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Advances in basic and clinical research in laminopathies.

Authors :
Politano L
Carboni N
Madej-Pilarczyk A
Marchel M
Nigro G
FidziaĆ³ska A
Opolski G
Hausmanowa-Petrusewicz I
Source :
Acta myologica : myopathies and cardiomyopathies : official journal of the Mediterranean Society of Myology [Acta Myol] 2013 May; Vol. 32 (1), pp. 18-22.
Publication Year :
2013

Abstract

Lamins (LMNA) are the main proteins of the nuclear lamina considered to be the ancestors of all intermediate filament proteins. They form complex protein assemblies with integral proteins of the inner nuclear membrane, transcriptional regulators, histones and chromatin modifiers. During recent years, interest in lamins has greatly increased due to the identification of many distinct heritable human disorders associated with lamin mutations. These disorders, collectively termed laminopathies, range from muscular dystrophies to premature aging. They may affect muscle, fat, bone, nerve and skin tissues. The workshop was addressed to understand lamin organization and its roles in nuclear processes, mutations in lamins affecting cell and tissues functions, the biology of the nucleus and laminopathic disease mechanisms, all aspects important for designing future therapies.

Details

Language :
English
ISSN :
1128-2460
Volume :
32
Issue :
1
Database :
MEDLINE
Journal :
Acta myologica : myopathies and cardiomyopathies : official journal of the Mediterranean Society of Myology
Publication Type :
Academic Journal
Accession number :
23853505