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Idiopathic Sclerosing Orbital Inflammation in a Relapsing Polychondritis Patient With Impaired Vision.
- Source :
-
Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseases [J Clin Rheumatol] 2019 Sep; Vol. 25 (6), pp. e82-e83. - Publication Year :
- 2019
-
Abstract
- A 55-year-old woman with relapsing polychondritis had progressively enlarged right retro-orbital tumor invading the optic nerve, followed by left retrobulbar infiltrating lesions despite prescription of high-dose corticosteroids and pulse methylprednisolone. Repeated histopathologic analyses showed dense collagen fibers with scanty inflammatory cells, consistent with the diagnosis of idiopathic sclerosing orbital inflammation. This disorder has been recognized as a distinct entity with unique clinical features and coexisting rheumatologic disorders, requiring more focused diagnostic strategies and therapeutic regimens. In summary, we demonstrate a rare ocular manifestation in relapsing polychondritis and emphasize the importance of serial radiological and pathological evaluations in such patients presenting with exophthalmos.
- Subjects :
- Biopsy methods
Diagnosis, Differential
Female
Glucocorticoids administration & dosage
Humans
Inflammation etiology
Inflammation pathology
Middle Aged
Pulse Therapy, Drug methods
Exophthalmos diagnosis
Exophthalmos etiology
Eye Diseases diagnostic imaging
Eye Diseases drug therapy
Eye Diseases etiology
Magnetic Resonance Imaging methods
Methylprednisolone administration & dosage
Orbital Neoplasms diagnosis
Polychondritis, Relapsing diagnosis
Polychondritis, Relapsing physiopathology
Polychondritis, Relapsing therapy
Tomography, X-Ray Computed methods
Subjects
Details
- Language :
- English
- ISSN :
- 1536-7355
- Volume :
- 25
- Issue :
- 6
- Database :
- MEDLINE
- Journal :
- Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseases
- Publication Type :
- Academic Journal
- Accession number :
- 29384827
- Full Text :
- https://doi.org/10.1097/RHU.0000000000000676