A Rare Case of Limited Cutaneous Systemic Sclerosis - A Case Report.

Limited cutaneous systemic sclerosis (lcSSc) is a sub-type of systemic sclerosis (SSc) characterized by association of Raynaud's phenomena with skin fibrosis limited to hand, face, feet and forearm. Manifests in females of 40-50 years (female: male - 4:1) with prevalence of 1/12500 adults. Disease originates from idiopathic auto-immune reaction leading to over production of collagen or with the chemical exposure. Prognosis of disease is relatively good with survival of 10 years in 80-90% patients. Complications of Pulmonary arterial hypertension and lung fibrosis have poor prognosis. [ABSTRACT FROM AUTHOR]