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An unusual presentation of peripapillary pachychoroid syndrome.

Authors :: Hubschman S
Hou K
Sarraf D
Tsui I
Source :: American journal of ophthalmology case reports [Am J Ophthalmol Case Rep] 2022 Jan 22; Vol. 25, pp. 101338. Date of Electronic Publication: 2022 Jan 22 (Print Publication: 2022).
Publication Year :: 2022
Abstract: Purpose: Peripapillary pachychoroid syndrome (PPS) is a recently described entity of the pachychoroid disease spectrum and is characterized by thickening of the nasal choroid and peripapillary fluid pockets. This case illustrates the remarkable natural history of this recently described disorder.<br />Observation: This case report describes a patient with PPS who presented with severe cystoid macular edema (CME) that spontaneously resolved without treatment.<br />Conclusions and Importance: This report indicates that PPS can exhibit significant fluctuation of CME and a favorable natural history in some cases. It also suggests that observation may be a viable option in the initial management of this finding if vision is not significantly unaffected.<br />Competing Interests: D. Sarraf is a consultant for 10.13039/100002429Amgen, 10.13039/100004326Bayer Healthcare, 10.13039/100004328Genentech, Iveric Bio, 10.13039/100004336Novartis, and Optovue and receives research support from 10.13039/100007819Allergan, Boehringer 10.13039/100004328Genentech, Heidelberg, Optovue, 10.13039/100009857Regeneron and 10.13039/501100010383Topcon. The remaining authors have no conflicting interests to disclose.<br /> (© 2022 Published by Elsevier Inc.)