1. Primary intracranial malignant peripheral nerve sheath tumour responding to chemotherapy.
- Author
-
Zambrana F, Vicente F, García-Manrique T, Pereira S, Sáinz De Zaitigui J, and De La Cruz Merino L
- Subjects
- Adult, Doxorubicin administration & dosage, Humans, Ifosfamide administration & dosage, Male, Antineoplastic Combined Chemotherapy Protocols therapeutic use, Brain Neoplasms drug therapy, Brain Neoplasms pathology, Nerve Sheath Neoplasms drug therapy
- Abstract
Malignant peripheral nerve sheath tumours (MPNST) are a rare variety of soft tissue sarcomas (STS) arising from major peripheral nerve branches and typically located in the lower extremity, chest wall or the retroperitoneum. It is a biologically aggressive neoplasm for which the treatment of choice is surgery, but usually requires a multimodality approach, having been generally labelled as chemoresistant. We present a case of MPNST located intracranially with a good response to chemotherapy.
- Published
- 2010
- Full Text
- View/download PDF