[Perioperative management for liver transplant in a patient with familial amyloid polyneuropathy with heart involvement].

Authors :: López-Herrera Rodríguez D
Guerrero Domínguez R
Mellado Miras P
Gómez Sosa L
Source :: Revista espanola de anestesiologia y reanimacion [Rev Esp Anestesiol Reanim] 2015 Jan; Vol. 62 (1), pp. 46-8. Date of Electronic Publication: 2014 Apr 16.
Publication Year :: 2015
Abstract: Familial amyloid polyneuropathy (FAP) is a systemic amyloidosis caused by mutated transthyretin. Cardiac amyloidosis, the major prognostic determinant in systemic amyloidosis, is characterized by infiltration of the myocardium, leading to cardiomyopathy and conduction disturbances. Liver transplantation is the only curative option for patients with FAP. The case is presented of a 36-year-old patient with type i FAP with cardiac involvement, proposed for liver transplant surgery, which was successfully performed without any preoperative event of interest.<br /> (Copyright © 2014 Sociedad Española de Anestesiología, Reanimación y Terapéutica del Dolor. Publicado por Elsevier España, S.L.U. All rights reserved.)

Subjects :: Adult
Atrioventricular Block diagnostic imaging
Atrioventricular Block etiology
Cardiomyopathies diagnostic imaging
Humans
Intraoperative Complications prevention & control
Male
Monitoring, Intraoperative
Norepinephrine therapeutic use
Postoperative Complications prevention & control
Vascular Resistance drug effects
Amyloid Neuropathies, Familial complications
Cardiomyopathies etiology
Liver Transplantation methods
Perioperative Care methods

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