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Dermatofibrosarcoma protuberans, version 1.2014.

Authors :
Bichakjian CK
Olencki T
Alam M
Andersen JS
Berg D
Bowen GM
Cheney RT
Daniels GA
Glass LF
Grekin RC
Grossman K
Ho AL
Lewis KD
Lydiatt DD
Morrison WH
Nehal KS
Nelson KC
Nghiem P
Perlis CS
Shaha AR
Thorstad WL
Tuli M
Urist MM
Wang TS
Werchniak AE
Wong SL
Zic JA
McMillian N
Hoffman K
Ho M
Source :
Journal of the National Comprehensive Cancer Network : JNCCN [J Natl Compr Canc Netw] 2014 Jun; Vol. 12 (6), pp. 863-8.
Publication Year :
2014

Abstract

Dermatofibrosarcoma protuberans (DFSP) is an uncommon soft tissue tumor characterized by a relatively high risk of local recurrence and low risk of metastasis. The NCCN Guidelines for DFSP provide multidisciplinary recommendations on the management of patients with this rare disease. These NCCN Guidelines Insights highlight the addition of the Principles of Pathology section, which provides recommendations on the pathologic assessment of DFSP. Because DFSP can mimic other lesions, immunohistochemical studies are often required to establish diagnosis. Cytogenetic testing for the characteristic translocation t(17;22)(q22;q13) can also be valuable in the differential diagnosis of DFSP with other histologically similar tumors.<br /> (Copyright © 2014 by the National Comprehensive Cancer Network.)

Details

Language :
English
ISSN :
1540-1413
Volume :
12
Issue :
6
Database :
MEDLINE
Journal :
Journal of the National Comprehensive Cancer Network : JNCCN
Publication Type :
Academic Journal
Accession number :
24925197
Full Text :
https://doi.org/10.6004/jnccn.2014.0081