Congenital ciliary body cysts causing lens abnormalities and secondary angle closure glaucoma in a child.

Authors :: Turner ML
de Alba Campomanes AG
Stewart JM
Oatts JT
Source :: American journal of ophthalmology case reports [Am J Ophthalmol Case Rep] 2022 Oct 14; Vol. 28, pp. 101723. Date of Electronic Publication: 2022 Oct 14 (Print Publication: 2022).
Publication Year :: 2022
Abstract: Purpose: To report a case of congenital ciliary body cysts causing microspherophakia, ectopia lentis, and secondary angle closure glaucoma in an infant.<br />Observations: A 16-month-old male was found to have bilateral ciliary body cysts associated with zonular laxity or absence causing microspherophakia and ectopia lentis as demonstrated on multimodal imaging. Additionally, the patient had secondary angle closure glaucoma which was likely multi-factorial related to both lens abnormalities and anterior displacement of the iris from the cysts themselves. The patient underwent lensectomy and cyst removal which resulted in intraocular pressure stabilization and visual rehabilitation.<br />Conclusions and Importance: Congenital ciliary body cysts are a rare cause of lens abnormalities and secondary angle closure glaucoma in children. Information regarding genetic underpinnings or systemic associations is limited.<br /> (© 2022 The Authors.)

Full Text Access

Tools