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[A Surgical Case of Currarino Syndrome with Syringomyelia].

Authors :
Nemoto T
Ochiai J
Oku S
Yamamoto Y
Hirade T
Kanai R
Hidaka T
Horie N
Akai T
Ikawa F
Source :
Brain and nerve = Shinkei kenkyu no shinpo [Brain Nerve] 2023 Aug; Vol. 75 (8), pp. 971-976.
Publication Year :
2023

Abstract

Currarino syndrome is characterized by a triad of anorectal malformations, sacral defects, and presacral masses. Although it is not extremely rare, this report presents a surgical case of Currarino syndrome with syringomyelia and discusses related literature. The patient is a girl, aged 2 years and 2 months, who presented with marked constipation, chronic cystitis, and lower limb weakness. After examining the patient through magnetic resonance imaging, we diagnosed her with rectal compression due to meningocele and syringomyelia. The base of the meningocele was detached, and the spinal cord was untethered. One week after surgery, her lower limb weakness and constipation improved. Following up on symptoms and performing imaging is essential to determine a treatment plan for Currarino syndrome. (Received 28 February, 2023; Accepted 22 March, 2023; Published 1 August, 2023).

Details

Language :
Japanese
ISSN :
1881-6096
Volume :
75
Issue :
8
Database :
MEDLINE
Journal :
Brain and nerve = Shinkei kenkyu no shinpo
Publication Type :
Academic Journal
Accession number :
37537744
Full Text :
https://doi.org/10.11477/mf.1416202452