Trans‐2,3‐enoyl‐CoA reductase‐like‐related catecholaminergic polymorphic ventricular tachycardia with regular ventricular tachycardia and response to flecainide.

Introduction: We describe a unique case of TECRL‐CPVT presented with cardiac arrest. Methods: Post resuscitation, the patient developed regular ventricular tachycardia featuring a left purkinje system morphology. Results: There was clear suppression of arrhythmia with the addition of flecainide and isolated ventricular ectopy causing secondary T‐wave changes. Conclusion: A high index of suspicion was required to eventually make the diagnosis through whole exome sequencing. [ABSTRACT FROM AUTHOR]