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Choreoathetosis, hypothyroidism, and pulmonary alterations due to human NKX2-1 haploinsufficiency.

Authors :
Krude, Heiko
Schutz, Barbara
Biebermann, Heike
von Moers, Arpad
Schnabel, Dirk
Neitzel, Heidi
Tonnies, Holger
Weise, Dagmar
Lafferty, Antony
Schwarz, Siegfried
DeFelice, Mario
von Deimling, Andreas
van Landeghem, Frank
DiLauro, Roberto
Source :
Journal of Clinical Investigation. 2/15/2002, Vol. 109 Issue 4, p475. 6p.
Publication Year :
2002

Abstract

Describes five patients with variable degrees of congenital hypothyroidism who suffered from choreoathetosis, muscular hypotonia and pulmonary problems. Definition of choreoathetosis; Phenotype of NKX2-1 mutant patients; Position of aa exchange due to the NKX2-1 mutations and structural consequences for the DNA interaction.

Details

Language :
English
ISSN :
00219738
Volume :
109
Issue :
4
Database :
Academic Search Index
Journal :
Journal of Clinical Investigation
Publication Type :
Academic Journal
Accession number :
9043321
Full Text :
https://doi.org/10.1172/JCI200214341