Harlequin syndrome in a young girl: An opportunity to rethink the terminology.

Authors :: Douvali T
Papageorgiou V
Gerochristou M
Gerodimou M
Tampouratzi E
Chasapi V
Source :: Pediatric dermatology [Pediatr Dermatol] 2021 Jul; Vol. 38 (4), pp. 984-985. Date of Electronic Publication: 2021 Jul 05.
Publication Year :: 2021
Abstract: Harlequin syndrome is a rare disorder of the autonomic nervous system, presenting as unilateral reduced flushing and sweating of the face induced by exercise, stress, or heat. It is caused by a cervical sympathetic deficit located at the preganglionic or postganglionic level on the non-flushing side. We present a case of an 8 year old with harlequin syndrome and review the other dermatological conditions for which the term "harlequin" is part of the nomenclature.<br /> (© 2021 Wiley Periodicals LLC.)