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[Clinical case of the month. A recurrent chylothorax in Bourneville tuberous sclerosis].
- Source :
-
Revue medicale de Liege [Rev Med Liege] 2002 Aug; Vol. 57 (8), pp. 493-6. - Publication Year :
- 2002
-
Abstract
- Bourneville's disease, first described in 1862, is a phacomatosis that is either autosomal dominant or sporadic. Its typical clinical signs include mental retardation, epilepsy and cutaneous adenomas. The pulmonary form is rare, less than 1%, and is secondary to occlusion of the bronchus, vascular and lymphatics by immature smooth muscle cells. Chylothorax may appear in more than 50% of all cases. No guidelines currently exist for treatment of recurrent chylothorax. However, several possibilities are described in the literature.
- Subjects :
- Adult
Chylothorax epidemiology
Chylothorax therapy
Drainage
Female
Humans
Oxygen Inhalation Therapy
Practice Guidelines as Topic
Recurrence
Thoracostomy
Tomography, X-Ray Computed
Tuberous Sclerosis epidemiology
Tuberous Sclerosis genetics
Chylothorax diagnostic imaging
Chylothorax etiology
Tuberous Sclerosis complications
Subjects
Details
- Language :
- French
- ISSN :
- 0370-629X
- Volume :
- 57
- Issue :
- 8
- Database :
- MEDLINE
- Journal :
- Revue medicale de Liege
- Publication Type :
- Academic Journal
- Accession number :
- 12405020