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Type IV Ehlers-Danlos syndrome with isolated arterial involvement.
- Source :
-
Annals of vascular surgery [Ann Vasc Surg] 1990 Jan; Vol. 4 (1), pp. 15-9. - Publication Year :
- 1990
-
Abstract
- Ehlers-Danlos syndrome is a connective tissue disorder characterized by skin hyperelasticity and friability, hyperextensible small articulations, vascular fragility, and ocular and visceral symptoms. Ten types of Ehlers-Danlos syndrome have been described to date. Type IV is characterized by isolated arterial involvement with the risk of rupture, making diagnosis difficult. A 25-year-old man was operated on for a ruptured left and then right iliac artery and once again for a hepatic artery aneurysm within a nine month period. The diagnosis of Ehlers-Danlos syndrome was based on clinical and histopathologic findings. An asymptomatic iliac artery aneurysm was found in the patient's 23-year-old brother.
- Subjects :
- Adult
Aneurysm diagnosis
Aneurysm surgery
Ehlers-Danlos Syndrome classification
Ehlers-Danlos Syndrome diagnosis
Hematoma diagnosis
Hematoma surgery
Humans
Ligation
Male
Rupture, Spontaneous
Aneurysm complications
Ehlers-Danlos Syndrome complications
Hematoma etiology
Hepatic Artery
Iliac Artery
Retroperitoneal Space
Subjects
Details
- Language :
- English
- ISSN :
- 0890-5096
- Volume :
- 4
- Issue :
- 1
- Database :
- MEDLINE
- Journal :
- Annals of vascular surgery
- Publication Type :
- Academic Journal
- Accession number :
- 2297468
- Full Text :
- https://doi.org/10.1007/BF02042682