Ablación renal por radiofrecuencia en una paciente con enfermedad de von Hippel-Lindau. Resultados y evolución.

Von Hippel-Lindau disease (VHL) is a rare entity (1/36.000 newborns), which is characterized by the occurrence of benign and malignant tumors in different regions. We present a case of a young VHL woman who developed several complications VHL related. Among them, multi and bilateral renal tumors of a mixt (cystic and solid) composition were noticed. Due to the fragile condition of the patient, it was decided to perform a radiofrequency ablation of the two bigger lesions (3.7 cm y 4.2 cm respectively).The subsequent result of the intraprocedural biopsy performed on the largest nodule confirmed the presumptive diagnosis showing confirmed the presence of a clear-cell tumor, stage 1 of Fuhrman. The procedure was technically successful reaching a complete coagulative necrosis of both tumors. The clinical evolution was uneventful with a clinic discharge on the following day. A CT scan two years later still confirms that the procedure has been successful. Renal function as estimated by the creatinine clearence (MDRD) was 119 at baseline and remains at 120 ml / min two years later. [ABSTRACT FROM AUTHOR]