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Understanding and managing a case of the omphalocele-exstrophy-imperforate anus-spinal defect complex.
- Source :
-
Journal of Surgical Case Reports . Mar2024, Vol. 2024 Issue 3, p1-3. 3p. - Publication Year :
- 2024
-
Abstract
- The omphalocele-exstrophy-imperforate anus-spinal defects (OEIS) complex is a rare birth disorder involving a combination of gastrointestinal, musculoskeletal, renal, neural, and genitourinary system defects. We present a case report of a neonate with OEIS born by vertex spontaneous delivery to non-consanguineous parents. The major presenting defect was exstrophy of the cecum lying between two exstrophied halves of the bladder, an imperforate anus and spina bifida myelomeningocele. Explorative laparotomy revealed a duplex kidney system, attachment of the terminal ileum and cecum to the exstrophy, and a sausage-like atretic large bowel. Malrotation was also noted. Ladd's bands were released followed by ileostomy and ureterostomy. Patient was stable post-operatively and in the incubator on room air. OEIS remains a challenging anomaly that requires optimal treatment to facilitate the quality of life. With appropriate surgical intervention, the functional and social treatment goals for this unusual congenital defect can be met. [ABSTRACT FROM AUTHOR]
Details
- Language :
- English
- ISSN :
- 20428812
- Volume :
- 2024
- Issue :
- 3
- Database :
- Academic Search Index
- Journal :
- Journal of Surgical Case Reports
- Publication Type :
- Academic Journal
- Accession number :
- 177084274
- Full Text :
- https://doi.org/10.1093/jscr/rjae166