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Mounier-Kuhn syndrome.
- Source :
-
Journal of bronchology & interventional pulmonology [J Bronchology Interv Pulmonol] 2014 Apr; Vol. 21 (2), pp. 145-9. - Publication Year :
- 2014
-
Abstract
- Mounier-Kuhn syndrome or congenital tracheobronchomegaly is a rare clinical and radiologic condition. It is characterized by a tracheal and bronchial dilation. Fewer than 100 cases have been reported in the medical literature since the original description in 1932. The first utilization of bronchoscopy for diagnosis of this condition was recorded by Lemoine only in 1949. The cause of this condition is not clearly understood; however, histopathologic findings of atrophy of smooth muscles and elastic tissue in the trachea and main bronchi have been observed. Tracheobronchomegaly can be associated with tracheal and bronchial diverticuli.
- Subjects :
- Aged
Atrophy
Bronchiectasis diagnostic imaging
Delayed Diagnosis
Diagnosis, Differential
Dilatation, Pathologic
Humans
Male
Radiography
Rare Diseases pathology
Rare Diseases physiopathology
Recurrence
Respiratory Tract Infections etiology
Tracheobronchomegaly pathology
Tracheobronchomegaly physiopathology
Treatment Failure
Diagnostic Techniques, Respiratory System
Diverticulum diagnostic imaging
Occupational Diseases diagnosis
Pulmonary Disease, Chronic Obstructive diagnosis
Rare Diseases diagnostic imaging
Tracheobronchomegaly diagnostic imaging
Subjects
Details
- Language :
- English
- ISSN :
- 1948-8270
- Volume :
- 21
- Issue :
- 2
- Database :
- MEDLINE
- Journal :
- Journal of bronchology & interventional pulmonology
- Publication Type :
- Academic Journal
- Accession number :
- 24739689
- Full Text :
- https://doi.org/10.1097/LBR.0000000000000068