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Malignant triton tumor of the left thoracic cavity: a case report.

Authors :
Ishikawa, Masashi
Chou, Hiroyuki
Imamura, Naoto
Shimazu, Yumeta
Ono, Kazuo
Source :
Journal of Surgical Case Reports. Aug2019, Vol. 2019 Issue 8, pN.PAG-N.PAG. 1p.
Publication Year :
2019

Abstract

Malignant triton tumor (MTT) is a rare subtype of malignant peripheral nerve sheath tumors with rhabdomyoblastic differentiation. Although the condition may manifest sporadically, it typically affects adult patients with neurofibromatosis type 1. In this article, an extremely rare case of MTT with chest wall origin, which expanded into the left thoracic cavity, is reported. A 64-year-old male was admitted to the institution with sudden shortness of breath. Radiological examination revealed a large mass with massive pleural effusion occupying the patient's left hemithorax. A percutaneous needle biopsy was performed and the patient underwent subtotal tumor resection with left pleuropneumonectomy. Immunohistochemical study of postsurgical pathologic specimens confirmed the diagnosis of MTT. Despite extensive surgical removal, tumor recurrence was reported soon after resection, leading to patient's death 20 days after surgery due to acute respiratory failure. Investigation of rare MTT cases is necessary for understanding this condition. [ABSTRACT FROM AUTHOR]

Details

Language :
English
ISSN :
20428812
Volume :
2019
Issue :
8
Database :
Academic Search Index
Journal :
Journal of Surgical Case Reports
Publication Type :
Academic Journal
Accession number :
138873003
Full Text :
https://doi.org/10.1093/jscr/rjz246