and mapping of tracheal lesions through flexible bronchoscopy. Diagnosis can be difficult in the absence of specific diagnostic tools, especially as there may exist a large number of differential diagnoses, particularly as regards inflammatory diseases. The prognosis has improved, due largely to upgraded interventional bronchoscopy techniques and the development of immunosuppressant drugs and targeted therapies, offering patients a number of treatment options.<br /> (Copyright © 2024 SPLF. Published by Elsevier Masson SAS. All rights reserved.)
- Subjects :
- Humans
Diagnosis, Differential
Tracheal Diseases diagnosis
Tracheal Diseases pathology
Bronchoscopy methods
Trachea pathology
Bronchi pathology
Polychondritis, Relapsing diagnosis
Polychondritis, Relapsing complications
Bronchial Diseases diagnosis
Bronchial Diseases pathology
Bronchial Diseases etiology
Subjects
Details
- Language :
- French
- ISSN :
- 1776-2588
- Volume :
- 41
- Issue :
- 6
- Database :
- MEDLINE
- Journal :
- Revue des maladies respiratoires
- Publication Type :
- Academic Journal
- Accession number :
- 38762394
- Full Text :
- https://doi.org/10.1016/j.rmr.2024.03.009