Back to Search Start Over

Doege-potter syndrome: a report of a histologically benign but clinically malignant case.

Authors :
Kim DW
Na KJ
Yun JS
Song SY
Source :
Journal of cardiothoracic surgery [J Cardiothorac Surg] 2017 Aug 07; Vol. 12 (1), pp. 64. Date of Electronic Publication: 2017 Aug 07.
Publication Year :
2017

Abstract

Background: Solitary fibrous tumors of the pleura (SFTPs) are relatively rare tumors that originate from mesenchymal cells of submesothelial tissue of the pleura. Most patients with SFTPs are asymptomatic; however, pleuritic chest pain, cough, and dyspnea can develop. If hypoglycemia is associated with a solitary fibrous tumor, it is referred to as the Doege-Potter syndrome.<br />Case Presentation: A 70-year-old man had visited our hospital with a chief complaint of dyspnea, and he was diagnosed as having a solitary fibrous tumor. A few years later, he developed hypoglycemia, and he underwent excision of the mass.<br />Conclusion: Occasionally, SFTPs induce several paraneoplastic events, such as hypertrophic osteoarthropathy. We described here a patient with an SFTP with Doege-Potter syndrome who was successfully treated with complete resection. Although lesions can be histologically benign, they can clinically present with malignant features.

Details

Language :
English
ISSN :
1749-8090
Volume :
12
Issue :
1
Database :
MEDLINE
Journal :
Journal of cardiothoracic surgery
Publication Type :
Academic Journal
Accession number :
28784156
Full Text :
https://doi.org/10.1186/s13019-017-0630-4