33 results on '"Dearborn, Joshua T."'
Search Results
2. Gene therapy ameliorates spontaneous seizures associated with cortical neuron loss in a [Cln2.sup.R207X] mouse model
3. Cell-autonomous expression of the acid hydrolase galactocerebrosidase
4. Genetic ablation of acid ceramidase in Krabbe disease confirms the psychosine hypothesis and identifies a new therapeutic target
5. Synergistic effects of treating the spinal cord and brain in CLN1 disease
6. Cross-species efficacy of enzyme replacement therapy for CLN1 disease in mice and sheep
7. Widespread Expression of a Membrane-Tethered Version of the Soluble Lysosomal Enzyme Palmitoyl Protein Thioesterase-1
8. Spontaneous seizures associated with cortical interneuron loss in mice are ameliorated via gene therapy
9. Conditional knockout of UBC13 produces disturbances in gait and spontaneous locomotion and exploration in mice
10. Adjunctive Therapy for Long-Term Support of Cognitive Impairment
11. Cortical interneuron loss and seizure generation as novel clinically relevant disease phenotypes in Cln2R207X mice
12. Effects of chronic cannabidiol in a mouse model of naturally occurring neuroinflammation, neurodegeneration, and spontaneous seizures
13. Efficacy of recombinant human PPT1 enzyme replacement therapy in mouse and sheep models of CLN1 disease
14. A MYT1L syndrome mouse model recapitulates patient phenotypes and reveals altered brain development due to disrupted neuronal maturation
15. Circadian clock proteins regulate neuronal redox homeostasis and neurodegeneration
16. Recombinant NAGLU-IGF2 prevents physical and neurological disease and improves survival in Sanfilippo B syndrome
17. A MYT1L Syndrome mouse model recapitulates patient phenotypes and reveals altered brain development due to disrupted neuronal maturation
18. Genetic ablation of acid ceramidase in Krabbe disease confirms the psychosine hypothesis and identifies a new therapeutic target.
19. Histochemical localization of palmitoyl protein thioesterase-1 activity
20. Comprehensive functional characterization of murine infantile Batten disease including Parkinson-like behavior and dopaminergic markers
21. An Anti-Neuroinflammatory That Targets Dysregulated Glia Enhances the Efficacy of CNS-Directed Gene Therapy in Murine Infantile Neuronal Ceroid Lipofuscinosis
22. Anti-ApoE Antibody Given after Plaque Onset Decreases Aβ Accumulation and Improves Brain Function in a Mouse Model of Aβ Amyloidosis
23. Expression of Nampt in Hippocampal and Cortical Excitatory Neurons Is Critical for Cognitive Function
24. Motivational Disturbances and Effects of L-dopa Administration in Neurofibromatosis-1 Model Mice
25. Loss of RBPj in Postnatal Excitatory Neurons Does Not Cause Neurodegeneration or Memory Impairments in Aged Mice
26. Adrenal Steroids Uniquely Influence Sexual Motivation Behavior in Male Rats
27. Bone Marrow Transplantation Alters the Tremor Phenotype in the Murine Model of Globoid-Cell Leukodystrophy
28. P1-153: Core features of human frontotemporal dementia recapitulated in progranulin knockout mice
29. Anti-ApoE Antibody Given after Plaque Onset Decreases Aβ Accumulation and Improves Brain Function in a Mouse Model of Aβ Amyloidosis.
30. Core features of human frontotemporal dementia recapitulated in progranulin knockout mice
31. Gene therapy ameliorates spontaneous seizures associated with cortical neuron loss in a Cln2R207X mouse model.
32. A MYT1L syndrome mouse model recapitulates patient phenotypes and reveals altered brain development due to disrupted neuronal maturation.
33. Spontaneous seizures associated with cortical interneuron loss in Cln2R207Xmice are ameliorated via gene therapy.
Catalog
Books, media, physical & digital resources
Discovery Service for Jio Institute Digital Library
For full access to our library's resources, please sign in.