1. Catecholamine-secreting adrenal lipomatous ganglioneuroma: A case study
- Author
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Kiyohito Yamamoto, MD, PhD, Yuki Inada, MD, PhD, Atsushi Nakamoto, MD, PhD, Hayahito Nomi, MD, PhD, Yoshitaka Kurisu, MD, PhD, Kazuhiro Yamamoto, MD, PhD, and Keigo Osuga, MD, PhD
- Subjects
Adrenal gland ,Catecholamine ,Ganglioneuroma ,Intratumoral fat ,Lipomatous ganglioneuroma ,Medical physics. Medical radiology. Nuclear medicine ,R895-920 - Abstract
Ganglioneuroma, which arise from neural crest cells, typically occurs in adolescents and young adults. Most ganglioneuromas are clinically asymptomatic and hormonally silent, therefore may be diagnosed incidentally during imaging studies. Ganglioneuroma containing fat (lipomatous ganglioneuroma) is a rare variant of ganglioneuroma that is histologically characterized by a mature adipocytic component admixed with a conventional ganglioneuroma. Herein, we report the case of adrenal lipomatous ganglioneuroma with elevated urinary catecholamine level.
- Published
- 2020
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