27 results on '"Magro, Pascal"'
Search Results
2. Development and validation of a quality of life measurement scale specific to hereditary hemorrhagic telangiectasia: the QoL-HHT
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Le, Thi Thao Truc, Martinent, Guillaume, Dupuis-Girod, Sophie, Parrot, Antoine, Contis, Anne, Riviere, Sophie, Chinet, Thierry, Grobost, Vincent, Espitia, Olivier, Dussardier-Gilbert, Brigitte, Alric, Laurent, Armengol, Guillaume, Maillard, Hélène, Leguy-Seguin, Vanessa, Leroy, Sylvie, Rondeau-Lutz, Murielle, Lavigne, Christian, Mohamed, Shirine, Chaussavoine, Laurent, Magro, Pascal, Seguier, Julie, Kerjouan, Mallorie, and Fourdrinoy, Sylvie
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- 2022
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3. Portopulmonary hypertension in the current era of pulmonary hypertension management
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Savale, Laurent, Guimas, Manuel, Ebstein, Nathan, Fertin, Marie, Jevnikar, Mitja, Renard, Sébastien, Horeau-Langlard, Delphine, Tromeur, Cécile, Chabanne, Céline, Prevot, Grégoire, Chaouat, Ari, Moceri, Pamela, Artaud-Macari, Élise, Degano, Bruno, Tresorier, Romain, Boissin, Clément, Bouvaist, Hélène, Simon, Anne-Claire, Riou, Marianne, Favrolt, Nicolas, Palat, Sylvain, Bourlier, Delphine, Magro, Pascal, Cottin, Vincent, Bergot, Emmanuel, Lamblin, Nicolas, Jaïs, Xavier, Coilly, Audrey, Durand, François, Francoz, Claire, Conti, Filomena, Hervé, Philippe, Simonneau, Gérald, Montani, David, Duclos-Vallée, Jean-Charles, Samuel, Didier, Humbert, Marc, De Groote, Pascal, and Sitbon, Olivier
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- 2020
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4. Seven cases of hereditary haemorrhagic telangiectasia-like hepatic vascular abnormalities associated withEPHB4pathogenic variants
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Guilhem, Alexandre, primary, Dupuis-Girod, Sophie, additional, Espitia, Olivier, additional, Rivière, Sophie, additional, Seguier, Julie, additional, Kerjouan, Mallorie, additional, Lavigne, Christian, additional, Maillard, Hélène, additional, Magro, Pascal, additional, Alric, Laurent, additional, Lipsker, Dan, additional, Parrot, Antoine, additional, Leguy, Vanessa, additional, Vanlemmens, Claire, additional, Guibaud, Laurent, additional, Vikkula, Miikka, additional, Eyries, Melanie, additional, Valette, Pierre-Jean, additional, and Giraud, Sophie, additional
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- 2023
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5. Seven cases of hereditary haemorrhagic telangiectasia-like hepatic vascular abnormalities associated with EPHB4 pathogenic variants.
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Guilhem, Alexandre, Dupuis-Girod, Sophie, Espitia, Olivier, Rivière, Sophie, Seguier, Julie, Kerjouan, Mallorie, Lavigne, Christian, Maillard, Hélène, Magro, Pascal, Alric, Laurent, Lipsker, Dan, Parrot, Antoine, Leguy, Vanessa, Vanlemmens, Claire, Guibaud, Laurent, Vikkula, Miikka, Eyries, Melanie, Valette, Pierre-Jean, and Giraud, Sophie
- Abstract
Background EPHB4 loss of function is associated with type 2 capillary malformation–arteriovenous malformation syndrome, an autosomal dominant vascular disorder. The phenotype partially overlaps with hereditary haemorrhagic telangiectasia (HHT) due to epistaxis, telangiectases and cerebral arteriovenous malformations, but a similar liver involvement has never been described. Methods Members of the French HHT network reported their cases of EPHB4 mutation identified after an initial suspicion of HHT. Clinical, radiological and genetic characteristics were analysed. Results Among 21 patients with EPHB4, 15 had a liver imaging, including 7 with HHT-like abnormalities (2 female patients and 5 male patients, ages 43–69 years). Atypical epistaxis and telangiectases were noted in two cases each. They were significantly older than the eight patients with normal imaging (median: 51 vs 20 years, p<0.0006). The main hepatic artery was dilated in all the cases (diameter: 8–11mm). Six patients had hepatic telangiectases. All kind of shunts were described (arteriosystemic: five patients, arterioportal: two patients, portosystemic: three patients). The overall liver appearance was considered as typical of HHT in six cases. Six EPHB4 variants were classified as pathogenic and one as likely pathogenic, with no specific hot spot. Conclusion EPHB4 loss-of-function variants can be associated with HHT-like hepatic abnormalities and should be tested for atypical HHT presentations. [ABSTRACT FROM AUTHOR]
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- 2023
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6. Mortality in myotonic dystrophy patients in the area of prophylactic pacing devices
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Laurent, Valérie, Pellieux, Sybille, Corcia, Philippe, Magro, Pascal, Pierre, Bertrand, Fauchier, Laurent, Raynaud, Martine, and Babuty, Dominique
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- 2011
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7. Development and validation of a quality of life measurement scale specific to Hereditary Hemorrhagic Telangiectasia: The QoL-HHT
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LE, Thi Thao Truc, primary, MARTINENT, Guillaume, additional, DUPUIS-GIROD, Sophie, additional, PARROT, Antoine, additional, CONTIS, Anne, additional, RIVIERE, Sophie, additional, CHINET, Thierry, additional, GROBOST, Vincent, additional, ESPITIA, Olivier, additional, DUSSARDIER-GILBERT, Brigitte, additional, ALRIC, Laurent, additional, ARMENGOL, Guillaume, additional, MAILLARD, Hélène, additional, LEGUY-SEGUIN, Vanessa, additional, LEROY, Sylvie, additional, RONDEAU-LUTZ, Murielle, additional, LAVIGNE, Christian, additional, MOHAMED, Shirine, additional, CHAUSSAVOINE, Laurent, additional, MAGRO, Pascal, additional, SEGUIER, Julie, additional, KERJOUAN, Mallorie, additional, and FOURDRINOY, Sylvie, additional
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- 2022
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8. Additional file 4 of Development and validation of a quality of life measurement scale specific to hereditary hemorrhagic telangiectasia: the QoL-HHT
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Le, Thi Thao Truc, Martinent, Guillaume, Dupuis-Girod, Sophie, Parrot, Antoine, Contis, Anne, Riviere, Sophie, Chinet, Thierry, Grobost, Vincent, Espitia, Olivier, Dussardier-Gilbert, Brigitte, Alric, Laurent, Armengol, Guillaume, Maillard, Hélène, Leguy-Seguin, Vanessa, Leroy, Sylvie, Rondeau-Lutz, Murielle, Lavigne, Christian, Mohamed, Shirine, Chaussavoine, Laurent, Magro, Pascal, Seguier, Julie, Kerjouan, Mallorie, and Fourdrinoy, Sylvie
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Additional file 4. The QoL-HHT questionnaire (original version validated in French).
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- 2022
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9. Association between Initial Treatment Strategy and Long-Term Survival in Pulmonary Arterial Hypertension
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Boucly, Athénaïs, primary, Savale, Laurent, additional, Jaïs, Xavier, additional, Bauer, Fabrice, additional, Bergot, Emmanuel, additional, Bertoletti, Laurent, additional, Beurnier, Antoine, additional, Bourdin, Arnaud, additional, Bouvaist, Hélène, additional, Bulifon, Sophie, additional, Chabanne, Céline, additional, Chaouat, Ari, additional, Cottin, Vincent, additional, Dauphin, Claire, additional, Degano, Bruno, additional, De Groote, Pascal, additional, Favrolt, Nicolas, additional, Feng, Yuanchao, additional, Horeau-Langlard, Delphine, additional, Jevnikar, Mitja, additional, Jutant, Etienne-Marie, additional, Liang, Zhiying, additional, Magro, Pascal, additional, Mauran, Pierre, additional, Moceri, Pamela, additional, Mornex, Jean-François, additional, Palat, Sylvain, additional, Parent, Florence, additional, Picard, François, additional, Pichon, Jérémie, additional, Poubeau, Patrice, additional, Prévot, Grégoire, additional, Renard, Sébastien, additional, Reynaud-Gaubert, Martine, additional, Riou, Marianne, additional, Roblot, Pascal, additional, Sanchez, Olivier, additional, Seferian, Andrei, additional, Tromeur, Cécile, additional, Weatherald, Jason, additional, Simonneau, Gérald, additional, Montani, David, additional, Humbert, Marc, additional, and Sitbon, Olivier, additional
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- 2021
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10. Cerebral aspergillosis in the critically ill: two cases of successful medical treatment
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Ehrmann, Stephan, Bastides, Frédéric, Gissot, Valérie, Mercier, Emmanuelle, Magro, Pascal, Bailly, Eric, and Legras, Annick
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- 2005
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11. Pulmonary Alveolar Proteinosis Revealing a Telomerase Disease
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Marchand-Adam, Sylvain, Diot, Bruno, Magro, Pascal, De Muret, Anne, Guignabert, Christophe, Kannengiesser, Caroline, Londono-Vallejo, Arturo, Draskovic, Irena, Toutain, Annick, and Diot, Patrice
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- 2013
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12. Periprandial administration of inhaled iloprost: a risk factor for digestive bleeding?
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Bigot, Adrien, Jonville-Bera, Annie-Pierre, Diot, Elisabeth, Magro, Pascal, and Diot, Patrice
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- 2012
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13. Corrigendum to: “Portopulmonary hypertension in the current era of pulmonary hypertension management” [J Hepatol (2020);73:130–139]
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Savale, Laurent, primary, Guimas, Manuel, additional, Ebstein, Nathan, additional, Fertin, Marie, additional, Jevnikar, Mitja, additional, Renard, Sébastien, additional, Horeau-Langlard, Delphine, additional, Tromeur, Cécile, additional, Chabanne, Céline, additional, Prevot, Grégoire, additional, Chaouat, Ari, additional, Moceri, Pamela, additional, Artaud-Macari, Élise, additional, Degano, Bruno, additional, Tresorier, Romain, additional, Boissin, Clément, additional, Bouvaist, Hélène, additional, Simon, Anne-Claire, additional, Riou, Marianne, additional, Favrolt, Nicolas, additional, Palat, Sylvain, additional, Bourlier, Delphine, additional, Magro, Pascal, additional, Cottin, Vincent, additional, Bergot, Emmanuel, additional, Lamblin, Nicolas, additional, Jaïs, Xavier, additional, Coilly, Audrey, additional, Durand, François, additional, Francoz, Claire, additional, Conti, Filomena, additional, Hervé, Philippe, additional, Simonneau, Gérald, additional, Montani, David, additional, Duclos-Vallée, Jean-Charles, additional, Samuel, Didier, additional, Humbert, Marc, additional, De Groote, Pascal, additional, and Sitbon, Olivier, additional
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- 2020
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14. Phenotype and Outcomes of Pulmonary Hypertension Associated with Neurofibromatosis Type 1
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Jutant, Etienne-Marie, primary, Jaïs, Xavier, additional, Girerd, Barbara, additional, Savale, Laurent, additional, Ghigna, Maria-Rosa, additional, Perros, Frédéric, additional, Mignard, Xavier, additional, Jevnikar, Mitja, additional, Bourlier, Delphine, additional, Prevot, Grégoire, additional, Tromeur, Cécile, additional, Bauer, Fabrice, additional, Bergot, Emmanuel, additional, Dauphin, Claire, additional, Favrolt, Nicolas, additional, Traclet, Julie, additional, Soumagne, Thibaud, additional, De Groote, Pascal, additional, Chabanne, Céline, additional, Magro, Pascal, additional, Bertoletti, Laurent, additional, Gueffet, Jean-Pierre, additional, Chaouat, Ari, additional, Goupil, François, additional, Moceri, Pamela, additional, Borie, Raphael, additional, Fadel, Elie, additional, Wolkenstein, Pierre, additional, Brillet, Pierre-Yves, additional, Simonneau, Gérald, additional, Sitbon, Olivier, additional, Humbert, Marc, additional, and Montani, David, additional
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- 2020
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15. Feasability of Human Endobronchial Imaging with a Linear-Array Ultrasound Catheter
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Tranquart, François, Palanchon, Peggy, Cladé, Odile, Bleuzen, Aurore, Dinet, Dominique, Magro, Pascal, and Diot, Patrice
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- 2008
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16. Implanted Phrenic Stimulation Impairs Local Diaphragm Myofiber Reinnervation in Amyotrophic Lateral Sclerosis
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Guimarães-Costa, Raquel, primary, Niérat, Marie-Cécile, additional, Rivals, Isabelle, additional, Morélot-Panzini, Capucine, additional, Romero, Norma Beatriz, additional, Menegaux, Fabrice, additional, Salachas, François, additional, Gonzalez-Bermejo, Jésus, additional, Similowski, Thomas, additional, Bruneteau, Gaëlle, additional, del Mar Amador, Maria, additional, Antoine, Jean Christophe, additional, Arne-Bes, Marie Christine, additional, Attali, Valérie, additional, Beauvais, Katell, additional, Brunaud-Danel, Veronique, additional, Bruneteau, Gaelle, additional, Camdessanche, Jean-Philippe, additional, Camu, William, additional, Carluer, Laurence, additional, Cassereau, Julien, additional, Chapart, Maud, additional, Chenuel, Bruno, additional, Chereau, Nathalie, additional, Cintas, Pascal, additional, Clavelou, Pierre, additional, Corcia, Philippe, additional, Cornette, André, additional, Couratier, Philippe, additional, Court-Fortune, Isabelle, additional, Cuvelier, Antoine, additional, Delclaux, Christophe, additional, Desnuelle, Claude, additional, Di Maria, Sophie, additional, Fargeot, Catherine, additional, Fauroux, Brigitte, additional, Finet-Monnier, Armelle, additional, Fleury, Marie Celine, additional, Gaillat, Carmen, additional, Georges, Marjolaine, additional, Giroud, Maurice, additional, Gonzalez-Bermejo, Jesus, additional, Greil, Annick, additional, Guerrier, Muriel, additional, Guillaume, Nicolas, additional, Guy, Nathalie, additional, Hannequin, Didier, additional, Juillien, Valérie, additional, Juntas-Morales, Raul, additional, Kessler, Romain, additional, Kolev, Yvan, additional, Lagarde, Julien, additional, Lautrette, Geraldine, additional, Le Cam, Pierre, additional, LeForestier, Nadine, additional, Lemasson, Gwendal, additional, Lenglet, Thimothée, additional, Magro, Pascal, additional, Mallart, Anne, additional, Martinaud, Olivier, additional, Meininger, Vincent, additional, Meslier, Nicole, additional, Moirot, Pierre, additional, Morelot-Panzini, Capucine, additional, Nadjar, Yann, additional, Niel-Duriez, Myriam, additional, Nierat, Marie-Cecile, additional, Noullet, Severine, additional, Pageot, Nicolas, additional, Perez, Thierry, additional, Perrin, Christophe, additional, Pillet, Odile, additional, Pittion, Sophie, additional, Pouget, Jean, additional, Pradat, Pierre-François, additional, Prigent, Hélène, additional, Rabec, Claudio, additional, Ricard, Jean-Damien, additional, Romero, Norma, additional, Royer, Catherine, additional, Schaup, Barbara, additional, Sedkaoui, Kamila, additional, Soriani, Marie-Hélène, additional, Straus, Christian, additional, Tanguy, Marie-Laure, additional, Tranchant, Christine, additional, Vandenberghue, Nadia, additional, Vershueren, Annie, additional, Viader, Fausto, additional, and Wienalek-Bachelet, Anne-Cecile, additional
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- 2019
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17. Late Breaking Abstract - Balloon pulmonary angioplasty versus riociguat for the treatment of inoperable chronic thromboembolic pulmonary hypertension: results from the randomised controlled RACE study
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Jais, Xavier, primary, Brenot, Philippe, additional, Bouvaist, Hélène, additional, Canuet, Matthieu, additional, Chabanne, Céline, additional, Chaouat, Ari, additional, Cottin, Vincent, additional, De Groote, Pascal, additional, Dromer, Claire, additional, Favrolt, Nicolas, additional, Garcia Alonso, Carlos, additional, Gérardin, Benoit, additional, Horeau-Langlard, Delphine, additional, Jevnikar, Mitja, additional, Magro, Pascal, additional, Montani, David, additional, Parent, Florence, additional, Pison, Christophe, additional, Prévot, Grégoire, additional, Renard, Sébastien, additional, Savale, Laurent, additional, Simon, Anne Claire, additional, Sitbon, Olivier, additional, Tresorier, Romain, additional, Tromeur, Cécile, additional, Agostini, Hélène, additional, Piedvache, Céline, additional, Fadel, Elie, additional, Humbert, Marc, additional, and Simonneau, Gérald, additional
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- 2019
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18. Pulmonary hypertension associated with neurofibromatosis type 1: data from the French Pulmonary Hypertension Registry
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Jutant, Etienne-Marie, primary, Jaïs, Xavier, additional, Girerd, Barbara, additional, Mignard, Xavier, additional, Ghigna, Maria-Rosa, additional, Bourlier, Delphine, additional, Tromeur, Cécile, additional, Bergot, Emmanuel, additional, Prévot, Grégoire, additional, Dauphin, Claire, additional, Favrolt, Nicolas, additional, Traclet, Julie, additional, Moceri, Pamela, additional, Soumagne, Thibaud, additional, Bauer, Fabrice, additional, Degroote, Pascal, additional, Chabanne, Cécile, additional, Magro, Pascal, additional, Bertoletti, Laurent, additional, Savale, Laurent, additional, Soubrier, Florent, additional, Simonneau, Gérald, additional, Sitbon, Olivier, additional, Brillet, Pierre-Yves, additional, Humbert, Marc, additional, and Montani, David, additional
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- 2019
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19. High-frequency ultrasound quantification of acute radiation dermatitis: pilot study of patients undergoing radiotherapy for breast cancer
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Reymond, Maud, Barbier, Louise, Salame, Ephrem, Besh, Camille, Dumortier, Jérome, Pageaux, Georges-Philippe, Bureau, Christophe, Dharancy, Sébastien, Vanlemmens, Claire, Abergel, Armand, Woehl Jaegle, Marie-Lorraine, Magro, Pascal, Patat, Frederic, Laurent, Emeline, Perarnau, Jean-Marc, Garnier, M., Champeaux, E., Boehm, A., Briard, O., Wachter, T., Vaillant, L., Bens, G., Machet, L., Service d'Hépatologie Gastro-entérologie [CHU Clermont-Ferrand], CHU Estaing [Clermont-Ferrand], CHU Clermont-Ferrand-CHU Clermont-Ferrand, Departement d'Hépato-Gastroentérologie et Cancérologie Digestive [CHRU Tours], CHU Trousseau [Tours], Centre Hospitalier Régional Universitaire de Tours (CHRU Tours), service d'Hépato-gastro-entérologie, Hospices Civiles de Lyon-Hôpital Edouard Heriault, Hôpital Saint Eloi (CHRU Montpellier), Centre Hospitalier Régional Universitaire [Montpellier] (CHRU Montpellier), Centre Hospitalier Universitaire de Toulouse (CHU Toulouse), Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille), Service d'Hépatologie [CHRU Besançon], Centre Hospitalier Régional Universitaire de Besançon (CHRU Besançon), Institut Pascal (IP), SIGMA Clermont (SIGMA Clermont)-Université Clermont Auvergne [2017-2020] (UCA [2017-2020])-Centre National de la Recherche Scientifique (CNRS), Université Clermont Auvergne [2017-2020] (UCA [2017-2020]), Centre National de la Recherche Scientifique (CNRS), SIGMA Clermont, Hépatologie Gastro-Entérologie, Université de Tours (UT), Centre de recherche en épidémiologie et santé des populations (CESP), Université de Versailles Saint-Quentin-en-Yvelines (UVSQ)-Université Paris-Sud - Paris 11 (UP11)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpital Paul Brousse-Institut National de la Santé et de la Recherche Médicale (INSERM), Éducation Éthique Santé EA 7505 (EES), Association pour la Pêche et la Protection des Milieux Aquatiques (AAPPMA), and Hôpital Bichat
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medicine.medical_specialty ,medicine.medical_treatment ,Breast Neoplasms ,Pilot Projects ,Dermatology ,[SHS]Humanities and Social Sciences ,030207 dermatology & venereal diseases ,03 medical and health sciences ,0302 clinical medicine ,Breast cancer ,Edema ,Humans ,Medicine ,ComputingMilieux_MISCELLANEOUS ,Aged ,Ultrasonography ,Univariate analysis ,integumentary system ,business.industry ,Ultrasound ,Lumpectomy ,Middle Aged ,medicine.disease ,Phototype ,Radiation therapy ,ROC Curve ,030220 oncology & carcinogenesis ,Acute Disease ,Female ,Radiology ,Radiodermatitis ,medicine.symptom ,business ,Complication - Abstract
Background Acute radiation dermatitis (ARD) is a frequent complication after breast cancer radiotherapy and is usually assessed by semi-quantitative clinical scores, which may be subject to inter-observer variability. High-frequency ultrasound imaging of the skin can reliably quantify thickness and edema in diseased skin. We aimed to compare the relative increase in dermal thickness of the irradiated zone in breast-cancer patients undergoing radiotherapy, with clinical severity. Methods A consecutive series of patients undergoing treatment for breast cancer by lumpectomy and radiotherapy in a 6-month period also underwent clinical and ultrasound evaluation of ARD. Results We included 34 female patients 17 had grade 1 (group 1), 17 had grade 2 or grade 3 ARD (group 2). The mean relative increase in dermal thickness in irradiated skin (RIDTIS) was greater for group 2 than 1: 0.53 vs 0.29 mm (P=.023). On univariate analysis, ARD was associated with skin phototype, breast volume and RIDTIS, and on multivariable analysis, breast volume and age remained predictive of the disease. Conclusion Patients with more severe dermatitis showed significantly increased dermal thickness. Dermal thickness is a quantitative variable that could help quantify the efficacy of drugs and improve the treatment of this disease in patients undergoing radiotherapy.
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- 2017
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20. Does Portopulmonary Hypertension Impede Liver Transplantation in Cirrhotic Patients? A French Multicentric Retrospective Study
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Reymond, Maud, primary, Barbier, Louise, additional, Salame, Ephrem, additional, Besh, Camille, additional, Dumortier, Jérome, additional, Pageaux, Georges-Philippe, additional, Bureau, Christophe, additional, Dharancy, Sébastien, additional, Vanlemmens, Claire, additional, Abergel, Armand, additional, Woehl Jaegle, Marie-Lorraine, additional, Magro, Pascal, additional, Patat, Frederic, additional, Laurent, Emeline, additional, and Perarnau, Jean-Marc, additional
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- 2018
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21. Long-acting recombinant coagulation factor IX albumin fusion protein (rIX-FP) in hemophilia B: results of a phase 3 trial
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Saiag, P., Gutzmer, R., Ascierto, P., Maio, M., Grob, J.-J., Murawa, P., Dréno, B., Ross, M., Weber, J., Hauschild, A., Rutkowski, P., Testori, A., Levchenko, E., Enk, A., Misery, L., Vanden Abeele, C., Vojtek, I., Peeters, O., Brichard, V., Therasse, P., Samier-Guérin, Anne, Saraux, Alain, Gestin, Simon, Cornec, Divi, Marhadour, Thierry, Devauchelle-Pensec, Valérie, Bressollette, Luc, Nonent, Michel, Jousse-Joulin, Sandrine, Sanges, Sébastien, Launay, David, Rhee, Rennie, Sitbon, Olivier, Hachulla, Eric, Mouthon, Luc, Guillevin, Loïc, Rottat, Laurence, Montani, David, de Groote, Pascal, Cottin, Vincent, Magro, Pascal, Prevot, Gregoire, Bauer, Fabrice, Bergot, Emmanuel, Chabanne, Céline, Reynaud-Gaubert, Martine, Leroy, Sylvie, Canuet, Matthieu, Sanchez, Olivier, Gut-Gobert, Christophe, Dauphin, Claire, Pison, Christophe, Boissin, Clement, Habib, Gilbert, Clerson, Pierre, Conesa, François, Cordier, François, Kawut, Steven, Simonneau, Gerald, Humbert, Marc, Santagostino, Elena, Martinowitz, Uri, Lissitchkov, Toshko, Pan-Petesch, Brigitte, Hanabusa, Hideji, Oldenburg, Johannes, Boggio, Lisa, Negrier, Claude, Pabinger, Ingrid, von Depka Prondzinski, Mario, Altisent, Carmen, Castaman, Giancarlo, Yamamoto, Koji, Álvarez-Roman, Maria-Teresa, Voigt, Christine, Blackman, Nicole, Jacobs, Iris, Hôpital Ambroise Paré [AP-HP], Skin Cancer Center Hannover, Hannover Medical School [Hannover] (MHH), Hôpital de la Timone [CHU - APHM] (TIMONE), Poznań University of Medical Sciences, Poznan University of Medical Sciences, Centre de Recherche en Cancérologie Nantes-Angers (CRCNA), Centre Hospitalier Universitaire d'Angers (CHU Angers), PRES Université Nantes Angers Le Mans (UNAM)-PRES Université Nantes Angers Le Mans (UNAM)-Hôtel-Dieu de Nantes-Institut National de la Santé et de la Recherche Médicale (INSERM)-Hôpital Laennec-Centre National de la Recherche Scientifique (CNRS)-Faculté de Médecine d'Angers-Centre hospitalier universitaire de Nantes (CHU Nantes), University of Kiel, UKSH, Maria Sklodowska Curie Memorial Center and Institute of Oncology, Division of Melanoma and Muscolocutaneous sarcoma, European Institute of Oncology, Hôpital de la Cavale Blanche - CHRU Brest (CHU - BREST ), GSK Vaccines - Belgium, Département de radiologie [Brest] (DR - Brest), Centre Hospitalier Régional Universitaire de Brest (CHRU Brest), Lymphocyte B et Auto-immunité (LBAI), Université de Brest (UBO)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Institut Brestois Santé Agro Matière (IBSAM), Université de Brest (UBO), Unité d'Echo-Doppler et de Médecine Vasculaire (BREST - ED MV), CHRU Brest - Service de Rhumatologie (CHU - BREST - Rhumato), Département de Médecine Interne et Pneumologie [Brest] (DMIP - Brest), Groupe d'Etude de la Thrombose de Bretagne Occidentale (GETBO), Institut Brestois Santé Agro Matière (IBSAM), Université de Brest (UBO)-Université de Brest (UBO)-Université de Brest (UBO), Centre Hospitalier Universitaire de Lille (CHU de Lille), Service de médecine interne [Lille], Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille), Hypertension arterielle pulmonaire physiopathologie et innovation thérapeutique, Centre chirurgical Marie Lannelongue-Institut National de la Santé et de la Recherche Médicale (INSERM), Institut Cochin (IC UM3 (UMR 8104 / U1016)), Université Paris Descartes - Paris 5 (UPD5)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Centre National de la Recherche Scientifique (CNRS), Hôpital Cochin [AP-HP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP), Université Paris-Sud - Paris 11 - Faculté de médecine (UP11 UFR Médecine), Université Paris-Sud - Paris 11 (UP11), Centre chirurgical Marie Lannelongue, Department of Pneumology [Lyon], Hospices Civils de Lyon (HCL), Service de pneumologie [Toulouse], CHU Toulouse [Toulouse]-Hôpital Larrey [Toulouse], CHU Toulouse [Toulouse], Service de cardiologie [CHU Rouen], Université de Rouen Normandie (UNIROUEN), Normandie Université (NU)-Normandie Université (NU)-CHU Rouen, Normandie Université (NU), Service de pneumologie [CHU Caen], Université de Caen Normandie (UNICAEN), Normandie Université (NU)-Normandie Université (NU)-CHU Caen, Normandie Université (NU)-Tumorothèque de Caen Basse-Normandie (TCBN)-Tumorothèque de Caen Basse-Normandie (TCBN), CHU Pontchaillou [Rennes], Unité de Recherche sur les Maladies Infectieuses Tropicales Emergentes (URMITE), Unité de Recherche sur les Maladies Infectieuses et Tropicales Emergentes (URMITE), Institut de Recherche pour le Développement (IRD)-Aix Marseille Université (AMU)-Institut National de la Santé et de la Recherche Médicale (INSERM)-IFR48, INSB-INSB-Centre National de la Recherche Scientifique (CNRS)-Institut de Recherche pour le Développement (IRD)-Aix Marseille Université (AMU)-Institut National de la Santé et de la Recherche Médicale (INSERM)-IFR48, INSB-INSB-Centre National de la Recherche Scientifique (CNRS), Centre de Ressources et de Compétences en Mucoviscidose [Nice] (CRCM [Nice]), Les Hôpitaux Pédiatriques de Nice CHU-Lenval, Service de pneumologie (Strasbourg), CHU Strasbourg-Nouvel Hôpital Civil, Hôpital Européen Georges Pompidou [APHP] (HEGP), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpitaux Universitaires Paris Ouest - Hôpitaux Universitaires Île de France Ouest (HUPO), Service de Médecine Interne [CHU Clermont-Ferrand], CHU Gabriel Montpied [Clermont-Ferrand], CHU Clermont-Ferrand-CHU Clermont-Ferrand, Laboratory of Fundamental and Applied Bioenergetics = Laboratoire de bioénergétique fondamentale et appliquée (LBFA), Institut National de la Santé et de la Recherche Médicale (INSERM)-Université Grenoble Alpes [2016-2019] (UGA [2016-2019]), Centre Hospitalier Universitaire [Grenoble] (CHU), Centre Hospitalier Régional Universitaire [Montpellier] (CHRU Montpellier), Orgamétrie biostatistiques, Service de pneumologie et Réanimation Respiratoire, Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpital Bicêtre-DHU Thorax Innovation, Hôpital Morvan [Brest], CIC Brest, Université de Brest (UBO)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Hôpital de la Cavale Blanche, University of Bonn, Centre Hospitalier Universitaire de Lyon (CHU Lyon), Division of Haematology and Haemostaseology, Department of Medicine I, Medizinische Universität Wien = Medical University of Vienna, Department of Cell Therapy and Hematology, San Bortolo Hospital, Calvez, Ghislaine, Lymphocytes B, Autoimmunité et Immunothérapies (LBAI), Université de Brest (UBO)-Institut National de la Santé et de la Recherche Médicale (INSERM)-LabEX IGO Immunothérapie Grand Ouest-Institut Brestois Santé Agro Matière (IBSAM), Université de Brest (UBO)-Université de Brest (UBO), Centre Chirurgical Marie Lannelongue (CCML)-Institut National de la Santé et de la Recherche Médicale (INSERM), Centre Chirurgical Marie Lannelongue (CCML), CHU Rouen, Normandie Université (NU)-Normandie Université (NU)-Université de Rouen Normandie (UNIROUEN), Université de Brest (UBO)-Institut National de la Santé et de la Recherche Médicale (INSERM)-LabEX IGO Immunothérapie Grand Ouest, Nantes Université (Nantes Univ)-Nantes Université (Nantes Univ)-Institut Brestois Santé Agro Matière (IBSAM), Centre Hospitalier Universitaire de Toulouse (CHU Toulouse), Institut des sciences biologiques (INSB-CNRS)-Institut des sciences biologiques (INSB-CNRS)-Centre National de la Recherche Scientifique (CNRS)-Institut de Recherche pour le Développement (IRD)-Aix Marseille Université (AMU)-Institut National de la Santé et de la Recherche Médicale (INSERM)-IFR48, Institut des sciences biologiques (INSB-CNRS)-Institut des sciences biologiques (INSB-CNRS)-Centre National de la Recherche Scientifique (CNRS), and Universität Bonn = University of Bonn
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[SDV] Life Sciences [q-bio] ,[SDV.MHEP.HEM] Life Sciences [q-bio]/Human health and pathology/Hematology ,[SDV.MHEP] Life Sciences [q-bio]/Human health and pathology ,[SDV]Life Sciences [q-bio] ,[SDV.MHEP.HEM]Life Sciences [q-bio]/Human health and pathology/Hematology ,ComputingMilieux_MISCELLANEOUS ,[SDV.MHEP]Life Sciences [q-bio]/Human health and pathology - Abstract
International audience
- Published
- 2016
22. Long-term outcomes of dasatinib-induced pulmonary arterial hypertension: a population-based study
- Author
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Weatherald, Jason, primary, Chaumais, Marie-Camille, additional, Savale, Laurent, additional, Jaïs, Xavier, additional, Seferian, Andrei, additional, Canuet, Matthieu, additional, Bouvaist, Hélène, additional, Magro, Pascal, additional, Bergeron, Anne, additional, Guignabert, Christophe, additional, Sitbon, Olivier, additional, Simonneau, Gérald, additional, Humbert, Marc, additional, and Montani, David, additional
- Published
- 2017
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23. Deterioration of pulmonary hypertension and pleural effusion with bosutinib following dasatinib lung toxicity
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Riou, Marianne, primary, Seferian, Andrei, additional, Savale, Laurent, additional, Chaumais, Marie-Camille, additional, Guignabert, Christophe, additional, Canuet, Matthieu, additional, Magro, Pascal, additional, Rea, Delphine, additional, Sitbon, Olivier, additional, Jaïs, Xavier, additional, Humbert, Marc, additional, and Montani, David, additional
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- 2016
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24. Periprandial administration of inhaled iloprost: a risk factor for digestive bleeding?
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Bigot, Adrien, Jonville-Bera, Annie-Pierre, Diot, Elisabeth, Magro, Pascal, and Diot, Patrice
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Letters to the Editors - Published
- 2011
25. Mortality in myotonic dystrophy patients in the area of prophylactic pacing devices
- Author
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Marijon, Eloi, Trinquart, Ludovic, Otmani, Akli, Leclercq, Christophe, Fauchier, Laurent, Chevalier, Philippe, Klug, Didier, Defaye, Pascal, Lellouche, Nicolas, Mansourati, Jacques, Deharo, Jean-Claude, Sadoul, Nicolas, Anselme, Frédéric, Maury, Philippe, Davy, Jean-Marc, Extramiana, Fabrice, Hidden-Lucet, Françoise, Probst, Vincent, Bordachar, Pierre, Mansour, Hassan, Chauvin, Michel, Jouven, Xavier, Lavergne, Thomas, Chatellier, Gilles, Le Heuzey, Jean-Yves, Laurent, Valérie, Pellieux, Sybille, Corcia, Philippe, Magro, Pascal, Pierre, Bertrand, Raynaud, Martine, Babuty, Dominique, Service de cardiologie pédiatrique [CHU Necker], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-CHU Necker - Enfants Malades [AP-HP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP), Centre d'Investigation Clinique - Epidemiologie Clinique/essais Cliniques [CHU HEGP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpital Européen Georges Pompidou [APHP] (HEGP), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpitaux Universitaires Paris Ouest - Hôpitaux Universitaires Île de France Ouest (HUPO)-Hôpitaux Universitaires Paris Ouest - Hôpitaux Universitaires Île de France Ouest (HUPO)-Institut National de la Santé et de la Recherche Médicale (INSERM), Service de cardiologie et maladies vasculaires [Rennes] = Cardiac, Thoracic, and Vascular Surgery [Rennes], CHU Pontchaillou [Rennes], CIC-IT Rennes, Hôpital Pontchaillou-Institut National de la Santé et de la Recherche Médicale (INSERM), Laboratoire Traitement du Signal et de l'Image (LTSI), Université de Rennes (UR)-Institut National de la Santé et de la Recherche Médicale (INSERM), CHU Trousseau [Tours], Centre Hospitalier Régional Universitaire de Tours (CHRU Tours), Service de cardiologie, Hôpital Est -Lyon, Service de Cardiologie A, Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille), Cardiac Stimulation and Rhythmology, CHU Grenoble, Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpital Henri Mondor-Université Paris-Est Créteil Val-de-Marne - Paris 12 (UPEC UP12), Optimisation des régulations physiologiques (ORPHY (EA 4324)), Université de Brest (UBO)-Centre Hospitalier Régional Universitaire de Brest (CHRU Brest)-Institut Brestois Santé Agro Matière (IBSAM), Université de Brest (UBO)-Université de Brest (UBO), Université de la Méditerranée - Aix-Marseille 2-Assistance Publique - Hôpitaux de Marseille (APHM)- Hôpital de la Timone [CHU - APHM] (TIMONE), Risque cardiovasculaire, rigidité-fibrose et hypercoagulabilité (RCV), Université Henri Poincaré - Nancy 1 (UHP)-Institut National de la Santé et de la Recherche Médicale (INSERM), Service de Cardiologie [CHRU Nancy], Centre Hospitalier Régional Universitaire de Nancy (CHRU Nancy), Service de cardiologie [CHU Rouen], CHU Rouen, Normandie Université (NU)-Normandie Université (NU)-Université de Rouen Normandie (UNIROUEN), Normandie Université (NU), Physiologie & médecine expérimentale du Cœur et des Muscles [U 1046] (PhyMedExp), Institut National de la Santé et de la Recherche Médicale (INSERM)-Université de Montpellier (UM)-Centre National de la Recherche Scientifique (CNRS), Centre Hospitalier Régional Universitaire [Montpellier] (CHRU Montpellier), Service de Cardiologie, Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Hôpital Lariboisière-Fernand-Widal [APHP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Université Paris Diderot - Paris 7 (UPD7), CHU Pitié-Salpêtrière [AP-HP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU), Institut du thorax, Université de Nantes (UN)-IFR26-Institut National de la Santé et de la Recherche Médicale (INSERM), Département de cardiologie, CHU Bordeaux [Bordeaux]-Hôpital Haut-Lévêque [CHU Bordeaux], CHU Bordeaux [Bordeaux], Laboratoire Interdisciplinaire de Physique [Saint Martin d’Hères] (LIPhy), Université Joseph Fourier - Grenoble 1 (UJF)-Centre National de la Recherche Scientifique (CNRS), Centre SLA, Griset SA, Diehl - Griset, Human Molecular Genetics, Université de Rennes 1 (UR1), Université de Rennes (UNIV-RENNES)-Université de Rennes (UNIV-RENNES)-Institut National de la Santé et de la Recherche Médicale (INSERM), Service de Chirurgie cardiaque et thoracique [CHU Pitié-Salpêtrière], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP), and Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU)
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Adult ,Male ,medicine.medical_specialty ,Pacemaker, Artificial ,Myotonic dystrophy ,Sudden death ,HV interval ,Pacemaker implantation ,[SHS]Humanities and Social Sciences ,Young Adult ,Internal medicine ,Medicine ,Humans ,Myotonic Dystrophy ,In patient ,ComputingMilieux_MISCELLANEOUS ,business.industry ,Middle Aged ,medicine.disease ,Death, Sudden, Cardiac ,Respiratory failure ,Sustained ventricular tachycardia ,Anesthesia ,Cardiology ,Female ,Cardiology and Cardiovascular Medicine ,business ,Atrioventricular block ,Follow-Up Studies - Abstract
Objectives Our study purports to determine whether implantation of a prophylactic pacemaker in MD patients with HV interval ≥70ms lowers the risk of sudden death, which may be essentially due to complete atrioventricular block. Background Sudden death occurs more frequently in patients with myotonic dystrophy (MD) than in the control population. Methods From 1994 to 2008, 100 consecutive patients were enrolled, 49 of whom were implanted. Results During an average follow-up of 74±39months, 10 deaths occurred. Nine were due to respiratory failure. Only one sudden death occurred, whereas 46% of patients were considered at risk of sudden death according to the criteria of Groh et al. [5]. The incidence rate of sudden death was only 0.2 per 100patient-years. One patient developed a paroxysmal syncopal sustained ventricular tachycardia. Conclusions The prophylactic implantation of PM in MD patients who are identified as being at risk of sudden death according to Groh's criteria reduced the incidence rate of sudden death. The one sudden death in an implanted MD patient suggests the likelihood that pacemaker implantation did not totally forestall this event. Ventricular arrhythmias may be involved in the sudden deaths in MD patients, in which case the implantation of an implantable cardiac defibrillator could be indicated.
- Published
- 2011
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26. A prospective study of the 6 min walk test as a surrogate marker for haemodynamics in two independent cohorts of treatment-naïve systemic sclerosis-associated pulmonary arterial hypertension
- Author
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Sanges, Sébastien, primary, Launay, David, additional, Rhee, Rennie L, additional, Sitbon, Olivier, additional, Hachulla, Éric, additional, Mouthon, Luc, additional, Guillevin, Loïc, additional, Rottat, Laurence, additional, Montani, David, additional, De Groote, Pascal, additional, Cottin, Vincent, additional, Magro, Pascal, additional, Prévot, Grégoire, additional, Bauer, Fabrice, additional, Bergot, Emmanuel, additional, Chabanne, Céline, additional, Reynaud-Gaubert, Martine, additional, Leroy, Sylvie, additional, Canuet, Matthieu, additional, Sanchez, Olivier, additional, Gut-Gobert, Christophe, additional, Dauphin, Claire, additional, Pison, Christophe, additional, Boissin, Clément, additional, Habib, Gilbert, additional, Clerson, Pierre, additional, Conesa, François, additional, Cordier, Jean-François, additional, Kawut, Steven M, additional, Simonneau, Gerald, additional, and Humbert, Marc, additional
- Published
- 2015
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27. A prospective study of the 6 min walk test as a surrogate marker for haemodynamics in two independent cohorts of treatment-naïve systemic sclerosis-associated pulmonary arterial hypertension.
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Sanges, Sébastien, Launay, David, Rhee, Rennie L., Sitbon, Olivier, Hachulla, Éric, Mouthon, Luc, Guillevin, Loïc, Rottat, Laurence, Montani, David, De Groote, Pascal, Cottin, Vincent, Magro, Pascal, Prévot, Grégoire, Bauer, Fabrice, Bergot, Emmanuel, Chabanne, Céline, Reynaud-Gaubert, Martine, Leroy, Sylvie, Canuet, Matthieu, and Sanchez, Olivier
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ANTIHYPERTENSIVE agents ,CARDIAC catheterization ,CARDIAC output ,COMPARATIVE studies ,HEMODYNAMICS ,LONGITUDINAL method ,RESEARCH methodology ,MEDICAL cooperation ,PULMONARY hypertension ,RESEARCH ,RESEARCH evaluation ,RESEARCH funding ,SYSTEMIC scleroderma ,EVALUATION research ,RANDOMIZED controlled trials ,DISEASE complications - Abstract
Objectives: Despite the wide use of the 6 min walk distance (6MWD), no study has ever assessed its validity as a surrogate marker for haemodynamics and predictor of outcome in isolated pulmonary arterial hypertension associated with systemic sclerosis (SSc-PAH). We designed this work to address this issue.Methods: Treatment-naïve patients with SSc-PAH were prospectively included from two sources: the French PAH Network (a prospective epidemiological cohort) (n=83) and randomised clinical trials submitted for drug approval (Food and Drug Administration) (n=332). Correlations between absolute values of the 6MWD and haemodynamics at baseline, as well as between variations of 6MWD and haemodynamics during follow-up, were studied in both populations.Results: In the French cohort, baseline cardiac output (CO) (R(2)=0.19, p=0.001) and New York Heart Association class (R(2)=0.10, p<0.001) were significantly and independently correlated with baseline 6MWD in multivariate analysis. A significant, independent, but weaker, correlation with CO was also found in the Food and Drug Administration sample (R(2)=0.04, p<0.001). During follow-up, there was no association between the changes in 6MWD and haemodynamic parameters in patients under PAH-specific treatments.Conclusions: In SSc-PAH, CO independently correlates with 6MWD at baseline, but accounts for a small amount of the variance of 6MWD in both study samples. This suggests that other non-haemodynamic factors could have an impact on the walk distance. Moreover, variations of 6MWD do not reflect changes in haemodynamics among treated patients. Our results suggest that 6MWD is not an accurate surrogate marker for haemodynamic severity, nor an appropriate outcome measure to assess changes in haemodynamics during follow-up in treated SSc-PAH. [ABSTRACT FROM AUTHOR]- Published
- 2016
- Full Text
- View/download PDF
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