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Severe lower limbs lymphedema of late onset revealing polysplenia syndrome--a case report.
- Source :
-
Angiology [Angiology] 2001 Jun; Vol. 52 (6), pp. 421-3. - Publication Year :
- 2001
-
Abstract
- Polysplenia syndrome includes a group of congenital abnormalities involving the spleen, gastrointestinal tract, liver, and cardiovascular system. A case of severe lower limbs lymphedema occurring in a young woman with polysplenia, azygous continuation of the inferior vena cava, short pancreas, and preduodenal portal vein is reported. Lower limb lymphedema could represent a new clinical manifestation associated with polysplenia syndrome. Lymphedema could be the result of a primary anomaly of the lymphatic system or be induced by high pressure in the venous system or by compression of the lymphatic circulation by the hypertrophic azygous vessels in the posterior mediastinum.
- Subjects :
- Adult
Cardiovascular System physiopathology
Chronic Disease
Diagnosis, Differential
Digestive System Abnormalities
Female
Humans
Leg
Mediastinum abnormalities
Portal Vein abnormalities
Severity of Illness Index
Syndrome
Tomography, X-Ray Computed
Vena Cava, Inferior abnormalities
Abnormalities, Multiple diagnosis
Liver abnormalities
Lymphedema etiology
Spleen abnormalities
Subjects
Details
- Language :
- English
- ISSN :
- 0003-3197
- Volume :
- 52
- Issue :
- 6
- Database :
- MEDLINE
- Journal :
- Angiology
- Publication Type :
- Academic Journal
- Accession number :
- 11437033
- Full Text :
- https://doi.org/10.1177/000331970105200608