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Massive Parallel DNA Sequencing of Patients with Inherited Cardiomyopathies in Cyprus and Suggestion of Digenic or Oligogenic Inheritance.

Authors :
Koutsofti C
Ioannides M
Polydorou C
Papagregoriou G
Malatras A
Michael G
Hadjiioannou I
Pieri S
Loizidou EM
Eftychiou C
Papasavvas E
Christophides T
Alkelai A
Kapoor M
Shuldiner AR
Avraamides P
Deltas C
Source :
Genes [Genes (Basel)] 2024 Feb 28; Vol. 15 (3). Date of Electronic Publication: 2024 Feb 28.
Publication Year :
2024

Abstract

Inherited cardiomyopathies represent a highly heterogeneous group of cardiac diseases. DNA variants in genes expressed in cardiomyocytes cause a diverse spectrum of cardiomyopathies, ultimately leading to heart failure, arrythmias, and sudden cardiac death. We applied massive parallel DNA sequencing using a 72-gene panel for studying inherited cardiomyopathies. We report on variants in 25 families, where pathogenicity was predicted by different computational approaches, databases, and an in-house filtering analysis. All variants were validated using Sanger sequencing. Familial segregation was tested when possible. We identified 41 different variants in 26 genes. Analytically, we identified fifteen variants previously reported in the Human Gene Mutation Database: twelve mentioned as disease-causing mutations (DM) and three as probable disease-causing mutations (DM?). Additionally, we identified 26 novel variants. We classified the forty-one variants as follows: twenty-eight (68.3%) as variants of uncertain significance, eight (19.5%) as likely pathogenic, and five (12.2%) as pathogenic. We genetically characterized families with a cardiac phenotype. The genetic heterogeneity and the multiplicity of candidate variants are making a definite molecular diagnosis challenging, especially when there is a suspicion of incomplete penetrance or digenic-oligogenic inheritance. This is the first systematic study of inherited cardiac conditions in Cyprus, enabling us to develop a genetic baseline and precision cardiology.

Details

Language :
English
ISSN :
2073-4425
Volume :
15
Issue :
3
Database :
MEDLINE
Journal :
Genes
Publication Type :
Academic Journal
Accession number :
38540378
Full Text :
https://doi.org/10.3390/genes15030319