Back to Search
Start Over
Long-segment Hirschsprung's disease.
- Source :
-
Archives of surgery (Chicago, Ill. : 1960) [Arch Surg] 1992 Sep; Vol. 127 (9), pp. 1047-50; discussion 1050-1. - Publication Year :
- 1992
-
Abstract
- We identified 21 children (14 boys and seven girls) with long-segment Hirschsprung's disease defined as aganglionosis extending proximal to the ileocecal valve. Long-segment Hirschsprung's disease is difficult to diagnose and treat; symptoms may be mild, and diagnosis delayed. Abdominal distention and constipation or delayed passage of meconium are the most common symptoms. Radiologic studies are unreliable in establishing the diagnosis. The morbidity rate is high because of the high transition zone and short gut. The long-term outcome of patients after the standard Duhamel procedure is satisfactory, except with extremely high transition zones. Pull-through procedures should not be performed in the small infant, but should be delayed until patients are old enough to be continent.
- Subjects :
- Abdomen pathology
Constipation physiopathology
Female
Follow-Up Studies
Hirschsprung Disease pathology
Hirschsprung Disease physiopathology
Humans
Ileal Diseases pathology
Ileal Diseases physiopathology
Ileal Diseases surgery
Ileocecal Valve pathology
Ileostomy adverse effects
Ileostomy methods
Infant
Infant, Newborn
Male
Meconium
Survival Rate
Vomiting physiopathology
Hirschsprung Disease surgery
Subjects
Details
- Language :
- English
- ISSN :
- 0004-0010
- Volume :
- 127
- Issue :
- 9
- Database :
- MEDLINE
- Journal :
- Archives of surgery (Chicago, Ill. : 1960)
- Publication Type :
- Academic Journal
- Accession number :
- 1514906
- Full Text :
- https://doi.org/10.1001/archsurg.1992.01420090051008