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Long-term orthodontic and surgical treatment and stability of a patient with Beckwith-Wiedemann syndrome.
- Source :
-
American journal of orthodontics and dentofacial orthopedics : official publication of the American Association of Orthodontists, its constituent societies, and the American Board of Orthodontics [Am J Orthod Dentofacial Orthop] 2014 May; Vol. 145 (5), pp. 672-84. - Publication Year :
- 2014
-
Abstract
- Beckwith-Wiedemann syndrome (BWS) is a congenital growth disorder. Children born with BWS develop enlarged organs, including the tongue, a large body, and other signs. A woman with BWS was treated and followed for 30 years. Treatment consisted of tongue reduction, orthopedic and orthodontic treatment, orthognathic surgery, and retention. The patient was first treated when she was 5 years old. Her original orthodontic problems included macroglossia, anterior open bite, anterior crossbite, and a skeletal Class III jaw relationship caused by significant mandibular protrusion. The jaw-base relationships did not improve in the early preadolescent period after phase 1 of orthodontic treatment with a vertical chincap. With the growth spurt accompanying puberty, she developed a severe skeletal Class III jaw relationship and a constricted maxillary arch. Surgically assisted rapid maxillary expansion was performed at 23 years of age to correct the severe discrepancy between the maxillary and mandibular dental arch widths. Then, at 26 years, a LeFort I osteotomy, a horseshoe osteotomy, a bilateral sagittal split ramus osteotomy, and genioplasty were performed after presurgical orthodontic treatment with extraction of the mandibular first molars. Both the facial profile and the occlusion were stable after 6 years of retention. This case report discusses the result of long-term observation of a patient with BWS who underwent tongue reduction, early orthodontic treatment, and surgical-orthodontic treatment.<br /> (Copyright © 2014 American Association of Orthodontists. Published by Mosby, Inc. All rights reserved.)
- Subjects :
- Beckwith-Wiedemann Syndrome surgery
Child, Preschool
Extraoral Traction Appliances
Female
Follow-Up Studies
Genioplasty methods
Glossectomy methods
Humans
Longitudinal Studies
Macroglossia surgery
Malocclusion, Angle Class III surgery
Malocclusion, Angle Class III therapy
Maxilla abnormalities
Open Bite surgery
Open Bite therapy
Osteotomy, Le Fort methods
Osteotomy, Sagittal Split Ramus methods
Palatal Expansion Technique
Patient Care Planning
Prognathism surgery
Prognathism therapy
Treatment Outcome
Beckwith-Wiedemann Syndrome therapy
Orthodontics, Corrective methods
Orthognathic Surgical Procedures methods
Subjects
Details
- Language :
- English
- ISSN :
- 1097-6752
- Volume :
- 145
- Issue :
- 5
- Database :
- MEDLINE
- Journal :
- American journal of orthodontics and dentofacial orthopedics : official publication of the American Association of Orthodontists, its constituent societies, and the American Board of Orthodontics
- Publication Type :
- Academic Journal
- Accession number :
- 24785932
- Full Text :
- https://doi.org/10.1016/j.ajodo.2013.08.019