1. Congenital Cystic Lesions of the Bile Ducts: Imaging-Based Diagnosis
- Author
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Mariangela Diamarco, Giuseppe Cutaia, Massimo Midiri, Dario Giambelluca, Roberto Cannella, Giovanni Caruana, Giuseppe Salvaggio, Cannella R., Giambelluca D., Diamarco M., Caruana G., Cutaia G., Midiri M., and Salvaggio G.
- Subjects
Liver Cirrhosis ,medicine.medical_specialty ,Caroli disease ,Digestive System Diseases ,Hamartoma ,Cystic lesions ,030218 nuclear medicine & medical imaging ,Diagnosis, Differential ,03 medical and health sciences ,Cystic lesion ,0302 clinical medicine ,Medicine ,Humans ,Radiology, Nuclear Medicine and imaging ,Choledochal cysts ,Fibropolycystic liver disease ,medicine.diagnostic_test ,business.industry ,Cysts ,Polycystic liver disease ,Liver Diseases ,Ultrasound ,Genetic Diseases, Inborn ,Magnetic resonance imaging ,medicine.disease ,Caroli Disease ,Liver ,030220 oncology & carcinogenesis ,Congenital hepatic fibrosis ,Radiology ,Differential diagnosis ,business ,Settore MED/36 - Diagnostica Per Immagini E Radioterapia - Abstract
Congenital cystic lesions of the bile ducts represent a spectrum of liver and biliary system lesions, resulting from abnormal embryologic development of the ductal plate. These disorders include Caroli disease, choledochal cysts, autosomal dominant polycystic liver disease, congenital hepatic fibrosis, and biliary hamartomas. Each disorder carries a peculiar clinical presentation, prognosis, and risk of complications. Knowledge of radiological findings of fibropolycystic liver diseases is crucial for their appropriate detection and for differential diagnosis with other similar hepatic cystic lesions, in order to avoid relevant misdiagnosis. The aim of this review is to provide an illustrative summary of the most relevant imaging findings of these conditions as encountered on ultrasound, computed tomography, and magnetic resonance imaging, and provide pearls for imaging-based differential diagnosis. (c) 2019 Elsevier Inc. All rights reserved.
- Published
- 2020