Mitral Annular Disjunction with bileaflet mitral valve prolapse.

Mitral annular disjunction (MAD) is a structural abnormality of the mitral valve whereby there is a distinct separation of the mitral valve annulus-left atrial wall continuum and the basal portion of the posterolateral ventricular myocardium, a region which would normally be attached. It is usually associated with myxomatous mitral valve disease. MAD has been reported in various studies since the last four decades as constituting around 42-90% of patients with myxomatous mitral valve disease and mitral valve prolapse. It is often associated with arrhythmias ranging from benign ventricular ectopics to malignant ventricular fibrillations causing sudden cardiac deaths in the young. This condition seems to be more common in women. Last few decades have witnessed many case reports and prospective studies about this entity enhancing our understanding about its pathophysiology. We report a case of a 34 year old male with mitral valve prolapse and MAD resulting in severe mitral regurgitation who underwent mitral valve replacement. [ABSTRACT FROM AUTHOR]