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Intracranial Erdheim-Chester Disease Mimicking Parafalcine Meningioma: Report of Two Cases and Review of the Literature.
- Source :
-
World neurosurgery [World Neurosurg] 2018 Feb; Vol. 110, pp. 365-370. Date of Electronic Publication: 2017 Nov 28. - Publication Year :
- 2018
-
Abstract
- Background: Erdheim-Chester disease (ECD) is a rare, non-Langerhans cell histiocytosis that typically occurs in middle-aged patients. It is usually characterized by multifocal osteosclerotic lesions of the long-bones, however many cases have extraskeletal involvement. Central nervous system (CNS) involvement is common, but isolated CNS involvement at presentation has rarely been reported.<br />Case Description: Here we report two cases of dural-based ECD mimicking meningioma on imaging with no other identified sites of disease.<br />Conclusion: ECD is a rare disease, with isolated CNS involvement reported only a few times in the literature. The significance of this presentation requires additional study and long-term follow up.<br /> (Copyright © 2017 Elsevier Inc. All rights reserved.)
- Subjects :
- Adult
Antigens, CD metabolism
Antigens, Differentiation, Myelomonocytic metabolism
Erdheim-Chester Disease diagnostic imaging
Female
Humans
Intralaminar Thalamic Nuclei diagnostic imaging
Magnetic Resonance Imaging
Male
Middle Aged
Erdheim-Chester Disease physiopathology
Meningeal Neoplasms physiopathology
Meningioma physiopathology
Subjects
Details
- Language :
- English
- ISSN :
- 1878-8769
- Volume :
- 110
- Database :
- MEDLINE
- Journal :
- World neurosurgery
- Publication Type :
- Academic Journal
- Accession number :
- 29191545
- Full Text :
- https://doi.org/10.1016/j.wneu.2017.11.074