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Submitted by Guilherme Lemeszenski (guilherme@nead.unesp.br) on 2013-08-22T18:48:25Z No. of bitstreams: 1 S0004-282X2007000300020.pdf: 387188 bytes, checksum: b3716f5d41df3e4ebf4e8c506a7b3883 (MD5) Made available in DSpace on 2013-08-22T18:48:25Z (GMT). No. of bitstreams: 1 S0004-282X2007000300020.pdf: 387188 bytes, checksum: b3716f5d41df3e4ebf4e8c506a7b3883 (MD5) Previous issue date: 2007-06-01 Made available in DSpace on 2013-09-30T19:38:15Z (GMT). No. of bitstreams: 2 S0004-282X2007000300020.pdf: 387188 bytes, checksum: b3716f5d41df3e4ebf4e8c506a7b3883 (MD5) S0004-282X2007000300020.pdf.txt: 23956 bytes, checksum: 323426ac4fe836f350cf3ce924373237 (MD5) Previous issue date: 2007-06-01 Submitted by Vitor Silverio Rodrigues (vitorsrodrigues@reitoria.unesp.br) on 2014-05-20T13:36:00Z No. of bitstreams: 2 S0004-282X2007000300020.pdf: 387188 bytes, checksum: b3716f5d41df3e4ebf4e8c506a7b3883 (MD5) S0004-282X2007000300020.pdf.txt: 23956 bytes, checksum: 323426ac4fe836f350cf3ce924373237 (MD5) Made available in DSpace on 2014-05-20T13:36:00Z (GMT). No. of bitstreams: 2 S0004-282X2007000300020.pdf: 387188 bytes, checksum: b3716f5d41df3e4ebf4e8c506a7b3883 (MD5) S0004-282X2007000300020.pdf.txt: 23956 bytes, checksum: 323426ac4fe836f350cf3ce924373237 (MD5) Previous issue date: 2007-06-01 A síndrome de Crouzon é caracterizada por deformidade craniana, alterações faciais e exoftalmia. O retardo no desenvolvimento neuropsicomotor é observado em alguns casos. Este estudo tem como objetivo analisar a influência do momento da cirurgia, da classe sócio-econômica associada ao nível educacional dos pais e da ocorrência de malformações do sistema nervoso central no desenvolvimento cognitivo destes pacientes correlacionando estes achados à qualidade de vida deles e de suas famílias. Foram estudados 11 pacientes com diagnóstico de síndrome de Crouzon com idade entre um ano e quatro meses e treze anos. A avaliação multidisciplinar dos pacientes incluiu, avaliação social, avaliação cognitiva, estudo do encéfalo por ressonância magnética e avaliação da qualidade de vida. O quociente de inteligência variou de 46 a 102 (m=84,2) e foi correlacionado de forma inversa com o Fator 4 do Questionário de Recursos e Estresse Simplificado (incapacidade da criança); não se correlacionou com as alterações encefálicas, com a condição sócio-econômica dos pais e nem com o momento do tratamento neurocirúrgico. Crouzon syndrome is characterized by cranial and facial abnormalities and exophtalmos. Mental retardation is sometimes observed. The objective of this study was to correlate brain malformations, timing for surgery and also social classification of families and parents education to the neuropsychological evaluation and to the quality of life of these families. Eleven patients with Crouzon syndrome were studied, whose ages were between 16 and 132 months. The multidisciplinary evaluation included : social evaluation, cognitive evaluation, brain studies by magnetic ressonance imaging and quality of life evaluation. The intelligence quotient values observed were between 46 and 102 (m=84.2) and was correlated (inverted correlation) to the factor IV of the short-form of the Questionnaire on Resources and Stress. Mental development was not correlated to brain malformation, neither to the age at time of operation or to the level of family environment and parents education. Universidade de São Paulo Hospital de Reabilitação de Anomalias Craniofaciais Departamento de Cirurgia Craniofacial Hospital Alemão Oswaldo Cruz Departamento de Neuroradiologia USP Hospital das Clínicas Departamento de Neurocirurgia Universidade Estadual Paulista Hospital das Clínicas Departamento de Neurologia e Psiquiatria UNESP Hospital das Clínicas Departamento de Cirurgia e Ortopedia USP Faculdade de Odontologia Departamento de Fonoaudiologia Universidade Estadual Paulista Hospital das Clínicas Departamento de Neurologia e Psiquiatria UNESP Hospital das Clínicas Departamento de Cirurgia e Ortopedia

Crouzon syndrome is characterized by cranial and facial abnormalities and exophtalmos. Mental retardation is sometimes observed. The objective of this study was to correlate brain malformations, timing for surgery and also social classification of families and parents education to the neuropsychological evaluation and to the quality of life of these families. Eleven patients with Crouzon syndrome were studied, whose ages were between 16 and 132 months. The multidisciplinary evaluation included : social evaluation, cognitive evaluation, brain studies by magnetic resonance imaging and quality of life evaluation. The intelligence quotient values observed were between 46 and 102 (m=84.2) and was correlated (inverted correlation) to the factor IV of the short-form of the Questionnaire on Resources and Stress. Mental development was not correlated to brain malformation, neither to the age at time of operation or to the level of family environment and parents education.

Submitted by Vitor Silverio Rodrigues (vitorsrodrigues@reitoria.unesp.br) on 2014-05-27T11:21:42Z No. of bitstreams: 0Bitstream added on 2014-05-27T14:44:25Z : No. of bitstreams: 1 2-s2.0-32244442191.pdf: 215165 bytes, checksum: 39be905176b23a840b6c19f8403d8db6 (MD5) Made available in DSpace on 2014-05-27T11:21:42Z (GMT). No. of bitstreams: 0 Previous issue date: 2005-12-01 Apert syndrome is characterized by craniosynostosis, symmetric syndactyly and other systemic malformations, with mental retardation usually present. The objective of this study was to correlate brain malformations and timing for surgery with neuropsychological evaluation. We also tried to determine other relevant aspects involved in cognitive development of these patients such as social classification of families and parents' education. Eighteen patients with Apert syndrome were studied, whose ages were between 14 and 322 months. Brain abnormalities were observed in 55.6% of them. The intelligence quotient or developmental quotient values observed were between 45 and 108. Mental development was related to the quality of family environment and parents' education. Mental development was not correlated to brain malformation or age at time of operation. In conclusion, quality of family environment was the most significant factor directly involved in mental development of patients with Apert syndrome. Department of Craniofacial Surgery Hospital de Reabilitação de Anomalias Craniofaciais University of Sao Paulo (USP), Bauru, SP Department of Neuroradiology Hospital Alemão Oswaldo Cruz, São Paulo SP Department of Neurosurgery Hospital Das Clínicas University of Sao Paulo (USP), São Paulo SP Department of Neurology and Psychiatry Hospital Das Clínicas University of the State of São Paulo (UNESP), Botucatu SP Department of Surgery Hospital Das Clínicas University of the State of Sao Paulo (UNESP), Botucatu SP Department of Fonoaudiology Faculty of Odontology University of Sao Paulo (USP), Bauru SP , Rua Moyses Leme da Silva 1-30, 17017-335 Bauru SP Department of Neurology and Psychiatry Hospital Das Clínicas University of the State of São Paulo (UNESP), Botucatu SP Department of Surgery Hospital Das Clínicas University of the State of Sao Paulo (UNESP), Botucatu SP

While the osteotomy techniques for craniofacial synostosis treatment are well-known and frequently used, the resolution of the nasal air impairment, ocular prolapse, and retromaxillism relapse remains unsatisfactory. The modification of the osteotomy presented here has the purpose of a new therapeutic trial.

Apert Syndrome, also called acrocephalosyndactylia type 1, is characterized by craniostenosis with early fusion of sutures of the vault and/or cranial base, associated to mid-face hypoplasia, symmetric syndactylia of the hands and feet and other systemic malformations. CNS malformations and intracranial hypertension are frequently observed in these patients. Early surgical treatment aims to minimize the deleterious effects of intracranial hypertension. Fronto-orbital advancement, the usual surgical technique, increases the intracranial Volume and improves the disposition of encephalic structures previously deformed by a short skull. This study analyzes CNS alterations revealed by magnetic resonance in 18 patients presenting Apert Syndrome, and the conformational alterations in the encephalic structures after surgical treatment. The patients' age in February 2001 ranged from 14 to 322 Months (m=107). Image study included brain magnetic resonance showing ventricular enlargement in five cases (27.8%), corpus callosum hypoplasia in five cases (27.8%), septum pellucidum hypoplasia in five cases (27.8%), cavum vergae in two cases (11.1%) and, arachnoid cyst in the posterior fossa in two cases (11.1%). Absence of CNS alterations was noted in 44.4% of cases. A corpus callosum morphologic index was established by dividing its height by its length, which revealed values that ranged from 0.4409 to 1.0237. The values of this index were correlated to the occurrence or absence of surgical treatment (p=0.012; t=2.83). Data analysis allowed the conclusion that the corpus callosum morphologic measure quantified the conformational alterations of the cerebral structures determined by the surgical treatment.

Made available in DSpace on 2021-07-14T10:48:02Z (GMT). No. of bitstreams: 0 Previous issue date: 1994-12. Added 1 bitstream(s) on 2021-07-14T11:38:32Z : No. of bitstreams: 1 S1516-31801994000400011.pdf: 261097 bytes, checksum: d5ac81751cbdc2936444aa18c0472b03 (MD5) Os autores propõem a utilização de um alongador ósseo composto de duas miniplacas. Através de uma válvula remota o expansor seria enchido e a distensão da bolsa promoveria afastamento das miniplacas e consequentemente das extremidades ósseas Since 1869, bone lengthening has been pursued; when Langenbeck (13) tried growing a shortened bone extremity utilizing for this an arteriovenous fistula in the thigh. At the begining of this century, codovilla (1905) (5,14) introduced bone lenghtening methods for lower limbs. Universidade Estadual Paulista Universidade Estadual Paulista

Made available in DSpace on 2022-04-28T18:54:02Z (GMT). No. of bitstreams: 0 Previous issue date: 1992-01-01 The purpose of this study was to develop an experimental model in rabbits that would permit us to analyze skull reconstruction and enable the study of bone autografts, osteofacial flaps, and other materials. We use the rabbit model to study the early integration of the skull autograft and to demonstrate the relationship between radioisotopical and histological analyses. © 1992 Mutaz B. Habal, MD. Instituto do Câncer ‘Arnaldo Vieira de Carvalho’, São Paulo Section of Plastic Surgery, São Paulo Section of Nuclear Medicine, São Paulo Section of Pathology, São Paulo UNESP, São Paulo Hospital de Reabilitação de Bauru University of São Paulo, São Paulo UNESP, São Paulo

This article describes a 20-year-old man with widespread polyostotic fibrous dysplasia that resulted in massive craniofacial deformity with unilateral exorbitism and oronasal obstruction. The patient illustrates the rare occurrence of fibrous dysplasia with major malformation of the face and skull, requiring multiple stages of surgical "sculpture" to improve function and appearance. The disease entity, differential diagnosis, and treatment are discussed.