730 results on '"Wajner M"'
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2. Evidence that l-Carnitine and Selenium Supplementation Reduces Oxidative Stress in Phenylketonuric Patients
3. Incidence of 3-hydroxy-3-methylglutaryl-coenzyme A lyase (HL) deficiency in Brazil, South America
4. Methylmalonate inhibits succinate-supported oxygen consumption by interfering with mitochondrial succinate uptake
5. Evidence for oxidative stress in tissues derived from succinate semialdehyde dehydrogenase-deficient mice
6. Cytoskeleton as a potential target in the neuropathology of maple syrup urine disease: Insight from animal studies
7. Investigation of oxidative stress parameters in treated phenylketonuric patients
8. Inhibition of energy metabolism by 2-methylacetoacetate and 2-methyl-3-hydroxybutyrate in cerebral cortex of developing rats
9. Effect of hyperprolinemia on acetylcholinesterase and butyrylcholinesterase activities in rat
10. Promotion of oxidative stress by 3-hydroxyglutaric acid in rat striatum
11. Modulation of glutamatergic and GABAergic neurotransmission in glutaryl-CoA dehydrogenase deficiency
12. Animal models for glutaryl-CoA dehydrogenase deficiency
13. The role of oxidative damage in the neuropathology of organic acidurias: Insights from animal studies
14. In vivo disruption of redox homeostasis caused by the synergistic action of methylmalonic acid and ammonia in brain of young rats: PTW08–45
15. Effect of Propionic and Methylmalonic Acids on the High Molecular Weight Neurofilament Subunit (NF-H) in Rat Cerebral Cortex
16. Effect of the Branched-Chain Alpha-Ketoacids Accumulating in Maple Syrup Urine Disease on the High Molecular Weight Neurofilament Subunit (NF-H) in Rat Cerebral Cortex
17. Ganglioside Alterations in the Central Nervous System of Rats Chronically Injected with Methylmalonic and Propionic Acids
18. D-2-Hydroxyglutaric Aciduria in a Patient with a Severe Clinical Phenotype and Unusual MRI Findings
19. L-Pyroglutamic Acid Inhibits Energy Production and Lipid Synthesis in Cerebral Cortex of Young Rats In Vitro
20. Creatine prevents behavioral alterations caused by methylmalonic acid administration into the hippocampus of rats in the open field task
21. Reduction of large neutral amino acid concentrations in plasma and CSF of patients with maple syrup urine disease during crises
22. Inhibition of energy productionin vitro by glutaric acid in cerebral cortex of young rats
23. Inhibition of Rat Brain Lipid Synthesis In Vitro by 4-Hydroxybutyric Acid
24. The effect of human alpha-fetoprotein on cell-mediated and humoral immunity during pregnancy
25. Oxidative stress in patients with phenylketonuria
26. Neurological dysfunction in methylmalonic acidaemia is probably related to the inhibitory effect of methylmalonate on brain energy production
27. Selective screening of 10,000 high-risk Brazilian patients for the detection of inborn errors of metabolism
28. Immunosuppressive effects of organic acids accumulating in patients with maple syrup urine disease
29. Isolated 3-methylcrotonyl-coenzyme A carboxylase deficiency in a child with metabolic stroke
30. Na+, K+ ATPase activity is markedly reduced by cis-4-decenoic acid in synaptic plasma membranes from cerebral cortex of rats
31. Inhibition of succinate dehydrogenase and β-hydroxybutyrate dehydrogenase activities by methylmalonate in brain and liver of developing rats
32. Evidence that oxidative stress is increased in patients with X-linked adrenoleukodystrophy
33. Effect of methylmalonate onin vitro lactate release and carbon dioxide production by brain of suckling rats
34. Inhibition of mitochondrial creatine kinase activity from rat cerebral cortex by methylmalonic acid
35. 3-Hydroxyglutaric acid enhances glutamate uptake into astrocytes from cerebral cortex of young rats
36. 3-HYDROXYGLUTARIC ACID INDUCES OXIDA-TIVE STRESS IN RAT CEREBRAL CORTEX: P10-134
37. GLUTATHIONE AND L-NAME PREVENT THE INHIBITION OF MITOCHONDRIAL CREATINE KINASE ACTIVITY CAUSED BY METHYLMALONIC ACID: P10-138
38. FREE RADICALS AND ANTIOXIDANT DEFENCES IN X-LINKED ADRENOLEUKODYSTROPHY: P11-154
39. TIGLIC ACID INDUCES OXIDATIVE STRESS IN RAT BRAIN: P11-152
40. L-PYROGLUTAMIC ACID REDUCES THE ANTIOXIDANT CAPACITY OF RAT BRAIN: P10-135
41. METHYLMALONIC ACID INDUCES OXIDATIVE STRESS IN RAT STRIATUM: P10-137
42. BRANCHED-CHAIN ALPHA-KETO ACIDS DIMINISH THE RAT BRAIN ANTIOXIDANT DEFENSES: P10-131
43. D-2-Hydroxyglutaric acid inhibits creatine kinase activity from cardiac and skeletal muscle of young rats
44. Reduction of plasma concentrations of large neutral amino acids in patients with maple syrup urine disease during crises
45. Corrigendum to “Cannabinoid Receptor Agonists Reduce the Short-Term Mitochondrial Dysfunction and Oxidative Stress Linked to Excitotoxicity in the Rat Brain” [Neuroscience 285C (2015) 97–106]
46. Inhibition of the mitochondrial respiratory chain complex activities in rat cerebral cortex by methylmalonic acid
47. Seven-year experience of a reference laboratory for detection of inborn errors of metabolism in Brazil
48. Reduction of large neutral amino acid levels in plasma and brain of hyperleucinemic rats
49. The effect of WIN 55,212-2 suggests a cannabinoid-sensitive component in the early toxicity induced by organic acids accumulating in glutaric acidemia type I and in related disorders of propionate metabolism in rat brain synaptosomes
50. Toxic synergism between quinolinic acid and organic acids accumulating in glutaric acidemia type I and in disorders of propionate metabolism in rat brain synaptosomes: Relevance for metabolic acidemias
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