Pleomorphic Pulmonary Manifestations of IgG4-Related Disease.

Authors :: Naramala S
Biswas S
Adapa S
Gayam V
Castillo RC
Annangi S
Konala VM
Source :: Case reports in rheumatology [Case Rep Rheumatol] 2019 Aug 20; Vol. 2019, pp. 7572869. Date of Electronic Publication: 2019 Aug 20 (Print Publication: 2019).
Publication Year :: 2019
Abstract: Immunoglobulin G4-related disease (IgG4-RD) is a fibroinflammatory disorder which has been first reported in 2001 by Hamano and colleagues in a patient with autoimmune sclerosing pancreatitis. Almost every organ in the human body can be affected by IgG4-RD from infiltration with IgG4-positive plasma cells. Involvement of lungs with IgG4 is reported previously, but still, there is no clear picture of the pathophysiology behind lung involvement. Here, we are presenting a patient who has IgG4-RD presenting as pseudotumor of the lungs.<br />Competing Interests: The authors declare that there are no conflicts of interest regarding the publication of this paper.