1. Low dose stereotactic irradiation and dexamethasone in primary cerebral light chain deposition disease (LCDD).
- Author
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Authier, Daniel, Hegenbart, Ute, Pohl, Fabian, Rosenwald, Andreas, Kircher, Stefan, Menhart, Karin, Perl, Markus, Cerny, Jindrich, Mayer, Stephanie, Herr, Wolfgang, and Grube, Matthias
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INAPPROPRIATE ADH syndrome , *THERAPEUTICS , *SYMPTOMS , *BLOOD diseases , *NON-Hodgkin's lymphoma , *DIAGNOSIS - Abstract
Since PET-CT imaging showed a clear SP 68 sp Ga-Pentixafor uptake in the cerebral mass, the hypothesis that clonal plasma cells are the cellular origin of the LCDD could be confirmed. Primary cerebral low-grade B-cell lymphoma, monoclonal immunoglobulin deposition disease, cerebral light chain deposition disease and "aggregoma": an update on classification and diagnosis. In our patient, the disease seemed to progress rather slowly, the interval from symptom onset to the final diagnosis was several months. Primary cerebral non-amyloid light chain deposition disease (LCDD) is a rare disease caused by the deposition of light chain fragments in brain tissue without a systemic hematological disorder. [Extracted from the article]
- Published
- 2021
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