Search

Mullerian duct malformations represent a miscellaneous group of congenital anomalies that result from the arrested development, abnormal formation or incomplete fusion of the paramesonephric ducts. Congenital Mullerian abnormalities usually present at adolescent age with menstrual irregulari¬ty, dysmenorrhea, infertility and recurrent pregnancy loss. The Unicornuate uterus is a rare uterine malformation which usually features a rudimentary accessory horn with or without functioning endometrium. We are presenting a case of perimenopausal multiparous patient who had history of secondary dysmenorrhea diagnosed with endometrioma on imaging studies, but on laparotomy incidentally found to have Unicornuate uterus with functioning noncommunicating rudimentary horn leading to hematometra and hematosalpinx. The objective of this clinical case report is to highlight this rare Mullerian malformation as a differential diagnosis of secondary dysmenorrhea, chronic pelvic pain or adnexal mass in perimenopausal age group females.