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We conducted a study of five patients with congenital diaphragmatic hernia (CDH) in the department of antenatal diagnosis over a period of two years. Our study highlights the overall benchmarks for this disease and its management as well as the news on prenatal assessment of neonatal prognosis using Lung Over Head Ratio (LHR): ultrasound versus magnetic resonance imaging (MRI) in the third world. The purpose of this study is to evaluate the prognosis of these new-born babies and support parents of a fetus with diaphragmatic hernia. [ABSTRACT FROM AUTHOR]

Multicystic dysplastic kidney (MCDK) is the most common Congenital Abnormalities of Kidney and Urinary Tract (CAKUT) in clinical practice. Its etiology and pathogenesis are still controversial and obstruction is a generally accepted causative assumption. Obstetric ultrasound is the gold standard for prenatal diagnosis and for the detection of other associated malformations. Prenatal management is based on ultrasound monitoring of pregnancy, of the disease, of the occurrence of other anomalies and of the amount of amniotic fluid. This study aims to report our experience in the Department of Gynecology-Obstetrics 2 at the University Hospital Hassan II-Fez in order to clarify the epidemiology of MCDK, highlight the role of obstetric ultrasound in positive and etiological diagnosis while describing the various sonographic appearances. It is essential to schedule for screening tests during pregnancy in order to assess the evolution of the disease diagnosed in the prenatal period, to implement a strategy in postpartum care and to establish a prognosis. [ABSTRACT FROM AUTHOR]

Amniotic band syndrome (ABS) comprises of a spectrum of complex congenital malformations mainly interesting the limbs, but even the craniofacial region and the thoracoabdominal axis. There are two major opposing pathophysiological theories: premature rupture of the amniotic sac (exogenous growth theory) would result in the formation of fibrous bands which would lead to strangulation, thus causing the observed abnormalities; the endogenous theory holds that this is a syndrome of vascular origin and that the bands have no causative role. Prognosis depends on the severity of malformations. We here report two cases of lethal malformations in order to discuss the challenges in the diagnosis and treatment of amniotic band syndrome. This study mainly aims to highlight the role of prenatal diagnosis in the therapeutic management of this embryo-fetopathy. [ABSTRACT FROM AUTHOR]

Les kystes para tubaires sont des lésions fréquentes, et peuvent être responsables de complications à type de torsion d'annexe qui est rarissime et difficile à diagnostiquer. Cette pathologie est souvent confondue à une torsion ovarienne, la prise en charge dans les deux cas nécessite une intervention chirurgicale en urgence afin de tenter de conserver l'annexe. Nous rapportons un cas rare d'une jeune patiente opérée d'un kyste para tubaire bénin tordue de diagnostic difficile. [ABSTRACT FROM AUTHOR]

L'association d'une appendicite aigue et une grossesse extra utérine est rare, seulement une vingtaine de cas ont été rapportés dans la littérature. Nous présentons un cas d'une patiente de 27 ans opérée pour suspicion de grossesse extra utérine droite, le diagnostic d'appendicite aigue a été fait en peropératoire devant la constatation d'un appendice enflé accolé à la masse latéroutérine. A travers ce cas rapporté et une revue de la littérature, nous mettons le point sur la nécessité de penser à l'appendicite aigue associée devant un tableau évoquant une grossesse extra utérine surtout à droite en raison de la relation étiopathogénique entre ces deux pathologies responsables de douleurs aigues bien que leur association reste rare. [ABSTRACT FROM AUTHOR]

Borderline para-ovarian cysts (PCs) are rare entities. They are commonly present in the third decade. Borderline PCs are often discovered fortuitously on routine ultrasound examination or they are common incidental findings during a laparotomy . They must be differentiated from simple ovarian cysts, peritoneal inclusion cysts and hydrosalpinges on ultrasound sonography. Papillary projections on the cyst wall should be searched carefully to suggest diagnosis. The treatment is surgical including fertility -sparing operation or more radical surgery depending on the case. The prognosis is good because borderline PCs are usually early-stage at diagnosis. Here is a report of a 38- year old woman with a borderline paratubal cyst. Adnexal torsion of hydrosalpinx was suspected; thus, she underwent an urgent surgery. Cystectomy was performed without rupture. The final diagnosis revealed a borderline PC. The patient underwent a radical surgery. Currently, she has had no evidence of disease recurrence. [ABSTRACT FROM AUTHOR]

Les carcinomes épidermoides du sein sont rares. Ils sont d'origine métaplasiques. Leur histogénèse est controversée. La présentation clinique et mammographique n'est pas spécifique, l'aspect kystisé des lésions et la présence de nécrose sont recherchés à l'échographie mammaire. Le diagnostic est histologique. Ce cancer est réputé être peu lymphophile et non hormonodépendant. Le traitement rejoint celui des carcinomes infiltrants canalaires et repose sur la chirurgie, la radiothérapie et la chimiothérapie. Le pronostic est péjoratif. Nous rapportons trois cas de carcinome épidermoide du sein colligés au service de Gynécologie obstétrique II au CHU Hassan II de Fès et une revue de la littérature. [ABSTRACT FROM AUTHOR]

Introduction Pregnancy-related compressive myelopathy secondary to vertebral hemangioma is a rare occurrence and its treatment antepartum is rare. Case presentation A 19-year-old North African woman in her 38th week of pregnancy presented with paraplegia that progressed within 2 days after a rapidly progressive weakness of her lower limbs. Magnetic resonance imaging studies showed compression of her spinal cord in front of the fourth thoracic vertebra for suspected tuberculous spondylitis. A Caesarean section was done followed by corpectomy with a bone graft because we intraoperatively discovered a vertebral hemangioma. Pathology showed an aggressive hemangioma. Conclusion At any term of pregnancy, extensive neurological involvement which is rapidly progressive due to compression should be considered for immediate decompression. [ABSTRACT FROM AUTHOR]

L'hyperplasie congénitale des surrénales (HCS) par déficit en 21 hydroxylase à révélation tardive est une maladie à transmission autosomique récessive dont la présentation usuelle est une virilisation tardive para ou post pubertaire. Nous rapportons le cas d'une patiente âgée de 17 ans, ayant consulté pour aménorrhée primaire, chez qui l'examen clinique a trouvé un morphotype masculin, des signes de virilisation, des caractères sexuels secondaires présents avec une hypertrophie péniforme du clitoris. L'échographie pelvienne a confirmé la présence de l'utérus et des ovaires et a éliminé une cause tumorale ovarienne. Le dosage du sulfate de DHA (1145 ug/dl) et la 17 OH progestérone à 49,6 ng/ml étant élevés, ont orienté le diagnostic vers l'hyperplasie congénitale des surrénales à révélation tardive par déficit partiel en 21 hydroxylase. La TDM abdominale a trouvé une hypertrophie homogène bilatérale des surrénales. La patiente a été mise sous déxaméthasone 0,5 mg/ j avec déclenchement des cycles menstruels au bout de 4 mois de traitement. Une plastie clitoridienne ainsi qu'une étude moléculaire génétique étaient prévues mais la patiente était perdue de vue. A travers cette observation, et à la lumière d'une revue de la littérature, nous insistons sur les caractéristiques cliniques et para cliniques de cette entité, ainsi que l'intérêt du diagnostic précoce pour permettre une croissance normale, une puberté féminine et une fertilité satisfaisante. [ABSTRACT FROM AUTHOR]

Introduction: Pregnancy-related compressive myelopathy secondary to vertebral hemangioma is a rare occurrence and its treatment antepartum is rare.Case Presentation: A 19-year-old North African woman in her 38th week of pregnancy presented with paraplegia that progressed within 2 days after a rapidly progressive weakness of her lower limbs. Magnetic resonance imaging studies showed compression of her spinal cord in front of the fourth thoracic vertebra for suspected tuberculous spondylitis. A Caesarean section was done followed by corpectomy with a bone graft because we intraoperatively discovered a vertebral hemangioma. Pathology showed an aggressive hemangioma.Conclusion: At any term of pregnancy, extensive neurological involvement which is rapidly progressive due to compression should be considered for immediate decompression. [ABSTRACT FROM AUTHOR]