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Pulmonary hypertension in connective tissue diseases, new evidence and challenges.

Authors :
Vonk, Madelon C.
Vandecasteele, Els
Dijk, Arie P.
Source :
European Journal of Clinical Investigation. Apr2021, Vol. 51 Issue 4, p1-12. 12p.
Publication Year :
2021

Abstract

Pulmonary arterial hypertension is a lethal complication of different connective tissue diseases such as systemic sclerosis, mixed connective tissue disease and systemic lupus erythematosus. Although the treatment possibilities for patients with pulmonary arterial hypertension have increased in the last two decades and survival of patients with idiopathic pulmonary arterial hypertension has improved, the latter is not the case for patients with pulmonary arterial hypertension associated with connective tissue disease. In this narrative review, we review recent literature and describe the improvement of early diagnostic possibilities, screening modalities and treatment options. We also point out the pitfalls in diagnosis in this patient category and describe the unmet needs and what the focus of future research should be. [ABSTRACT FROM AUTHOR]

Details

Language :
English
ISSN :
00142972
Volume :
51
Issue :
4
Database :
Academic Search Index
Journal :
European Journal of Clinical Investigation
Publication Type :
Academic Journal
Accession number :
149219354
Full Text :
https://doi.org/10.1111/eci.13453