11 results on '"Schouvey, Sylvie"'
Search Results
2. Clinical Features and Natural History of Preadolescent Nonsyndromic Hypertrophic Cardiomyopathy
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Norrish, Gabrielle, primary, Cleary, Aoife, additional, Field, Ella, additional, Cervi, Elena, additional, Boleti, Olga, additional, Ziółkowska, Lidia, additional, Olivotto, Iacopo, additional, Khraiche, Diala, additional, Limongelli, Giuseppe, additional, Anastasakis, Aris, additional, Weintraub, Robert, additional, Biagini, Elena, additional, Ragni, Luca, additional, Prendiville, Terence, additional, Duignan, Sophie, additional, McLeod, Karen, additional, Ilina, Maria, additional, Fernandez, Adrian, additional, Marrone, Chiara, additional, Bökenkamp, Regina, additional, Baban, Anwar, additional, Kubus, Peter, additional, Daubeney, Piers E.F., additional, Sarquella-Brugada, Georgia, additional, Cesar, Sergi, additional, Klaassen, Sabine, additional, Ojala, Tiina H., additional, Bhole, Vinay, additional, Medrano, Constancio, additional, Uzun, Orhan, additional, Brown, Elspeth, additional, Gran, Ferran, additional, Sinagra, Gianfranco, additional, Castro, Francisco J., additional, Stuart, Graham, additional, Yamazawa, Hirokuni, additional, Barriales-Villa, Roberto, additional, Garcia-Guereta, Luis, additional, Adwani, Satish, additional, Linter, Katie, additional, Bharucha, Tara, additional, Gonzales-Lopez, Esther, additional, Siles, Ana, additional, Rasmussen, Torsten B., additional, Calcagnino, Margherita, additional, Jones, Caroline B., additional, De Wilde, Hans, additional, Kubo, Toru, additional, Felice, Tiziana, additional, Popoiu, Anca, additional, Mogensen, Jens, additional, Mathur, Sujeev, additional, Centeno, Fernando, additional, Reinhardt, Zdenka, additional, Schouvey, Sylvie, additional, Elliott, Perry M., additional, and Kaski, Juan Pablo, additional
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- 2022
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3. External validation of the HCM Risk-Kids model for predicting sudden cardiac death in childhood hypertrophic cardiomyopathy
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Norrish, Gabrielle, primary, Qu, Chen, additional, Field, Ella, additional, Cervi, Elena, additional, Khraiche, Diala, additional, Klaassen, Sabine, additional, Ojala, Tiina H, additional, Sinagra, Gianfranco, additional, Yamazawa, Hirokuni, additional, Marrone, Chiara, additional, Popoiu, Anca, additional, Centeno, Fernando, additional, Schouvey, Sylvie, additional, Olivotto, Iacopo, additional, Day, Sharlene M, additional, Colan, Steve, additional, Rossano, Joseph, additional, Wittekind, Samuel G, additional, Saberi, Sara, additional, Russell, Mark, additional, Helms, Adam, additional, Ingles, Jodie, additional, Semsarian, Christopher, additional, Elliott, Perry M, additional, Ho, Carolyn Y, additional, Omar, Rumana Z, additional, and Kaski, Juan P, additional
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- 2021
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4. Evaluation of a cardiac transplanted children cohort: long term pediatric follow-up and transiant to adulthood. Twenty years of monocentric experience
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Wanert, Chloé, primary, El Louali, Fedoua, additional, Ovaert, Caroline, additional, Schouvey, Sylvie, additional, Lenoir, Marien, additional, Fouilloux, Virginie, additional, Tsimaratos, Michel, additional, Rousset-Rouvière, Caroline, additional, and Garaix, Florentine, additional
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- 2021
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5. Coronary artery spasm and dobutamine stress echocardiography
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Aboukhoudir, Falah, Rekik, Sofiene, Andrieu, Stephane, Cheggour, Saida, Pansieri, Michel, Metge, Marc, Barnay, Pierre, Faugier, Jean Paul, Schouvey, Sylvie, Quaino, Gonzalo, Unal, Clement, Gonzalez, Stéphanie, and Hirsch, Jean Lou
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- 2009
6. External validation of the HCM Risk-Kids model for predicting sudden cardiac death in childhood hypertrophic cardiomyopathy.
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Norrish, Gabrielle, Qu, Chen, Field, Ella, Cervi, Elena, Khraiche, Diala, Klaassen, Sabine, Ojala, Tiina H, Sinagra, Gianfranco, Yamazawa, Hirokuni, Marrone, Chiara, Popoiu, Anca, Centeno, Fernando, Schouvey, Sylvie, Olivotto, Iacopo, Day, Sharlene M, Colan, Steve, Rossano, Joseph, Wittekind, Samuel G, Saberi, Sara, and Russell, Mark
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- 2022
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7. 129 Dobutamine stress echocardiography and coronary artery spasm: a missed link
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Aboukhoudir, Falah, primary, Rekik, Sofiene, additional, Andrieu, Stephane, additional, Cheggour, Saida, additional, Pansieri, Michel, additional, Barnay, Pierre, additional, Metge, Marc, additional, Faugier, Jean Paul, additional, Unal, Clement, additional, Schouvey, Sylvie, additional, Gonzalez, Stephanie, additional, and Hirsch, Jean Lou, additional
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- 2010
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8. 854-3 Fundamental errors in current applications of gorlin formula and continuity equation for aortic valve anatomical orifice area estimate.
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Isaaz, Karl and Schouvey, Sylvie
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AORTIC valve , *MYOCARDIAL infarction , *ELECTROCARDIOGRAPHY , *CARDIOVASCULAR diseases , *AORTIC stenosis , *ANATOMY - Published
- 2004
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9. External validation of the HCM Risk-Kids model for predicting sudden cardiac death in childhood hypertrophic cardiomyopathy
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Chen Qu, Fernando Centeno, Sara Saberi, Joseph W. Rossano, Gabrielle Norrish, Sabine Klaassen, Anca Popoiu, Carolyn Y. Ho, Elena Cervi, Ella Field, Steve Colan, Hirokuni Yamazawa, Diala Khraiche, Chiara Marrone, Iacopo Olivotto, Samuel G. Wittekind, Christopher Semsarian, Mark W. Russell, Adam S. Helms, Perry M. Elliott, Sharlene M. Day, Juan Pablo Kaski, Jodie Ingles, Tiina Ojala, Rumana Z Omar, Gianfranco Sinagra, Sylvie Schouvey, Norrish, Gabrielle, Qu, Chen, Field, Ella, Cervi, Elena, Khraiche, Diala, Klaassen, Sabine, Ojala, Tiina H, Sinagra, Gianfranco, Yamazawa, Hirokuni, Marrone, Chiara, Popoiu, Anca, Centeno, Fernando, Schouvey, Sylvie, Olivotto, Iacopo, Day, Sharlene M, Colan, Steve, Rossano, Joseph, Wittekind, Samuel G, Saberi, Sara, Russell, Mark, Helms, Adam, Ingles, Jodie, Semsarian, Christopher, Elliott, Perry M, Ho, Carolyn Y, Omar, Rumana Z, Kaski, Juan P, University of Helsinki, Clinicum, Children's Hospital, and HUS Children and Adolescents
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Epidemiology ,CHILDREN ,030204 cardiovascular system & hematology ,GUIDELINES ,Ventricular tachycardia ,Sudden cardiac death ,Cohort Studies ,0302 clinical medicine ,Risk Factors ,Ventricular outflow tract ,030212 general & internal medicine ,Child ,OUTCOMES ,Sudden death ,LGE ,Incidence ,Hypertrophic cardiomyopathy ,EUROPEAN-SOCIETY ,3. Good health ,Paediatric ,Child, Preschool ,Cohort ,SURVIVAL ,Cardiology ,cardiovascular system ,Cardiology and Cardiovascular Medicine ,medicine.medical_specialty ,Adolescent ,DIAGNOSIS ,Risk Assessment ,03 medical and health sciences ,Internal medicine ,medicine ,Humans ,cardiovascular diseases ,Risk stratification ,Retrospective Studies ,business.industry ,External validation ,Infant ,Cardiomyopathy, Hypertrophic ,medicine.disease ,PREVENTION ,Confidence interval ,Death, Sudden, Cardiac ,Cardiovascular and Metabolic Diseases ,3121 General medicine, internal medicine and other clinical medicine ,business - Abstract
Aims Sudden cardiac death (SCD) is the most common mode of death in childhood hypertrophic cardiomyopathy (HCM). The newly developed HCM Risk-Kids model provides clinicians with individualized estimates of risk. The aim of this study was to externally validate the model in a large independent, multi-centre patient cohort. Methods and results A retrospective, longitudinal cohort of 421 patients diagnosed with HCM aged 1–16 years independent of the HCM Risk-Kids development and internal validation cohort was studied. Data on HCM Risk-Kids predictor variables (unexplained syncope, non-sustained ventricular tachycardia, maximal left ventricular wall thickness, left atrial diameter, and left ventricular outflow tract gradient) were collected from the time of baseline clinical evaluation. The performance of the HCM Risk-Kids model in predicting risk at 5 years was assessed. Twenty-three patients (5.4%) met the SCD end-point within 5 years, with an overall incidence rate of 2.03 per 100 patient-years [95% confidence interval (CI) 1.48–2.78]. Model validation showed a Harrell’s C-index of 0.745 (95% CI 0.52–0.97) and Uno’s C-index 0.714 (95% 0.58–0.85) with a calibration slope of 1.15 (95% 0.51–1.80). A 5-year predicted risk threshold of ≥6% identified 17 (73.9%) SCD events with a corresponding C-statistic of 0.702 (95% CI 0.60–0.81). Conclusions This study reports the first external validation of the HCM Risk-Kids model in a large and geographically diverse patient population. A 5-year predicted risk of ≥6% identified over 70% of events, confirming that HCM Risk-Kids provides a method for individualized risk predictions and shared decision-making in children with HCM.
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- 2022
10. Relationship Between Maximal Left Ventricular Wall Thickness and Sudden Cardiac Death in Childhood Onset Hypertrophic Cardiomyopathy
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Gabrielle Norrish, Tao Ding, Ella Field, Elena Cervi, Lidia Ziółkowska, Iacopo Olivotto, Diala Khraiche, Giuseppe Limongelli, Aris Anastasakis, Robert Weintraub, Elena Biagini, Luca Ragni, Terrence Prendiville, Sophie Duignan, Karen McLeod, Maria Ilina, Adrián Fernández, Chiara Marrone, Regina Bökenkamp, Anwar Baban, Peter Kubus, Piers E.F. Daubeney, Georgia Sarquella-Brugada, Sergi Cesar, Sabine Klaassen, Tiina H. Ojala, Vinay Bhole, Constancio Medrano, Orhan Uzun, Elspeth Brown, Ferran Gran, Gianfranco Sinagra, Francisco J. Castro, Graham Stuart, Gabriele Vignati, Hirokuni Yamazawa, Roberto Barriales-Villa, Luis Garcia-Guereta, Satish Adwani, Katie Linter, Tara Bharucha, Pablo Garcia-Pavia, Ana Siles, Torsten B. Rasmussen, Margherita Calcagnino, Caroline B. Jones, Hans De Wilde, Toru Kubo, Tiziana Felice, Anca Popoiu, Jens Mogensen, Sujeev Mathur, Fernando Centeno, Zdenka Reinhardt, Sylvie Schouvey, Costas O’Mahony, Rumana Z. Omar, Perry M. Elliott, Juan Pablo Kaski, Institut Català de la Salut, [Norrish G] Centre for Inherited Cardiovascular Diseases, Great Ormond Street Hospital, London, United Kingdom. Institute of Cardiovascular Sciences, University College London, United Kingdom. [Ding T] Department of Statistical Science, University College London, United Kingdom. [Field E, Cervi E] Centre for Inherited Cardiovascular Diseases, Great Ormond Street Hospital, London, United Kingdom. [Ziółkowska L] The Children’s Memorial Health Institute, Warsaw, Poland. [Olivotto I] Careggi University Hopsital, Florence, Italy. [Gran F] Vall d’Hebron Hospital Universitari, Barcelona, Spain, Vall d'Hebron Barcelona Hospital Campus, University of Helsinki, Clinicum, Children's Hospital, HUS Children and Adolescents, Norrish, Gabrielle, Ding, Tao, Field, Ella, Cervi, Elena, Ziółkowska, Lidia, Olivotto, Iacopo, Khraiche, Diala, Limongelli, Giuseppe, Anastasakis, Ari, Weintraub, Robert, Biagini, Elena, Ragni, Luca, Prendiville, Terrence, Duignan, Sophie, Mcleod, Karen, Ilina, Maria, Fernandez, Adrian, Marrone, Chiara, Bökenkamp, Regina, Baban, Anwar, Kubus, Peter, Daubeney, Piers E F, Sarquella-Brugada, Georgia, Cesar, Sergi, Klaassen, Sabine, Ojala, Tiina H, Bhole, Vinay, Medrano, Constancio, Uzun, Orhan, Brown, Elspeth, Gran, Ferran, Sinagra, Gianfranco, Castro, Francisco J, Stuart, Graham, Vignati, Gabriele, Yamazawa, Hirokuni, Barriales-Villa, Roberto, Garcia-Guereta, Lui, Adwani, Satish, Linter, Katie, Bharucha, Tara, Garcia-Pavia, Pablo, Siles, Ana, Rasmussen, Torsten B, Calcagnino, Margherita, Jones, Caroline B, De Wilde, Han, Kubo, Toru, Felice, Tiziana, Popoiu, Anca, Mogensen, Jen, Mathur, Sujeev, Centeno, Fernando, Reinhardt, Zdenka, Schouvey, Sylvie, O'Mahony, Costa, Omar, Rumana Z, Elliott, Perry M, and Kaski, Juan Pablo
- Subjects
Hypertrophy, Left Ventricular/complications ,sistema cardiovascular::corazón::ventrículos cardíacos [ANATOMÍA] ,Heart Ventricles ,FEATURES ,enfermedades cardiovasculares::enfermedades cardíacas::paro cardíaco::muerte súbita cardíaca [ENFERMEDADES] ,Cardiomyopathy, Hypertrophic/complications ,CHILDREN ,Heart Ventricles/diagnostic imaging ,DIAGNOSIS ,Cor - Hipertròfia - Complicacions ,Risk Assessment ,LONG-TERM OUTCOMES ,3123 Gynaecology and paediatrics ,Risk Factors ,death ,Physiology (medical) ,ADOLESCENTS ,human ,cardiovascular diseases ,humans ,death, sudden ,Death, Sudden, Cardiac/epidemiology ,Retrospective Studies ,sudden ,child ,IDENTIFICATION ,Mort sobtada ,adult ,Defibrillators, Implantable/adverse effects ,Cardiovascular Diseases::Heart Diseases::Cardiomyopathies::Cardiomyopathy, Hypertrophic [DISEASES] ,Cardiomyopathy, Hypertrophic ,Cardiovascular Diseases::Heart Diseases::Heart Arrest::Death, Sudden, Cardiac [DISEASES] ,hypertrophic cardiomyopathy ,Defibrillators, Implantable ,heart ventricle ,enfermedades cardiovasculares::enfermedades cardíacas::miocardiopatías::miocardiopatía hipertrófica [ENFERMEDADES] ,Death, Sudden, Cardiac ,Cardiovascular and Metabolic Diseases ,3121 General medicine, internal medicine and other clinical medicine ,RISK-FACTORS ,SURVIVAL ,cardiovascular system ,Hypertrophy, Left Ventricular ,hypertrophy ,Cardiology and Cardiovascular Medicine ,TASK-FORCE ,Cor - Ventricle esquerre ,Cardiovascular System::Heart::Heart Ventricles [ANATOMY] - Abstract
Background: Maximal left ventricular wall thickness (MLVWT) is a risk factor for sudden cardiac death (SCD) in hypertrophic cardiomyopathy (HCM). In adults, the severity of left ventricular hypertrophy has a nonlinear relationship with SCD, but it is not known whether the same complex relationship is seen in childhood. The aim of this study was to describe the relationship between left ventricular hypertrophy and SCD risk in a large international pediatric HCM cohort. Methods: The study cohort comprised 1075 children (mean age, 10.2 years [±4.4]) diagnosed with HCM (1–16 years) from the International Paediatric Hypertrophic Cardiomyopathy Consortium. Anonymized, noninvasive clinical data were collected from baseline evaluation and follow-up, and 5-year estimated SCD risk was calculated (HCM Risk-Kids). Results: MLVWT Z score was Z scores were associated with heart failure symptoms, unexplained syncope, left ventricular outflow tract obstruction, left atrial dilatation, and nonsustained ventricular tachycardia. One hundred twenty-two patients (71.3%) with MLVWT Z score ≥20 had coexisting risk factors for SCD. Over a median follow-up of 4.9 years (interquartile range, 2.3–9.3), 115 (10.7%) had an SCD event. Freedom from SCD event at 5 years for those with MLVWT Z scores Z score, peaking at Z score +23. The presence of coexisting risk factors had a summative effect on risk. Conclusions: In children with HCM, an inverted U-shaped relationship exists between left ventricular hypertrophy and estimated SCD risk. The presence of additional risk factors has a summative effect on risk. While MLVWT is important for risk stratification, it should not be used either as a binary variable or in isolation to guide implantable cardioverter defibrillator implantation decisions in children with HCM.
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- 2022
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11. [Atrial septal defect in the adult].
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Schouvey S, Assaidi A, and Fraisse A
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- Adult, Humans, Heart Septal Defects, Atrial diagnosis, Heart Septal Defects, Atrial therapy
- Published
- 2013
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