41 results on '"Zagozdzon, Ilona"'
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2. Safety and Efficacy of Cinacalcet in Children Aged Under 3 Years on Maintenance Dialysis
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Bernardor, Julie, Flammier, Sacha, Zagozdzon, Ilona, Lalayiannis, Alexander D., Koster-Kamphuis, Linda, Verrina, Enrico, Dorresteijn, Eiske, Guzzo, Isabella, Haffner, Dieter, Shroff, Rukshana, Schmitt, Claus P., and Bacchetta, Justine
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- 2024
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3. FIBROMUSCULAR DYSPLASIA IN CHILDREN – A SINGLE-CENTER EXPERIENCE
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Skrzypczyk, Piotr, primary, Bujanowicz, Adam, additional, Ofiara, Anna, additional, Szyszka, Michal, additional, Tutka, Agnieszka, additional, Wabik, Anna Maria, additional, Zagozdzon, Ilona, additional, Krysiak, Remigiusz, additional, Zylkowski, Jaroslaw, additional, and Panczyk-tomaszewska, Malgorzata, additional
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- 2024
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4. Safety and efficacy of cinacalcet in children below 3 years of age on maintenance dialysis
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Bernardor, Julie, primary, Flammier, Sacha, additional, Zagozdzon, Ilona, additional, Lalayiannis, Alexander D., additional, Koster-Kamphuis, Linda, additional, Verrina, Enrico, additional, Dorresteijn, Eiske, additional, Guzzo, Isabella, additional, Haffner, Dieter, additional, Shroff, Rukshana, additional, Schmitt, Claus P., additional, and Bacchetta, Justine, additional
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- 2024
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5. Refining genotype–phenotype correlations in 304 patients with autosomal recessive polycystic kidney disease and PKHD1 gene variants
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Eid, Loai Akram, Arbeiter, Klaus, Godefroid, Nathalie, Lombet, Jacques, De Mul, Aurélie, Feldkoetter, Markus, Zieg, Jakub, Grundmann, Franziska, Galiano, Matthias, Buchholz, Björn, Buescher, Anja, Häffner, Karsten, Gross, Oliver, Patzer, Ludwig, Oh, Jun, Haffner, Dieter, Bernhardt, Wanja, Schaefer, Susanne, Wygoda, Simone, Halbritter, Jan, Derichs, Ute, Klaus, Günter, Lechner, Felix, Ponsel, Sabine, König, Jens, Staude, Hagen, Wurm, Donald, Bald, Martin, Gessner, Michaela, Soliman, Neveen A., Ariceta, Gema, Gonzalez Rodriguez, Juan David, Ojeda, Francisco de la Cerda, Harambat, Jerome, Morin, Denis, Dossier, Claire, Dorval, Guillaume, Shroff, Rukshana, Stabouli, Stella, Hooman, Nakysa, Mencarelli, Francesca, Morello, William, Longo, Germana, Emma, Francesco, Jankauskiene, Augustina, Taranta-Janusz, Katarzyna, Zagozdzon, Ilona, Zachwieja, Katarzyna, Stanczyk, Malgorzata, Bienias, Beata, Litwin, Mieczyslaw, Morawiec-Knysak, Aurelia, Afonso, Alberto Caldas, Dunand, Oliver, Rachisan, Andreea, Miloševski-Lomić, Gordana, Papizh, Svetlana, Rus, Rina, Jilani, Houweyda, Atmis, Bahriye, Duzova, Ali, Soylu, Alper, Candan, Cengiz, Caliskan, Salim, Yilmaz, Alev, Gökce, İbrahim, Akinci, Nurver, Mir, Sevgi, Dursun, Ismail, Tabel, Yilmaz, Nalcacioglu, Hulya, Burgmaier, Kathrin, Brinker, Leonie, Erger, Florian, Beck, Bodo B., Benz, Marcus R., Bergmann, Carsten, Boyer, Olivia, Collard, Laure, Dafinger, Claudia, Fila, Marc, Kowalewska, Claudia, Lange-Sperandio, Bärbel, Massella, Laura, Mastrangelo, Antonio, Mekahli, Djalila, Miklaszewska, Monika, Ortiz-Bruechle, Nadina, Prikhodina, Larisa, Ranchin, Bruno, Ranguelov, Nadejda, Schild, Raphael, Seeman, Tomas, Sever, Lale, Sikora, Przemyslaw, Szczepanska, Maria, Teixeira, Ana, Thumfart, Julia, Uetz, Barbara, Weber, Lutz Thorsten, Wühl, Elke, Zerres, Klaus, Dötsch, Jörg, Schaefer, Franz, and Liebau, Max Christoph
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- 2021
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6. Twenty years of growth hormone treatment in dialyzed children in Poland—Results of national multicenter study
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Adamczuk, Dominika, Leszczyńska, Beata, Skrzypczyk, Piotr, Turczyn, Agnieszka, Antonowicz, Agnieszka, Majcher, Anna, Szczepańska, Maria, Adamczyk, Piotr, Zagożdżon, Ilona, Żurowska, Aleksandra, Tkaczyk, Marcin, Jander, Anna, Sikora, Przemysław, Wasilewska, Anna, Warzywoda, Alfred, Kiliś-Pstrusińska, Katarzyna, Zwolińska, Danuta, Zachwieja, Katarzyna, Drożdż, Dorota, Stankiewicz, Roman, Grenda, Ryszard, and Pańczyk-Tomaszewska, Małgorzata
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- 2019
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7. Risk Factors for Early Dialysis Dependency in Autosomal Recessive Polycystic Kidney Disease
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Ranguelov, Nadejda, Godefroid, Nathalie, Collard, Laure, Lombet, Jacques, Maquet, Julie, Schalk, Gesa, Querfeld, Uwe, Beck, Bodo B., Benzing, Thomas, Buettner, Reinhard, Grundmann, Franziska, Kurschat, Christine, Benz, Kerstin, Tzschoppe, Anja, Buchholz, Björn, Buescher, Rainer, Häffner, Karsten, Pohl, Martin, Gross, Oliver, Krügel, Jenny, Stock, Johanna, Patzer, Ludwig, Oh, Jun, Bernhardt, Wanja, Doyon, Anke, Vinke, Tobias, Sander, Anja, Henn, Michael, Derichs, Ute, Beetz, Rolf, Jeck, Nikola, Lange-Sperandio, Bärbel, Ponsel, Sabine, Kusser, Franziska, Uetz, Barbara, Benz, Marcus, Schmidt, Silke, Huppertz-Kessler, Christina, Kranz, Birgitta, Titieni, Andrea, Wurm, Donald, Leichter, Heinz E., Bald, Martin, Billing, Heiko, Nabhan, Marwa M., Lara, Luis Enrique, Papachristou, Fotios, Emma, Francesco, Cerkauskiene, Rimante, Azukaitis, Karolis, Wasilewska, Anna, Balasz-Chmielewska, Irena, Miklaszewska, Monika, Tkaczyk, Marcin, Sikora, Przemyslaw, Zaniew, Marcin, Niemirska, Ania, Antoniewicz, Jolanta, Lesiak, Justyna, Afonso, Alberto Caldas, Teixeira, Ana, Milosevski-Lomic, Gordana, Paripović, Dusan, Peco-Antic, Amira, Papizh, Svetlana, Bayazit, Aysun Karabay, Anarat, Ali, Soylu, Alper, Kavukcu, Salih, Candan, Cengiz, Caliskan, Salim, Canpolat, Nur, Emre, Sevinc, Alpay, Harika, Akinci, Nurver, Conkar, Secil, Poyrazoglu, Hakan M., Dusunsel, Ruhan, Burgmaier, Kathrin, Kunzmann, Kevin, Ariceta, Gema, Bergmann, Carsten, Buescher, Anja Katrin, Burgmaier, Mathias, Dursun, Ismail, Duzova, Ali, Eid, Loai, Erger, Florian, Feldkoetter, Markus, Galiano, Matthias, Geßner, Michaela, Goebel, Heike, Gokce, Ibrahim, Haffner, Dieter, Hooman, Nakysa, Hoppe, Bernd, Jankauskiene, Augustina, Klaus, Guenter, König, Jens, Litwin, Mieczyslaw, Massella, Laura, Mekahli, Djalila, Melek, Engin, Mir, Sevgi, Pape, Lars, Prikhodina, Larisa, Ranchin, Bruno, Schild, Raphael, Seeman, Tomas, Sever, Lale, Shroff, Rukshana, Soliman, Neveen A., Stabouli, Stella, Stanczyk, Malgorzata, Tabel, Yilmaz, Taranta-Janusz, Katarzyna, Testa, Sara, Thumfart, Julia, Topaloglu, Rezan, Weber, Lutz Thorsten, Wicher, Dorota, Wühl, Elke, Wygoda, Simone, Yilmaz, Alev, Zachwieja, Katarzyna, Zagozdzon, Ilona, Zerres, Klaus, Dötsch, Jörg, Schaefer, Franz, and Liebau, Max Christoph
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- 2018
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8. Mortality risk disparities in children receiving chronic renal replacement therapy for the treatment of end-stage renal disease across Europe: an ESPN-ERA/EDTA registry analysis
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Chesnaye, Nicholas C, Schaefer, Franz, Bonthuis, Marjolein, Holman, Rebecca, Baiko, Sergey, Baskın, Esra, Bjerre, Anna, Cloarec, Sylvie, Cornelissen, Elisabeth A M, Espinosa, Laura, Heaf, James, Stone, Rosário, Shtiza, Diamant, Zagozdzon, Ilona, Harambat, Jérôme, Jager, Kitty J, Groothoff, Jaap W, and van Stralen, Karlijn J
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- 2017
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9. Growth Patterns After Kidney Transplantation in European Children Over the Past 25 Years: An ESPN/ERA-EDTA Registry Study
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Bonthuis, Marjolein, Groothoff, Jaap W., Ariceta, Gema, Baiko, Sergey, Battelino, Nina, Bjerre, Anna, Cransberg, Karlien, Kolvek, Gabriel, Maxwell, Heather, Miteva, Polina, Molchanova, Maria S., Neuhaus, Thomas J., Pape, Lars, Reusz, Gyorgy, Rousset-Rouviere, Caroline, Sandes, Ana Rita, Topaloglu, Rezan, Van Dyck, Maria, Ylinen, Elisa, Zagozdzon, Ilona, Jager, Kitty J., and Harambat, Jérôme
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- 2020
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10. Growth and nutritional status in children with chronic kidney disease on maintenance dialysis in Poland
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Stańczyk, Małgorzata, Miklaszewska, Monika, Zachwieja, Katarzyna, Wierciński, Ryszard, Stankiewicz, Roman, Firszt-Adamczyk, Agnieszka, Zachwieja, Jacek, Borzęcka, Hanna, Zagożdżon, Ilona, Ziółkowska, Helena, Leszczyńska, Beata, Medyńska, Anna, Adamczyk, Piotr, Szczepańska, Maria, and Tkaczyk, Marcin
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- 2016
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11. Do children with end-stage renal disease live shorter? Analysis of mortality on the basis of data from the Polish Registry of Renal Replacement Therapy in Children
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Zagożdżon, Ilona, Żurowska, Aleksandra, Prokurat, Sylwester, Rubik, Jacek, Drożdż, Dorota, Szczepańska, Maria, Warzywoda, Alfred, Jander, Anna, Ziółkowska, Helena, Makulska, Irena, Bieniaś, Beata, Kipigroch, Hanna, Wierciński, Ryszard, and Siteń, Grzegorz
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- 2015
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12. SODIUM BALANCE IN CHILDREN ON DIALYSIS: A MULTICENTER PROSPECTIVE STUDY FROM THE EUROPEAN PEDIATRIC DIALYSIS WORKING GROUP
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Zagozdzon, Ilona, Consolo, Silvia, Cruz, Alejandro, Jankauskiene, Augustina, Zaloszyc, Ariane, BAKKALOĞLU EZGÜ, SEVCAN AZİME, Edefonti, Alberto, Shroff, Rukshana, and Paglialonga, Fabio
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- 2022
13. Early childhood height-adjusted total kidney volume as a risk marker of kidney survival in ARPKD
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Nalcacioglu, Hulya, Dunand, Oliver, Mastrangelo, Antonio, Murer, Luisa, Emma, Francesco, Ruzgiene, Dovile, Taranta-Janusz, Katarzyna, Balasz-Chmielewska, Irena, Miklaszewska, Monika, Stanczyk, Malgorzata, Sikora, Przemyslaw, Kowalewska, Claudia, Szczepanska, Maria, Teixeira, Ana, Rachisan, Andreea, Papachristou, Fotios, Paripović, Dušan, Prikhodina, Larisa, Jilani, Houweyda, Bayazit, Aysun Karabay, Soylu, Alper, Candan, Cengiz, Sever, Lale, Emre, Sevinc, Cicek, Neslihan, Akinci, Nurver, Mir, Sevgi, Poyrazoğlu, Hakan M., Tabel, Yilmaz, Mencarelli, Francesca, Burgmaier, Kathrin, Kilian, Samuel, Arbeiter, Klaus, Atmis, Bahriye, Büscher, Anja, Derichs, Ute, Dursun, Ismail, Duzova, Ali, Eid, Loai Akram, Galiano, Matthias, Gessner, Michaela, Gokce, Ibrahim, Haeffner, Karsten, Hooman, Nakysa, Jankauskiene, Augustina, Körber, Friederike, Longo, Germana, Massella, Laura, Mekahli, Djalila, Miloševski-Lomić, Gordana, Rus, Rina, Shroff, Rukshana, Stabouli, Stella, Weber, Lutz T., Wygoda, Simone, Yilmaz, Alev, Zachwieja, Katarzyna, Zagozdzon, Ilona, Dötsch, Jörg, Schaefer, Franz, Liebau, Max Christoph, Potemkina, Alexandra, Ranguelov, Nadejda, Collard, Laure, De Mul, Aurélie, Feldkoetter, Markus, Seeman, Tomas, Zieg, Jakub, Thumfart, Julia, Grundmann, Franziska, Buchholz, Björn, Pape, Lars, Gross, Oliver, Patzer, Ludwig, Schild, Raphael, Haffner, Dieter, Bernhardt, Wanja, Wuehl, Elke, Henn, Michael, Halbritter, Jan, Klaus, Günter, Lechner, Felix, Lange-Sperandio, Bärbel, Uetz, Barbara, Benz, Marcus, König, Jens, Staude, Hagen, Wurm, Donald, Bald, Martin, Soliman, Neveen A., Ariceta, Gema, Rodriguez, Juan David Gonzalez, de la Cerda Ojeda, Francisco, Harambat, Jerome, Ranchin, Bruno, Fila, Marc, Dossier, Claire, Boyer, Olivia, Marlais, Matko, UCL - (SLuc) Département de pédiatrie, Ruzgienė, Dovilė, Burgmaier, Kathrin, Kilian, Samuel, Arbeiter, Klaus, Atmis, Bahriye, Buescher, Anja, Derichs, Ute, Dursun, Ismail, Duzova, Ali, Eid, Loai Akram, Galiano, Matthias, Gessner, Michaela, Gokce, Ibrahim, Haeffner, Karsten, Hooman, Nakysa, Jankauskiene, Augustina, Koerber, Friederike, Longo, Germana, Massella, Laura, Mekahli, Djalila, Milosevski-Lomic, Gordana, Nalcacioglu, Hulya, Rus, Rina, Shroff, Rukshana, Stabouli, Stella, Weber, Lutz T., Wygoda, Simone, Yilmaz, Alev, Zachwieja, Katarzyna, Zagozdzon, Ilona, Doetsch, Joerg, Schaefer, Franz, and Liebau, Max Christoph
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Liver Cirrhosis ,Male ,glomerulus filtration rate ,Medizin ,cell surface receptor ,preschool child ,DISEASE ,Cohort Studies ,Chronic kidney disease ,Polycystic kidney disease ,Medicine ,genetics ,Longitudinal Studies ,Child ,pathophysiology ,Ultrasonography ,Kidney ,Multidisciplinary ,longitudinal study ,organ size ,chronic kidney failure ,biological marker ,cohort analysis ,Prognosis ,Autosomal Recessive Polycystic Kidney Disease ,PKHD1 protein, human ,Multidisciplinary Sciences ,medicine.anatomical_structure ,female ,Quartile ,Child, Preschool ,Cohort ,Disease Progression ,Science & Technology - Other Topics ,Glomerular Filtration Rate ,medicine.medical_specialty ,kidney ,Adolescent ,Science ,Urology ,Renal function ,Kidney Volume ,Receptors, Cell Surface ,Article ,Humans ,ddc:610 ,human ,Renal Insufficiency, Chronic ,Polycystic Kidney, Autosomal Recessive ,Paediatric kidney disease ,Science & Technology ,business.industry ,echography ,Infant ,medicine.disease ,mortality ,kidney polycystic disease ,disease exacerbation ,physiology ,business ,metabolism ,Biomarkers ,Kidney disease - Abstract
Autosomal recessive polycystic kidney disease (ARPKD) is characterized by bilateral fibrocystic changes resulting in pronounced kidney enlargement. Impairment of kidney function is highly variable and widely available prognostic markers are urgently needed as a base for clinical decision-making and future clinical trials. In this observational study we analyzed the longitudinal development of sonographic kidney measurements in a cohort of 456 ARPKD patients from the international registry study ARegPKD. We furthermore evaluated correlations of sonomorphometric findings and functional kidney disease with the aim to describe the natural disease course and to identify potential prognostic markers. Kidney pole-to-pole (PTP) length and estimated total kidney volume (eTKV) increase with growth throughout childhood and adolescence despite individual variability. Height-adjusted PTP length decreases over time, but such a trend cannot be seen for height-adjusted eTKV (haeTKV) where we even observed a slight mean linear increase of 4.5 ml/m per year during childhood and adolescence for the overall cohort. Patients with two null PKHD1 variants had larger first documented haeTKV values than children with missense variants (median (IQR) haeTKV 793 (450–1098) ml/m in Null/null, 403 (260–538) ml/m in Null/mis, 230 (169–357) ml/m in Mis/mis). In the overall cohort, estimated glomerular filtration rate decreases with increasing haeTKV (median (IQR) haeTKV 210 (150–267) ml/m in CKD stage 1, 472 (266–880) ml/m in stage 5 without kidney replacement therapy). Strikingly, there is a clear correlation between haeTKV in the first eighteen months of life and kidney survival in childhood and adolescence with ten-year kidney survival rates ranging from 20% in patients of the highest to 94% in the lowest quartile. Early childhood haeTKV may become an easily obtainable prognostic marker of kidney disease in ARPKD, e.g. for the identification of patients for clinical studies. © 2021, The Author(s)., ESPN 2014.2; PKD Foundation, PKDF; Bundesministerium für Bildung und Forschung, BMBF: 01GM1515, 01GM1903; Universität zu Köln, UoC; Marga und Walter Boll-Stiftung; Universitätsklinikum Köln, We thank the German Society for Pediatric Nephrology (GPN), the ESCAPE Network, and the European Society for Paediatric Nephrology (ESPN; Working Groups CAKUT and Inherited Renal Diseases) for their support. ML was supported by grants of the GPN, ESPN (Grant ESPN 2014.2), and the German PKD foundation. KB and ML were supported by the Medical Faculty of the University of Cologne (Koeln Fortune program), and the Marga and Walter Boll-Foundation. FS and ML are supported by the German Federal Ministry of Research and Education (BMBF grant 01GM1515 and 01GM1903). This work was generated within the European Reference Network for Rare Kidney Disorders (ERKNet).
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- 2021
14. Perception of health-related quality of life in children with chronic kidney disease by the patients and their caregivers: Multicentre national study results
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Kiliś-Pstrusińska, Katarzyna, Medyńska, Anna, Chmielewska, Irena Bałasz, Grenda, Ryszard, Kluska-Jóźwiak, Agnieszka, Leszczyńska, Beata, Niedomagała, Julita, Olszak-Szot, Ilona, Miklaszewska, Monika, Szczepańska, Maria, Tkaczyk, Marcin, Urzykowska, Agnieszka, Wasilewska, Anna, Zachwieja, Katarzyna, Zajączkowska, Maria, Ziółkowska, Helena, Zagożdżon, Ilona, and Zwolińska, Danuta
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- 2013
15. Demographics of paediatric renal replacement therapy in Europe: a report of the ESPN/ERA-EDTA registry
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Chesnaye, Nicholas, Bonthuis, Marjolein, Schaefer, Franz, Groothoff, Jaap W., Verrina, Enrico, Heaf, James G., Jankauskiene, Augustina, Lukosiene, Viktorija, Molchanova, Elena A., Mota, Conceicao, Peco-Antic, Amira, Ratsch, Ilse-Maria, Bjerre, Anna, Roussinov, Dimitar L., Sukalo, Alexander, Topaloglu, Rezan, Van Hoeck, Koen, Zagozdzon, Ilona, Jager, Kitty J., and Van Stralen, Karlijn J.
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Chronic kidney failure -- Demographic aspects -- Care and treatment -- Research ,Health - Abstract
Background The ESPN/ERA-EDTA Registry collects data on European children with end-stage renal disease receiving renal replacement therapy (RRT) who are listed on national and regional renal registries in Europe. In this paper we report on the analysis of demographic data collected from 2009 to 2011. Methods Data on primary renal disease, incidence, prevalence, 4-year survival, transplantation rate and causes of death in paediatric patients receiving RRT were extracted from the ESPN/ERA-EDTA Registry for 37 European countries. Results The incidence of RRT in paediatric patients in Europe during the study period was 5.5 cases per million age-related population (pmarp) in patients aged 0-14 years and varied markedly between countries (interquartile range 3.4 7.0 years). The prevalence of RRT was 27.9 pmarp and increased with age, with 67% of prevalent patients living with a functioning graft. The probability of receiving a transplant within 4 years was 76.9% and was lowest in patients aged 0-4 years (68.9%). Mortality in paediatric patients treated with RRT was 55-fold higher than that of the general EU paediatric population. Overall survival at 4 years was 93.7%, with the poorest survival in patients aged 0-4 years and in patients starting on dialysis. Infections (19.9%) were the primary cause of death in European paediatric RRT patients. Conclusion Considerable variation exists in the current demographics of children treated with RRT across Europe. Keywords Paediatrics * Renal replacement therapy * Chronic kidney failure * Europe * Incidence * Prevalence * Survival, Introduction End-stage renal disease (ESRD) is a very rare condition in children [1]. Information on the number of new cases (incidence), the size of the problem (prevalence) and the outcomes [...]
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- 2014
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16. EARLY CHILDHOOD HEIGHT-ADJUSTED TOTAL KIDNEY VOLUME AS A RISK MARKER OF KIDNEY SURVIVAL IN AUTOSOMAL RECESSIVE POLYCYSTIC KIDNEY DISEASE (ARPKD)
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Burgmaier, Kathrin, Kilian, Samuel, Arbeiter, Klaus, Atmis, Bahriye, Buescher, Anja, Derichs, Ute, Dursun, Ismail, Duzova, Ali, Eid, Loai, Galiano, Matthias, Gessner, Michaela, Gokce, Ibrahim, Haeffner, Karsten, Hooman, Nakysa, Jankauskiene, Augustina, Koerber, Friederike, Longo, Germana, Massella, Laura, Mekahli, Djalila, Milosevski-Lomic, Gordana, Hulya Nalcacioglu, Rus, Rina, Shroff, Rukshana, Stabouli, Stella, Weber, Lutz, Wygoda, Simone, Yilmaz, Alev, Zachwieja, Katarzyna, Zagozdzon, Ilona, Doetsch, Joerg, Schaefer, Franz, and Liebau, Max Christoph
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- 2021
17. Psychosocial aspects of children and families of children treated with automated peritoneal dialysis
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Kilis-Pstrusinska, Katarzyna, Wasilewska, Anna, Medynska, Anna, Balasz-Chmielewska, Irena, Grenda, Ryszard, Kluska-Jozwiak, Agnieszka, Leszczynska, Beata, Olszak-Szot, Ilona, Miklaszewska, Monika, Szczepanska, Maria, Tkaczyk, Marcin, Urzykowska, Agnieszka, Zachwieja, Katarzyna, Zajaczkowska, Maria, Ziolkowska, Helena, Zagozdzon, Ilona, and Zwolinska, Danuta
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Continuous ambulatory peritoneal dialysis -- Methods -- Patient outcomes ,Children -- Diseases ,Parents -- Surveys -- Psychological aspects -- Social aspects ,Peritoneal dialysis -- Methods -- Patient outcomes ,Kidney diseases -- Care and treatment -- Psychological aspects -- Social aspects ,Hemodialysis patients -- Demographic aspects -- Family -- Care and treatment ,Caregivers -- Surveys ,Quality of life -- Surveys -- Health aspects ,Health - Abstract
Background The aim of this study was to analyze psychosocial aspects of chronic kidney disease (CKD) in children treated with automated peritoneal dialysis (APD). Methods The study assessed 41 children > 2 (range 2.1-18) years of age and their parents. Data concerning the illness and sociodemographic parameters were collected. Patients completed the Paediatric Quality of Life Inventory (PedsQL) and their parents the PedsQL-proxy version, General Health Questionnaire (GHQ-12), Berlin Social Support Scales (BSSS), and Caregiver's Burden Scale (CBS). Results Parents rated their children's overall health-related quality of life (QoL) as well as their physical and emotional functioning lower than the patients themselves. The majority of primary caregivers had a medium level of the total burden index in the CBS and higher values in the scales need for support and perceived available support than in the received support (BSSS). In the GHQ-12, 51.2% of primary caregivers had scores >2 points, which indicated the possible occurrence of abnormal mental functioning. Conclusions Financial support for patients' families is necessary. Parents who provide primary care to children on PD require, above all, emotional support and assistance in self-fulfilment. More than half of them may have impaired mental function. There is the strong need to provide continuous psychological care for caregivers. Differences in perception of the children's activity in varied areas by the patients themselves and their caregivers may contribute to further problems within families. Keywords Children * Peritoneal dialysis * Health-related quality of life * Parents' perceived burdens * Primary caregivers, Introduction Home peritoneal dialysis (PD) is the preferred chronic dialysis modality for children with end-stage renal disease (ESRD) [1]. Thanks to technological advances, inter alia, various PD regimens and solutions, [...]
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- 2013
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18. Severe neurological outcomes after very early bilateral nephrectomies in patients with autosomal recessive polycystic kidney disease (ARPKD)
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Häffner, Karsten, Gross, Oliver, Bernhardt, Wanja, Doyon, Anke, Henn, Michael, Halbritter, Jan, Derichs, Ute, Klaus, Günter, Lange-Sperandio, Bärbel, Uetz, Barbara, Benz, Marcus, Titieni, Andrea, Staude, Hagen, Leichter, Heinz E., Soliman, Neveen A., Lara, Luis Enrique, de la Cerda Ojeda, Francisco, Harambat, Jerome, Ranchin, Bruno, Fila, Marc, Dossier, Claire, Boyer, Olivia, Stabouli, Stella, Hooman, Nakysa, Mencarelli, Francesca, Morello, William, Longo, Germana, Emma, Francesco, Ruzgiene, Dovile, Wasilewska, Anna, Balasz-Chmielewska, Irena, Miklaszewska, Monika, Stanczyk, Malgorzata, Sikora, Przemyslaw, Litwin, Mieczyslaw, Morawiec-Knysak, Aurelia, Teixeira, Ana, Milosevski-Lomic, Gordana, Prikhodina, Larisa, Rus, Rina, Jilani, Houweyda, Melek, Engin, Duzova, Ali, Candan, Cengiz, Sever, Lale, Ranguelov, Nadejda, Yilmaz, Alev, Cicek, Neslihan, Akinci, Nurver, Mir, Sevgi, Dursun, Ismail, Tabel, Yilmaz, Nalcacioglu, Hulya, Shroff, Rukshana, Marlais, Matko, Soylu, Alper, Arbeiter, Klaus, Eid, Loai Akram, Liebau, Max Christoph, Schaefer, Franz, Oh, Jun, Dötsch, Jörg, Zagozdzon, Ilona, Wygoda, Simone, Wurm, Donald, Wühl, Elke, Weber, Lutz Thorsten, Tkaczyk, Marcin, Burgmaier, Kathrin, Ariceta, Gema, Bald, Martin, Buescher, Anja Katrin, Burgmaier, Mathias, Erger, Florian, Gessner, Michaela, GÖKCE, İBRAHİM, König, Jens, Kowalewska, Claudia, Massella, Laura, Mastrangelo, Antonio, Mekahli, Djalila, Pape, Lars, Patzer, Ludwig, Potemkina, Alexandra, Schalk, Gesa, Schild, Raphael, Szczepanska, Maria, Taranta-Janusz, Katarzyna, Collard, Laure, De Mul, Aurélie, Feldkoetter, Markus, Seeman, Tomas, Thumfart, Julia, Grundmann, Franziska, Galiano, Matthias, Buchholz, Björn, Buescher, Rainer, UCL - (SLuc) Service de pédiatrie générale, De Mul, Aurélie, Burgmaier, Kathrin, Ariceta, Gema, Bald, Martin, Buescher, Anja Katrin, Burgmaier, Mathias, Erger, Florian, Gessner, Michaela, Gokce, Ibrahim, Koenig, Jens, Kowalewska, Claudia, Massella, Laura, Mastrangelo, Antonio, Mekahli, Djalila, Pape, Lars, Patzer, Ludwig, Potemkina, Alexandra, Schalk, Gesa, Schild, Raphael, Shroff, Rukshana, Szczepanska, Maria, Taranta-Janusz, Katarzyna, Tkaczyk, Marcin, Weber, Lutz Thorsten, Wuehl, Elke, Wurm, Donald, Wygoda, Simone, Zagozdzon, Ilona, Doetsch, Joerg, Oh, Jun, Schaefer, Franz, Liebau, Max Christoph, and Ege Üniversitesi
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Male ,Pediatrics ,medicine.medical_treatment ,Medizin ,030232 urology & nephrology ,INFANTS ,lcsh:Medicine ,Nephrectomy ,RECOMMENDATIONS ,Cohort Studies ,0302 clinical medicine ,Postoperative Complications ,Risk Factors ,HYPOTENSION ,Polycystic Kidney ,Medicine ,UNILATERAL NEPHRECTOMY ,ENCODES ,lcsh:Science ,Renal Dialysis/statistics & numerical data ,PERITONEAL-DIALYSIS ,Kidney ,ddc:618 ,Multidisciplinary ,Autosomal recessive polycystic kidney disease (ARPKD) ,Autosomal Recessive Polycystic Kidney Disease ,medicine.anatomical_structure ,Cohort ,ARegPKD consortium ,Disease Progression ,Female ,Cohort study ,Nephrectomy/adverse effects ,medicine.medical_specialty ,Renal function ,MATURATION ,Article ,03 medical and health sciences ,Polycystic kidney disease ,Renal Dialysis ,030225 pediatrics ,MANAGEMENT ,Humans ,In patient ,Dialysis ,Polycystic Kidney, Autosomal Recessive ,Nervous System Diseases/epidemiology/etiology ,Autosomal Recessive/surgery ,Paediatric kidney disease ,business.industry ,lcsh:R ,1ST YEAR ,NEUROPATHY ,Infant, Newborn ,Infant ,Newborn ,medicine.disease ,Postoperative Complications/epidemiology/etiology ,lcsh:Q ,Nervous System Diseases ,business - Abstract
To test the association between bilateral nephrectomies in patients with autosomal recessive polycystic kidney disease (ARPKD) and long-term clinical outcome and to identify risk factors for severe outcomes, a dataset comprising 504 patients from the international registry study ARegPKD was analyzed for characteristics and complications of patients with very early (? 3 months; VEBNE) and early (4–15 months; EBNE) bilateral nephrectomies. Patients with very early dialysis (VED, onset ? 3 months) without bilateral nephrectomies and patients with total kidney volumes (TKV) comparable to VEBNE infants served as additional control groups. We identified 19 children with VEBNE, 9 with EBNE, 12 with VED and 11 in the TKV control group. VEBNE patients suffered more frequently from severe neurological complications in comparison to all control patients. Very early bilateral nephrectomies and documentation of severe hypotensive episodes were independent risk factors for severe neurological complications. Bilateral nephrectomies within the first 3 months of life are associated with a risk of severe neurological complications later in life. Our data support a very cautious indication of very early bilateral nephrectomies in ARPKD, especially in patients with residual kidney function, and emphasize the importance of avoiding severe hypotensive episodes in this at-risk cohort. © 2020, The Author(s)., Marga und Walter Boll-Stiftung Universität zu Köln, UoC Bundesministerium für Bildung und Forschung, BMBF: 01GM1903, 01GM1515 PKD Foundation, PKDF European Paediatric Neurology Society, EPNS, We thank the German Society for Pediatric Nephrology (GPN) and the ESCAPE Network for their support. ML was supported by grants of the GPN, the European Society for Paediatric Nephrology (ESPN), the German PKD foundation, the Koeln Fortune program, the GEROK program of the Medical Faculty of University of Cologne, and the Marga and Walter Boll-Foundation. FS and ML are supported by the the German Federal Ministry of Research and Education (BMBF grant 01GM1515 and 01GM1903). KB was supported by the Koeln Fortune program of the Medical Faculty of University of Cologne and the Marga and Walter Boll-Foundation. This work was generated within the European Reference Network for Rare Kidney Disorders (ERKNet). Open Access funding provided by Projekt DEAL.
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- 2020
19. Refining genotype–phenotype correlations in 304 patients with autosomal recessive polycystic kidney disease and PKHD1 gene variants
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Burgmaier, Kathrin, primary, Brinker, Leonie, additional, Erger, Florian, additional, Beck, Bodo B., additional, Benz, Marcus R., additional, Bergmann, Carsten, additional, Boyer, Olivia, additional, Collard, Laure, additional, Dafinger, Claudia, additional, Fila, Marc, additional, Kowalewska, Claudia, additional, Lange-Sperandio, Bärbel, additional, Massella, Laura, additional, Mastrangelo, Antonio, additional, Mekahli, Djalila, additional, Miklaszewska, Monika, additional, Ortiz-Bruechle, Nadina, additional, Patzer, Ludwig, additional, Prikhodina, Larisa, additional, Ranchin, Bruno, additional, Ranguelov, Nadejda, additional, Schild, Raphael, additional, Seeman, Tomas, additional, Sever, Lale, additional, Sikora, Przemyslaw, additional, Szczepanska, Maria, additional, Teixeira, Ana, additional, Thumfart, Julia, additional, Uetz, Barbara, additional, Weber, Lutz Thorsten, additional, Wühl, Elke, additional, Zerres, Klaus, additional, Dötsch, Jörg, additional, Schaefer, Franz, additional, Liebau, Max Christoph, additional, Eid, Loai Akram, additional, Arbeiter, Klaus, additional, Godefroid, Nathalie, additional, Lombet, Jacques, additional, De Mul, Aurélie, additional, Feldkoetter, Markus, additional, Zieg, Jakub, additional, Grundmann, Franziska, additional, Galiano, Matthias, additional, Buchholz, Björn, additional, Buescher, Anja, additional, Häffner, Karsten, additional, Gross, Oliver, additional, Oh, Jun, additional, Haffner, Dieter, additional, Bernhardt, Wanja, additional, Schaefer, Susanne, additional, Wygoda, Simone, additional, Halbritter, Jan, additional, Derichs, Ute, additional, Klaus, Günter, additional, Lechner, Felix, additional, Ponsel, Sabine, additional, König, Jens, additional, Staude, Hagen, additional, Wurm, Donald, additional, Bald, Martin, additional, Gessner, Michaela, additional, Soliman, Neveen A., additional, Ariceta, Gema, additional, Gonzalez Rodriguez, Juan David, additional, Ojeda, Francisco de la Cerda, additional, Harambat, Jerome, additional, Morin, Denis, additional, Dossier, Claire, additional, Dorval, Guillaume, additional, Shroff, Rukshana, additional, Stabouli, Stella, additional, Hooman, Nakysa, additional, Mencarelli, Francesca, additional, Morello, William, additional, Longo, Germana, additional, Emma, Francesco, additional, Jankauskiene, Augustina, additional, Taranta-Janusz, Katarzyna, additional, Zagozdzon, Ilona, additional, Zachwieja, Katarzyna, additional, Stanczyk, Malgorzata, additional, Bienias, Beata, additional, Litwin, Mieczyslaw, additional, Morawiec-Knysak, Aurelia, additional, Afonso, Alberto Caldas, additional, Dunand, Oliver, additional, Rachisan, Andreea, additional, Miloševski-Lomić, Gordana, additional, Papizh, Svetlana, additional, Rus, Rina, additional, Jilani, Houweyda, additional, Atmis, Bahriye, additional, Duzova, Ali, additional, Soylu, Alper, additional, Candan, Cengiz, additional, Caliskan, Salim, additional, Yilmaz, Alev, additional, Gökce, İbrahim, additional, Akinci, Nurver, additional, Mir, Sevgi, additional, Dursun, Ismail, additional, Tabel, Yilmaz, additional, and Nalcacioglu, Hulya, additional
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- 2021
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20. P182125 YEARS OF GROWTH HORMONE TREATMENT IN CHILDREN WITH CHRONIC KIDNEY DISEASE IN POLAND - RESULTS OF NATIONAL MULTICENTER STUDY
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Leszczyńska, Beata, primary, Daniel, Maria, primary, Majcher, Anna, primary, Pyrzak, Beata, primary, Szczepanska, Maria, primary, Zagozdzon, Ilona, primary, Jander, Anna, primary, Tkaczyk, Marcin, primary, Sikora, Przemysław, primary, Wasilewska, Anna, primary, Zachwieja, Katarzyna, primary, Miklaszewska, Monika, primary, Stankiewicz, Roman, primary, Jarmuzek, Wioletta, primary, Rubik, Jacek, primary, Makulska, Irena, primary, and Pańczyk-Tomaszewska, Małgorzata, primary
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- 2020
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21. Influenza and pneumococcus vaccination rates in pediatric dialysis patients in Europe: recommendations vs reality A European Pediatric Dialysis Working Group and European Society for Pediatric Nephrology Dialysis Working Group study.
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ATİKEL, Yeşim Özdemir, BAKKALOĞLU, Sevcan A., PAGLIALONGA, Fabio, STEFANIDIS, Constantinos J., ASKITI, Varvara, VIDAL, Enrico, ARICETA, Gema, MELEK, Engin, VERRINA, Enrico, PRINTZA, Nikoleta, VONDRAK, Karel, ZUROWSKA, Aleksandra, ZAGOZDZON, Ilona, EKİM, Mesiha, ÖZMERT, Elif Nursel, DUFEK, Stephanie, JANKAUSKIENE, Augustina, SCHMITT, Claus Peter, LÉVAI, Eszter, and WALLE, Johan Vande
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INFLUENZA ,HEMODIALYSIS patients ,INFLUENZA vaccines ,PEDIATRIC nephrology ,FLU vaccine efficacy ,PNEUMOCOCCAL vaccines - Abstract
Background/aim: Children on dialysis are under increased risk of influenza and invasive pneumococcal disease. Although vaccination against these microorganisms are recommended in dialysis patients and despite the fact that these vaccines can reduce disease burden and rates of hospitalization due to infection, vaccination rates are below expected and desired. We aimed to evaluate influenza and pneumococcal vaccination and infection rates in European pediatric dialysis centers. Materials and methods: In 16 centers from 11 countries, 357 pediatric dialysis patients were evaluated retrospectively during 1 year of observation period between 01.01.2014 and 01.01.2015. Results: In all centers, vaccination policy included immunization of dialysis patients with inactive influenza vaccine and pneumococcal conjugate vaccine (PCV). Fifty percent of the centers recommended pneumococcal polysaccharide vaccine following routine PCV series. A significantly higher pneumococcal vaccination rate (43.9%) was seen in peritoneal dialysis (PD) patients compared to those on hemodialysis (HD) (32.9%) (p = 0.035), while the rates for influenza were similar (42.4% and 46.1% respectively, p = 0.496). Among all dialysis patients, 2.2% (n = 8) developed pneumonia and 6.4% (n = 23) was infected by Influenza. Pneumococcic pneumonia rate was 5% for 140 patients who received antipneumococcal vaccine, while only one pneumonia episode was recorded out of 217 unvaccinated patients (p = 0.007). The influenza virus infection rates were similar for patients vaccinated and nonvaccinated (7 % and 6 %, respectively). Conclusions: Although influenza and pneumococcal vaccines are highly recommended in pediatric dialysis patients, vaccination rates were lower than expected. Pneumococcal vaccination rates were higher in PD compared to the patients on HD. The rate of children with influenza infection was higher than pneumonia. The efficacy of influenza and pneumococcal vaccines was highlighted by the low infection rates. Higher pneumonia rates in patients vaccinated against pneumococcus compared to unvaccinated ones might be due to coexisting risk factors. [ABSTRACT FROM AUTHOR]
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- 2021
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22. ICODEXTRIN SOLUTION IN ANURIC CHILDREN TREATED WITH AUTOMATED PERITONEAL DIALYSIS
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Balasz, Irena, Zurowska, Aleksandra, Zagozdzon, Ilona, Lesniewska, Iga, and Marczak, Ewa
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- 2003
23. RELATIVE PREVALENCE OF GRAM NEGATIVE PERITONITIS IN CHILDREN ON AUTOMATED PERITONEAL DIALYSIS AND ST.AUREUS PROPHYLAXIS
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Zurowska, Aleksandra, Zagozdzon, Ilona, Balasz, Irena, and Lesniewska, Iga
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- 2003
24. Association between timing of dialysis initiation and clinical outcomes in the paediatric population: an ESPN/ERA-EDTA registry study
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Preka, Evgenia, primary, Bonthuis, Marjolein, additional, Harambat, Jerome, additional, Jager, Kitty J, additional, Groothoff, Jaap W, additional, Baiko, Sergey, additional, Bayazit, Aysun K, additional, Boehm, Michael, additional, Cvetkovic, Mirjana, additional, Edvardsson, Vidar O, additional, Fomina, Svitlana, additional, Heaf, James G, additional, Holtta, Tuula, additional, Kis, Eva, additional, Kolvek, Gabriel, additional, Koster-Kamphuis, Linda, additional, Molchanova, Elena A, additional, Muňoz, Marina, additional, Neto, Gisela, additional, Novljan, Gregor, additional, Printza, Nikoleta, additional, Sahpazova, Emilija, additional, Sartz, Lisa, additional, Sinha, Manish D, additional, Vidal, Enrico, additional, Vondrak, Karel, additional, Vrillon, Isabelle, additional, Weber, Lutz T, additional, Weitz, Marcus, additional, Zagozdzon, Ilona, additional, Stefanidis, Constantinos J, additional, and Bakkaloglu, Sevcan A, additional
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- 2019
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25. AVRUPA DAKİ ÇOCUK NEFROLOJİ MERKEZLERİNDE DİYALİZ HASTALARININ AŞILANMA DURUMU
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SCHMIT, CP, PAGLIALONGA, FABIO, BAKKALOĞLU EZGÜ, SEVCAN AZİME, EDEFONTI, ALBERTO, FISCHBACH, MICHEL, HOLTTA, TUULA, WANDEWALLE, JOHAN, JANKAUSİKENE, AUGUSTINA, DUFEK, STEFAINE, SHROFF, rukshana, EKİM, MESİHA, ZAGOZDZON, ILONA, ZUROWSKA, ALEXANDRA, VONDRAK, KAREL, PRINTZA, NICOLETA, VERRINA, ENRICO, MELEK, ENGİN, ARICETA, GEMA, ASCITI, VA, STEFANIDIS, CJ, VIDAL, ENRICO, and ÖZDEMİR, YEŞİM
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- 2016
26. Risk Factors for Early Dialysis Dependency in Autosomal Recessive Polycystic Kidney Disease
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Burgmaier, Kathrin, primary, Kunzmann, Kevin, additional, Ariceta, Gema, additional, Bergmann, Carsten, additional, Buescher, Anja Katrin, additional, Burgmaier, Mathias, additional, Dursun, Ismail, additional, Duzova, Ali, additional, Eid, Loai, additional, Erger, Florian, additional, Feldkoetter, Markus, additional, Galiano, Matthias, additional, Geßner, Michaela, additional, Goebel, Heike, additional, Gokce, Ibrahim, additional, Haffner, Dieter, additional, Hooman, Nakysa, additional, Hoppe, Bernd, additional, Jankauskiene, Augustina, additional, Klaus, Guenter, additional, König, Jens, additional, Litwin, Mieczyslaw, additional, Massella, Laura, additional, Mekahli, Djalila, additional, Melek, Engin, additional, Mir, Sevgi, additional, Pape, Lars, additional, Prikhodina, Larisa, additional, Ranchin, Bruno, additional, Schild, Raphael, additional, Seeman, Tomas, additional, Sever, Lale, additional, Shroff, Rukshana, additional, Soliman, Neveen A., additional, Stabouli, Stella, additional, Stanczyk, Malgorzata, additional, Tabel, Yilmaz, additional, Taranta-Janusz, Katarzyna, additional, Testa, Sara, additional, Thumfart, Julia, additional, Topaloglu, Rezan, additional, Weber, Lutz Thorsten, additional, Wicher, Dorota, additional, Wühl, Elke, additional, Wygoda, Simone, additional, Yilmaz, Alev, additional, Zachwieja, Katarzyna, additional, Zagozdzon, Ilona, additional, Zerres, Klaus, additional, Dötsch, Jörg, additional, Schaefer, Franz, additional, Liebau, Max Christoph, additional, Ranguelov, Nadejda, additional, Godefroid, Nathalie, additional, Collard, Laure, additional, Lombet, Jacques, additional, Maquet, Julie, additional, Schalk, Gesa, additional, Querfeld, Uwe, additional, Beck, Bodo B., additional, Benzing, Thomas, additional, Buettner, Reinhard, additional, Grundmann, Franziska, additional, Kurschat, Christine, additional, Benz, Kerstin, additional, Tzschoppe, Anja, additional, Buchholz, Björn, additional, Buescher, Rainer, additional, Häffner, Karsten, additional, Pohl, Martin, additional, Gross, Oliver, additional, Krügel, Jenny, additional, Stock, Johanna, additional, Patzer, Ludwig, additional, Oh, Jun, additional, Bernhardt, Wanja, additional, Doyon, Anke, additional, Vinke, Tobias, additional, Sander, Anja, additional, Henn, Michael, additional, Derichs, Ute, additional, Beetz, Rolf, additional, Jeck, Nikola, additional, Lange-Sperandio, Bärbel, additional, Ponsel, Sabine, additional, Kusser, Franziska, additional, Uetz, Barbara, additional, Benz, Marcus, additional, Schmidt, Silke, additional, Huppertz-Kessler, Christina, additional, Kranz, Birgitta, additional, Titieni, Andrea, additional, Wurm, Donald, additional, Leichter, Heinz E., additional, Bald, Martin, additional, Billing, Heiko, additional, Nabhan, Marwa M., additional, Lara, Luis Enrique, additional, Papachristou, Fotios, additional, Emma, Francesco, additional, Cerkauskiene, Rimante, additional, Azukaitis, Karolis, additional, Wasilewska, Anna, additional, Balasz-Chmielewska, Irena, additional, Miklaszewska, Monika, additional, Tkaczyk, Marcin, additional, Sikora, Przemyslaw, additional, Zaniew, Marcin, additional, Niemirska, Ania, additional, Antoniewicz, Jolanta, additional, Lesiak, Justyna, additional, Afonso, Alberto Caldas, additional, Teixeira, Ana, additional, Milosevski-Lomic, Gordana, additional, Paripović, Dusan, additional, Peco-Antic, Amira, additional, Papizh, Svetlana, additional, Bayazit, Aysun Karabay, additional, Anarat, Ali, additional, Soylu, Alper, additional, Kavukcu, Salih, additional, Candan, Cengiz, additional, Caliskan, Salim, additional, Canpolat, Nur, additional, Emre, Sevinc, additional, Alpay, Harika, additional, Akinci, Nurver, additional, Conkar, Secil, additional, Poyrazoglu, Hakan M., additional, and Dusunsel, Ruhan, additional
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- 2018
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27. Vaccination Practices in Pediatric Dialysis Patients Across Europe. A European Pediatric Dialysis Working Group and European Society for Pediatric Nephrology Dialysis Working Group Study
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Bakkaloğlu, Sevcan A., primary, Özdemir Atikel, Yesim, additional, Paglialonga, Fabio, additional, Stefanidis, Constantinos J., additional, Askiti, Varvara, additional, Vidal, Enrico, additional, Ariceta, Gema, additional, Melek, Engin, additional, Verrina, Enrico, additional, Printza, Nikoleta, additional, Vondrak, Karel, additional, Zurowska, Aleksandra, additional, Zagozdzon, Ilona, additional, Ekim, Mesiha, additional, Özmert, Elif Nursel, additional, Dufek, Stephanie, additional, Jankauskiene, Augustina, additional, Schmitt, Claus Peter, additional, Lévai, Eszter, additional, Vande Walle, Johan, additional, Canpolat, Nur, additional, Holtta, Tuula, additional, Fischbach, Michel, additional, Klaus, Guenter, additional, Aufricht, Christoph, additional, Shroff, Rukshana, additional, and Edefonti, Alberto, additional
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- 2017
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28. Difficulties in diagnosing severe Pneumocystis jiroveci pneumonia after rituximab therapy for steroid-dependent nephrotic syndrome
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Czarniak, Piotr, Zaluska-Lesniewska, Iga, Zagozdzon, Ilona, and Zurowska, Aleksandra
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Pneumocystis carinii pneumonia -- Causes of -- Diagnosis -- Research ,Nephrotic syndrome -- Drug therapy -- Patient outcomes -- Research ,Health - Abstract
Dear Editors, We read with great interest the article by Sato et al., recently published in Pediatric Nephrology, who presented a patient with atypical Pneumocystis jiroveci pneumonia (PCP) with multiple [...]
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- 2013
29. Mortality risk in European children with end-stage renal disease on dialysis
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Chesnaye, Nicholas C., primary, Schaefer, Franz, additional, Groothoff, Jaap W., additional, Bonthuis, Marjolein, additional, Reusz, György, additional, Heaf, James G., additional, Lewis, Malcolm, additional, Maurer, Elisabeth, additional, Paripović, Dušan, additional, Zagozdzon, Ilona, additional, van Stralen, Karlijn J., additional, and Jager, Kitty J., additional
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- 2016
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30. SO057MORTALITY RISK IN EUROPEAN CHILDREN WITH END-STAGE RENAL DISEASE ON DIALYSIS RESULTS FROM THE ESPN/ERA-EDTA REGISTRY
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Chesnaye, Nicholas, primary, Schaefer, Franz, additional, Groothoff, Jaap W., additional, Bonthuis, Marjolein, additional, Reusz, Gyorgy, additional, Heaf, James G., additional, Lewis, Malcolm, additional, Maurer, Elisabeth, additional, Paripović, Dušan, additional, Zagozdzon, Ilona, additional, van Stralen, Karlijn J, additional, and Jager, Kitty J, additional
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- 2016
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31. Vaccination Practices in Pediatric Dialysis Patients Across Europe. A European Pediatric Dialysis Working Group and European Society for Pediatric Nephrology Dialysis Working Group Study
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Bakkaloğlu, Sevcan A., Özdemir Atikel, Yesim, Paglialonga, Fabio, Stefanidis, Constantinos J., Askiti, Varvara, Vidal, Enrico, Ariceta, Gema, Melek, Engin, Verrina, Enrico, Printza, Nikoleta, Vondrak, Karel, Zurowska, Aleksandra, Zagozdzon, Ilona, Ekim, Mesiha, Özmert, Elif Nursel, Dufek, Stephanie, Jankauskiene, Augustina, Schmitt, Claus Peter, Lévai, Eszter, Vande Walle, Johan, Canpolat, Nur, Holtta, Tuula, Fischbach, Michel, Klaus, Guenter, Aufricht, Christoph, Shroff, Rukshana, and Edefonti, Alberto
- Abstract
Background:Data on the immunization practices in pediatric chronic kidney disease (CKD) patients are scarce. The purpose of this study was to evaluate current vaccination practices for children on dialysis across European pediatric nephrology centers. Methods:A total of 18 tertiary pediatric nephrology centers from 12 European countries were included in the study. The data on universal national immunization programs and immunization practices for children with chronic disease or risk were recorded from European Center for Disease Prevention and Control and the World Health Organization. The immunization practices and center protocols for monitoring antibody titers after vaccination in dialysis patients were obtained through a questionnaire. Results:All centers included in the study recommended immunization against hepatitis B virus (HBV), diphtheria, tetanus, pertussis, Hemophilus influenzaetype b (Hib), poliomyelitis, measles, mumps, rubella (MMR), and streptococcus pneumonia in dialysis patients. In 16 centers, dialysis patients were vaccinated against influenza virus annually. HBV protective antibody titers were measured in 17 centers (during dialysis period in 14 centers, during pre-renal transplantation preparations in 14 centers or in both times in 11 centers). Hepatitis A virus (HAV) was reported to be followed in 13 centers, in 8 centers during dialysis period, and in 11 centers during pre-RTx preparations. MMR and varicella-zoster virus (VZV) protective antibody titers were measured during the dialysis period or before renal transplantation (RTx) in 12 and 15 centers, respectively, and in 6 centers both titers were checked both times. Conclusion:There are variations in vaccination practice across Europe. Children with CKD, those undergoing dialysis, and transplant candidates should receive age-appropriate vaccinations before RTx as well as before the transition to adult nephrology clinics and antibody levels should be monitored to evaluate the immunization status before and after RTx.
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- 2018
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32. RESPONSE TO RITUXIMAB OF NEPHROTIC SYNDROME IN A CHILD WITH IPEX SYNDROME
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Drozynska-Duklas, Magdalena, Zagozdzon, Ilona, Malgorzata Mysliwiec, Mlynarski, Wojciech, Irga-Jaworska, Ninela, and Zurowska, Aleksandra
33. [Chronic peritoneal dialysis in infants--preliminary results of the multicenter survey]
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Jander, Anna, Nowicki, Michal, Tkaczyk, Marcin, Makulska, Irena, Zwolinska, Danuta, Latoszynska, Joanna, Boguszewska-Baczkowska, Anna, Grenda, Ryszard, Balasz-Chmielewska, Irena, Zagozdzon, Ilona, Zaluska-Lesniewska, Iga, Zurowska, Aleksandra, Stefaniak, Ewa, Zachwieja, Jacek, Beata Leszczynska, Roszkowska-Blaim, Maria, Zachwieja, Katarzyna, Pietrzyk, Jacek A., Wiercinski, Ryszard, Zoch-Zwierz, Walentyna, and Stankiewicz, Roman
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Causality ,Survival Rate ,Hernia ,Population Surveillance ,Infant, Newborn ,Humans ,Infant ,Comorbidity ,Poland ,Peritonitis ,Infections ,Peritoneal Dialysis ,Retrospective Studies - Abstract
We retrospectively analysed peritoneal dialysis treatment in 29 infants dialysed in 9 paediatric centres in Poland in the years 1993-2004. The mean age at the start of dialysis was 4.9 +/- 3.5 months (range 2 days to 11 months), mean body mass 5.6 +/- 2.5 kg (range 2.5 to 11 kg). The mean duration of PD was 6.8 +/- 3.9 in the first year of life and total duration of the therapy 34 +/- 27 months. Of the 29 infants 4 died (2 in infancy), 11 underwent renal transplantation, in 2 children PD was stopped (they received a conventional treatment) and 12 were still dialysed at the date of data collection. The peritonitis rate was 1/9.5 patient-month and exit site infection rate 1/16 patient-month up to 1 year of life. 9 children (31%) required hernia repairs and in 9 catheters were replaced. Chronic peritoneal dialysis in infants is associated with high risk of infections and surgical complications and remains a challenge for paediatric nephrologists.
34. Risk Factors for Early Dialysis Dependency in Autosomal Recessive Polycystic Kidney Disease
- Author
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Kathrin Burgmaier, Kevin Kunzmann, Gema Ariceta, Carsten Bergmann, Anja Katrin Buescher, Mathias Burgmaier, Ismail Dursun, Ali Duzova, Loai Eid, Florian Erger, Markus Feldkoetter, Matthias Galiano, Michaela Geßner, Heike Goebel, Ibrahim Gokce, Dieter Haffner, Nakysa Hooman, Bernd Hoppe, Augustina Jankauskiene, Guenter Klaus, Jens König, Mieczyslaw Litwin, Laura Massella, Djalila Mekahli, Engin Melek, Sevgi Mir, Lars Pape, Larisa Prikhodina, Bruno Ranchin, Raphael Schild, Tomas Seeman, Lale Sever, Rukshana Shroff, Neveen A. Soliman, Stella Stabouli, Malgorzata Stanczyk, Yilmaz Tabel, Katarzyna Taranta-Janusz, Sara Testa, Julia Thumfart, Rezan Topaloglu, Lutz Thorsten Weber, Dorota Wicher, Elke Wühl, Simone Wygoda, Alev Yilmaz, Katarzyna Zachwieja, Ilona Zagozdzon, Klaus Zerres, Jörg Dötsch, Franz Schaefer, Max Christoph Liebau, Nadejda Ranguelov, Nathalie Godefroid, Laure Collard, Jacques Lombet, Julie Maquet, Gesa Schalk, Uwe Querfeld, Bodo B. Beck, Thomas Benzing, Reinhard Buettner, Franziska Grundmann, Christine Kurschat, Kerstin Benz, Anja Tzschoppe, Björn Buchholz, Rainer Buescher, Karsten Häffner, Martin Pohl, Oliver Gross, Jenny Krügel, Johanna Stock, Ludwig Patzer, Jun Oh, Wanja Bernhardt, Anke Doyon, Tobias Vinke, Anja Sander, Michael Henn, Ute Derichs, Rolf Beetz, Nikola Jeck, Bärbel Lange-Sperandio, Sabine Ponsel, Franziska Kusser, Barbara Uetz, Marcus Benz, Silke Schmidt, Christina Huppertz-Kessler, Birgitta Kranz, Andrea Titieni, Donald Wurm, Heinz E. Leichter, Martin Bald, Heiko Billing, Marwa M. Nabhan, Luis Enrique Lara, Fotios Papachristou, Francesco Emma, Rimante Cerkauskiene, Karolis Azukaitis, Anna Wasilewska, Irena Balasz-Chmielewska, Monika Miklaszewska, Marcin Tkaczyk, Przemyslaw Sikora, Marcin Zaniew, Ania Niemirska, Jolanta Antoniewicz, Justyna Lesiak, Alberto Caldas Afonso, Ana Teixeira, Gordana Milosevski-Lomic, Dusan Paripović, Amira Peco-Antic, Svetlana Papizh, Aysun Karabay Bayazit, Ali Anarat, Alper Soylu, Salih Kavukcu, Cengiz Candan, Salim Caliskan, Nur Canpolat, Sevinc Emre, Harika Alpay, Nurver Akinci, Secil Conkar, Hakan M. Poyrazoglu, Ruhan Dusunsel, Çukurova Üniversitesi, Burgmaier, Kathrin, Kunzmann, Kevin, Ariceta, Gema, Bergmann, Carsten, Buescher, Anja Katrin, Burgmaier, Mathias, Dursun, Ismail, Duzova, Ali, Eid, Loai, Erger, Florian, Feldkoetter, Markus, Galiano, Matthias, Gessner, Michaela, Goebel, Heike, Gokce, Ibrahim, Haffner, Dieter, Hooman, Nakysa, Hoppe, Bernd, Jankauskiene, Augustina, Klaus, Guenter, Koenig, Jens, Litwin, Mieczyslaw, Massella, Laura, Mekahli, Djalila, Melek, Engin, Mir, Sevgi, Pape, Lars, Prikhodina, Larisa, Ranchin, Bruno, Schild, Raphael, Seeman, Tomas, Sever, Late, Shroff, Rukshana, Soliman, Neveen A., Stabouli, Stella, Stanczyk, Malgorzata, Tabel, Yilmaz, Taranta-Janusz, Katarzyna, Testa, Sara, Thumfart, Julia, Topaloglu, Rezan, Weber, Lutz Thorsten, Wicher, Dorota, Wuehl, Elke, Wygoda, Simone, Yilmaz, Alev, Zachwieja, Katarzyna, Zagozdzon, Ilona, Zerres, Klaus, Doetsch, Joerg, Schaefer, Franz, and Liebau, Max Christoph
- Subjects
Male ,0301 basic medicine ,Time Factors ,medicine.medical_treatment ,ARPKD ,Medizin ,030232 urology & nephrology ,PROTEIN ,Oligohydramnios ,Pediatrics ,PKHD1 MUTATIONS ,0302 clinical medicine ,Pregnancy ,Risk Factors ,Prospective Studies ,ENCODES ,GENOTYPE-PHENOTYPE CORRELATIONS ,Obstetrics ,Hazard ratio ,Autosomal Recessive Polycystic Kidney Disease ,CLINICAL-EXPERIENCE ,Female ,Apgar score ,Life Sciences & Biomedicine ,renal replacement therapy ,medicine.medical_specialty ,GENETICS ,PKHD1 ,Risk Assessment ,Ultrasonography, Prenatal ,03 medical and health sciences ,Renal Dialysis ,medicine ,Humans ,Renal replacement therapy ,Dialysis ,Polycystic Kidney, Autosomal Recessive ,Retrospective Studies ,Science & Technology ,business.industry ,Infant, Newborn ,Infant ,Retrospective cohort study ,medicine.disease ,030104 developmental biology ,ciliopathy ,Pediatrics, Perinatology and Child Health ,business ,oligohydramnios ,Follow-Up Studies - Abstract
OBJECTIVE: To identify prenatal, perinatal, and postnatal risk factors for dialysis within the first year of life in children with autosomal recessive polycystic kidney disease (ARPKD) as a basis for parental counseling after prenatal and perinatal diagnosis. STUDY DESIGN: A dataset comprising 385 patients from the ARegPKD international registry study was analyzed for potential risk markers for dialysis during the first year of life. RESULTS: Thirty-six out of 385 children (9.4%) commenced dialysis in the first year of life. According to multivariable Cox regression analysis, the presence of oligohydramnios or anhydramnios, prenatal kidney enlargement, a low Apgar score, and the need for postnatal breathing support were independently associated with an increased hazard ratio for requiring dialysis within the first year of life. The increased risk associated with Apgar score and perinatal assisted breathing was time-dependent and vanished after 5 and 8 months of life, respectively. The predicted probabilities for early dialysis varied from 1.5% (95% CI, 0.5%-4.1%) for patients with ARPKD with no prenatal sonographic abnormalities to 32.3% (95% CI, 22.2%-44.5%) in cases of documented oligohydramnios or anhydramnios, renal cysts, and enlarged kidneys. CONCLUSIONS: This study, which identified risk factors associated with onset of dialysis in ARPKD in the first year of life, may be helpful in prenatal parental counseling in cases of suspected ARPKD. ispartof: JOURNAL OF PEDIATRICS vol:199 pages:22-+ ispartof: location:United States status: published
- Published
- 2018
35. Early childhood height-adjusted total kidney volume as a risk marker of kidney survival in ARPKD.
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Burgmaier K, Kilian S, Arbeiter K, Atmis B, Büscher A, Derichs U, Dursun I, Duzova A, Eid LA, Galiano M, Gessner M, Gokce I, Haeffner K, Hooman N, Jankauskiene A, Körber F, Longo G, Massella L, Mekahli D, Miloševski-Lomić G, Nalcacioglu H, Rus R, Shroff R, Stabouli S, Weber LT, Wygoda S, Yilmaz A, Zachwieja K, Zagozdzon I, Dötsch J, Schaefer F, and Liebau MC
- Subjects
- Adolescent, Biomarkers, Child, Child, Preschool, Cohort Studies, Disease Progression, Female, Glomerular Filtration Rate physiology, Humans, Infant, Liver Cirrhosis physiopathology, Longitudinal Studies, Male, Organ Size genetics, Organ Size physiology, Polycystic Kidney, Autosomal Recessive metabolism, Prognosis, Receptors, Cell Surface genetics, Renal Insufficiency, Chronic physiopathology, Ultrasonography, Kidney physiopathology, Polycystic Kidney, Autosomal Recessive mortality, Polycystic Kidney, Autosomal Recessive physiopathology
- Abstract
Autosomal recessive polycystic kidney disease (ARPKD) is characterized by bilateral fibrocystic changes resulting in pronounced kidney enlargement. Impairment of kidney function is highly variable and widely available prognostic markers are urgently needed as a base for clinical decision-making and future clinical trials. In this observational study we analyzed the longitudinal development of sonographic kidney measurements in a cohort of 456 ARPKD patients from the international registry study ARegPKD. We furthermore evaluated correlations of sonomorphometric findings and functional kidney disease with the aim to describe the natural disease course and to identify potential prognostic markers. Kidney pole-to-pole (PTP) length and estimated total kidney volume (eTKV) increase with growth throughout childhood and adolescence despite individual variability. Height-adjusted PTP length decreases over time, but such a trend cannot be seen for height-adjusted eTKV (haeTKV) where we even observed a slight mean linear increase of 4.5 ml/m per year during childhood and adolescence for the overall cohort. Patients with two null PKHD1 variants had larger first documented haeTKV values than children with missense variants (median (IQR) haeTKV 793 (450-1098) ml/m in Null/null, 403 (260-538) ml/m in Null/mis, 230 (169-357) ml/m in Mis/mis). In the overall cohort, estimated glomerular filtration rate decreases with increasing haeTKV (median (IQR) haeTKV 210 (150-267) ml/m in CKD stage 1, 472 (266-880) ml/m in stage 5 without kidney replacement therapy). Strikingly, there is a clear correlation between haeTKV in the first eighteen months of life and kidney survival in childhood and adolescence with ten-year kidney survival rates ranging from 20% in patients of the highest to 94% in the lowest quartile. Early childhood haeTKV may become an easily obtainable prognostic marker of kidney disease in ARPKD, e.g. for the identification of patients for clinical studies., (© 2021. The Author(s).)
- Published
- 2021
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36. Severe neurological outcomes after very early bilateral nephrectomies in patients with autosomal recessive polycystic kidney disease (ARPKD).
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Burgmaier K, Ariceta G, Bald M, Buescher AK, Burgmaier M, Erger F, Gessner M, Gokce I, König J, Kowalewska C, Massella L, Mastrangelo A, Mekahli D, Pape L, Patzer L, Potemkina A, Schalk G, Schild R, Shroff R, Szczepanska M, Taranta-Janusz K, Tkaczyk M, Weber LT, Wühl E, Wurm D, Wygoda S, Zagozdzon I, Dötsch J, Oh J, Schaefer F, and Liebau MC
- Subjects
- Cohort Studies, Disease Progression, Female, Humans, Infant, Infant, Newborn, Male, Nervous System Diseases etiology, Postoperative Complications epidemiology, Postoperative Complications etiology, Risk Factors, Nephrectomy adverse effects, Nervous System Diseases epidemiology, Polycystic Kidney, Autosomal Recessive surgery, Renal Dialysis statistics & numerical data
- Abstract
To test the association between bilateral nephrectomies in patients with autosomal recessive polycystic kidney disease (ARPKD) and long-term clinical outcome and to identify risk factors for severe outcomes, a dataset comprising 504 patients from the international registry study ARegPKD was analyzed for characteristics and complications of patients with very early (≤ 3 months; VEBNE) and early (4-15 months; EBNE) bilateral nephrectomies. Patients with very early dialysis (VED, onset ≤ 3 months) without bilateral nephrectomies and patients with total kidney volumes (TKV) comparable to VEBNE infants served as additional control groups. We identified 19 children with VEBNE, 9 with EBNE, 12 with VED and 11 in the TKV control group. VEBNE patients suffered more frequently from severe neurological complications in comparison to all control patients. Very early bilateral nephrectomies and documentation of severe hypotensive episodes were independent risk factors for severe neurological complications. Bilateral nephrectomies within the first 3 months of life are associated with a risk of severe neurological complications later in life. Our data support a very cautious indication of very early bilateral nephrectomies in ARPKD, especially in patients with residual kidney function, and emphasize the importance of avoiding severe hypotensive episodes in this at-risk cohort.
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- 2020
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37. [Pre-emptive renal transplantation in a boy with obstructive uropathy following reconstruction procedures].
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Borzych D, Załuska-Leśniewska I, Zagozdzon I, Komasara L, Czauderna P, and Zurowska A
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- Cadaver, Humans, Infant, Male, Nephrectomy, Urinary Catheterization, Urinary Diversion methods, Urinary Tract Infections etiology, Urologic Surgical Procedures, Male, Kidney Transplantation adverse effects, Urethra abnormalities, Urethra surgery, Urethral Stricture congenital, Urethral Stricture surgery
- Abstract
Patients with bladder dysfunction comprise over 30% of pediatric patients on renal replacement therapy. We report on a successful cadaveric pre-emptive renal transplantation performed in a boy born with posterior urethral valve. Following bilateral ureterocutaneostomies, left nephrectomy and valve resection, at 6 years of age a continent ileocolonocystoplasty was performed. The boy started intermittent daytime catheterization, passing urine both via urethra and fistula. At the age of 18 he received a renal transplant. Continuing the previous regime, at 1.5 years follow up his graft is well functioning (GFR >75 ml/min/1.73 m2) with sporadic episodes of urinary tract infection.
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- 2008
38. [Peritoneal transport properties for glucose and creatinine in Polish children and adolescents on chronic peritoneal dialysis].
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Zurowska A, Borzych D, Zagozdzon I, Drozdz D, Ziółkowska H, Boguszewska A, Szczepańska M, Stefaniak E, Jander A, and Kiliś-Pstrusińska K
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- Adolescent, Adult, Child, Child, Preschool, Glucose metabolism, Humans, Infant, Permeability, Poland, Retrospective Studies, Creatinine blood, Glucose pharmacokinetics, Kidney Failure, Chronic metabolism, Kidney Failure, Chronic therapy, Peritoneal Dialysis
- Abstract
Introduction: The mode of PD treatment is dependent on the individual transport properties of the peritoneal membrane. Two multicentre trials performed in the U.S. (PPDSC) and Europe (MEPPS) have established reference curves for solute equilibration in children performed with the use of 1100 ml/m2 fill volume in the former and 1000 ml/m2 in the latter study., Aim of the Study: Assessment of basal peritoneal membrane equilibration based on PET tests in polish children and adolescents treated with chronic peritoneal dialysis., Material and Methods: 58 PET tests from patients treated at 8 Polish PD centres were analysed. The mean time of performing PET test was 6,5 months after the start of PD therapy. All of the patients had been peritonitis free from onset. The mean fill volume was 1021 (906-1170) ml/m2., Results: Based on the results of creatinine and glucose equilibration we established basal peritoneal solute transport curves for polish PD children using an average fill volume of 1020 ml/m2. The following values were obtained at 4hrs of dwell time for 2.27% glucose solution: D/P for creatinine = 0.68 +/- 0.15 and D/Do for glucose = 0.39 +/- 0.12., Conclusions: The DIP creatinine equilibration curves were similar to the previously published reference curves for children, whereas those for glucose was significantly lower. Using a fill volume scaled to body surface area of 1020 ml/m2 equilibration curves for glucose and creatinine are similar in children over 1 year of age and adults.
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- 2006
39. [Chronic peritoneal dialysis in infants--preliminary results of the multicenter survey].
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Jander A, Nowicki M, Tkaczyk M, Makulska I, Zwolińska D, Latoszyńska J, Boguszewska-Baczkowska A, Grenda R, Bałasz-Chmielewska I, Zagozdzon I, Załuska-Leśniewska I, Zurowska A, Stefaniak E, Zachwieja J, Leszczyńska B, Roszkowska-Blaim M, Zachwieja K, Pietrzyk JA, Wierciński R, Zoch-Zwierz W, and Stankiewicz R
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- Causality, Comorbidity, Hernia epidemiology, Humans, Infant, Infant, Newborn, Poland epidemiology, Population Surveillance, Retrospective Studies, Survival Rate, Infections epidemiology, Peritoneal Dialysis statistics & numerical data, Peritonitis epidemiology, Peritonitis therapy
- Abstract
We retrospectively analysed peritoneal dialysis treatment in 29 infants dialysed in 9 paediatric centres in Poland in the years 1993-2004. The mean age at the start of dialysis was 4.9 +/- 3.5 months (range 2 days to 11 months), mean body mass 5.6 +/- 2.5 kg (range 2.5 to 11 kg). The mean duration of PD was 6.8 +/- 3.9 in the first year of life and total duration of the therapy 34 +/- 27 months. Of the 29 infants 4 died (2 in infancy), 11 underwent renal transplantation, in 2 children PD was stopped (they received a conventional treatment) and 12 were still dialysed at the date of data collection. The peritonitis rate was 1/9.5 patient-month and exit site infection rate 1/16 patient-month up to 1 year of life. 9 children (31%) required hernia repairs and in 9 catheters were replaced. Chronic peritoneal dialysis in infants is associated with high risk of infections and surgical complications and remains a challenge for paediatric nephrologists.
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- 2006
40. [Percutaneus endoscopic gastrostomy (PEG) in an infant with chronic renal failure].
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Zurowska A, Tyl J, Zagozdzon I, and Załuska-Leśniewska I
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- Body Height, Body Weight, Enteral Nutrition methods, Female, Humans, Infant, Malnutrition etiology, Treatment Outcome, Endoscopy, Gastrointestinal methods, Gastrostomy instrumentation, Kidney Failure, Chronic complications, Kidney Failure, Chronic congenital, Malnutrition therapy
- Abstract
Malnutrition is a major problem in patients with chronic renal failure, especially in children in the first three years of life. Meeting high energy needs in these patients may be difficult because of anorexia and vomiting, which are common in predialysis renal failure. Nutritional support for children with chronic renal failure often involves the use of nasogastric tubes or gastrostomy feeding. We describe an infant with pre-dialysis renal failure and severe malnutrition in whom only insertion of percutaneus endoscopic gastrostomy provided adequate caloric intake and satisfactory weight gain.
- Published
- 2006
41. [Congenital and genetic related causes of end-stage renal disease--data from Polish Registry of Renal Rreplacement Therapy in Children 2000-2004].
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Zurowska A, Zagozdzon I, Bałasz I, Boguszewska A, Prokurat C, Pietrzyk J, Drozdz D, Szczepańska M, Stefaniak E, Jander A, Roszkowska-Blaim D, Ziółkowska H, Makulska I, Kołłataj B, Jarmoliński T, Siteń G, Stankiewicz R, and Wierciński R
- Subjects
- Adolescent, Adult, Causality, Child, Child, Preschool, Female, Humans, Infant, Infant, Newborn, Kidney Diseases, Cystic congenital, Kidney Failure, Chronic epidemiology, Kidney Failure, Chronic therapy, Male, Poland epidemiology, Prevalence, Puberty physiology, Urologic Diseases congenital, Genes, Dominant genetics, Kidney Failure, Chronic congenital, Kidney Failure, Chronic genetics, Registries, Renal Replacement Therapy statistics & numerical data
- Abstract
Unlabelled: One of the objectives of Polish Registry of Renal Replacement Therapy in Children established on 31st Dec. 2000 was to collect complete data on etiology of end stage renal disease (ESRD) in polish children., Material and Methods: Data on 469 patients (251 boys, 218 girls) aged 0-22 years treated with renal replacement therapy (RRT) at 13 pediatric dialysis units in Poland from 2000 to 2004 were analyzed. The mean age at start of dialysis was 10 years and 3 months. Renal diseases were defined according to EDTA coding system. Data is presented for the whole group, in 5-year age groups and separately for both sexes., Results: Congenital and genetic renal diseases were the cause of ESRF in 56% of the polish population of children and adolescents on RRT. 39% of causes were acquired diseases, 5% remained unidentified. Congenital and genetic causes dominated in children < 5 years of age (71%). They accounted for 49%, 61% and 45% of causes in the consecutive 5-year age groups. The most numerous group of congenital diseases leading to ESRF were uropathies 37% and 25% of causes in the consecutive age groups. In boys the most frequent uropathy was obstructive uropathy (25%), the majority caused by posterior urethral valves. In girls the most frequent uropathies were reflux nephropathy (10%) and nephropathy secondary to neurogenic bladder (9%). Uropathies were followed by renal hypo-dysplasia without urinary tract anomalies (11%) and cystic diseases (10%)., Conclusions: Congenital kidney anomalies and genetic diseases are the leading cause of end-stage renal disease in children up to 15 years of age.
- Published
- 2006
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