Pyoblepharitis Vegetans in Association With Pyodermatitis-Pyostomatitis Vegetans: Expanding the Spectrum of a Rare, Multisystem Disorder.

Background: Pyodermatitis-pyostomatitis vegetans (PDPSV) is a rare inflammatory disorder of the skin and oral mucosa that is commonly associated with inflammatory bowel disease (IBD). Ocular involvement is uncommon.
Objective: Given the association with IBD, it is important for dermatologists to be aware of the varying manifestations of PDPSV.
Methods: A biopsy was performed for diagnosis confirmation, and the literature was reviewed for similar cases.
Observations: Our 48-year-old PDPSV patient presented with rare ocular findings. There have been 8 PDPSV reports of ocular involvement. Only 3 of those patients developed blepharitis and/or conjunctival disease. None showed simultaneous involvement of sites at disease onset like our patient.
Results: Our patient's concomitant presentation at onset of multiple mucocutaneous sites with blepharitis and conjunctivitis is unique.
Conclusions: We propose the term pyoblepharitis vegetans (PBV) to describe vegetating lesions of the eyelids. The diagnosis of PDPSPBV should be considered with presentation of these signs.
(© The Author(s) 2015.)