[Dermatofibrosarcoma protuberans of Darier and Ferranda study of 28 cases in adult].

Dermatofibrosarcoma protuberans of Darier and Ferrand is a mesenchymatous skin tumor of intermediate malignant potential, characterised by slow growth, local malignancy and a high rate of recurrence. It is a rare tumor, accounting for approximately 0.1% to 0.18% of all malignant skin tumors. Peak incidence of the disease is between 20 to 40 years of age. We report a retrospective study of 28 cases of dermatofibrosarcoma protuberans. We reviewed the clinical features, histopathological and immunohistochemical aspects of this tumor.